Densidade mineral óssea em crianças talassêmicas: uma experiência brasileira Bone mineral density in thalassemic children: a Brazilian experience [PDF]
A osteoporose, caracterizada por aumento da fragilidade óssea e suscetibilidade a fraturas, é inversamente proporcional ao pico de massa óssea adquirido na infância.
Perla Vicari +5 more
doaj +4 more sources
Thalassemia: essential radiographic and clinical features of interest to dentistry [PDF]
Thalassemia is a type of hereditary anemia that predominantly affects individuals born in or descendents of countries bathed by the Mediterranean Sea, such as Italy and Greece.
Luiz Roberto Coutinho Manhães Junior +4 more
doaj +2 more sources
Hemoglobinopatias no Distrito Federal, Brasil [PDF]
Em uma amostra de 3137 pessoas, residentes no Distrito Federal, foram detectadas as seguintes hemoglobinas: em 3009(95,92%) HbAA; em 91 (2,90%) HbAS; em 20(0,64%) HbAC; em 8 (0,26%) talassemia beta minor; em 5(0,16%) HbAJ alfa; em 3 (0,09%) HbAM e em 1 ...
J. Tavares-Neto +15 more
doaj +7 more sources
Incidence of cancer and related deaths in hemoglobinopathies: A follow-up of 4631 patients between 1970 and 2021. [PDF]
Abstract Background The correlation between thalassemia and malignancies other than hepatocellular carcinoma (HCC) and the possible relationship between other hemoglobinopathies and tumor risk have been poorly evaluated. Methods Eight Italian specialized centers evaluated the incidence of malignant neoplasms in hemoglobinopathies as well as their sites
Origa R +20 more
europepmc +2 more sources
Thalassaemia is paradoxically associated with a reduced risk of in-hospital complications and mortality in COVID-19: Data from an international registry. [PDF]
Abstract Although numerous patient‐specific co‐factors have been shown to be associated with worse outcomes in COVID‐19, the prognostic value of thalassaemic syndromes in COVID‐19 patients remains poorly understood. We studied the outcomes of 137 COVID‐19 patients with a history of transfusion‐dependent thalassaemia (TDT) and transfusion independent ...
El-Battrawy I +49 more
europepmc +2 more sources
5613417 CO-TREATMENT OF ERYTHROID CELLS ISOLATED FROM Β039-THALASSEMIA PATIENTS WITH CRISPR-CAS9 GENE EDITING AND FETAL HEMOGLOBIN INDUCTION [PDF]
HemaSphere, Volume 7, Issue S1, Page 41-41, April 2023.
M.L.P. Lipucci di Paola +5 more
europepmc +2 more sources
5613423 TREATMENT OF ERYTHROID PRECURSOR CELLS FROM β-THALASSEMIC PATIENTS WITH ISOXAZOLE DERIVATIVES: POTENT INDUCTION OF FETAL HEMOGLOBIN [PDF]
HemaSphere, Volume 7, Issue S1, Page 17-17, April 2023.
C.Z. Cristina Zuccato +9 more
europepmc +2 more sources
P129: NARRATING SICKLE CELL DISEASE: THE EXPERIENCES OF PATIENTS AND CARGIVERS [PDF]
HemaSphere, Volume 6, Issue S1, Page 32-32, January 2022.
De Franceschi L +13 more
europepmc +2 more sources
Abstract Background The average hemoglobin content of red cell concentrates (RCC) varies depending on the method of preparation. Surprisingly less data are available concerning the clinical impact of those differences. Study Design and Methods The effects of two types of RCC (RCC‐A, RCC‐B) on transfusion regime were compared in a non‐blinded ...
Maria Rita Gamberini +15 more
wiley +1 more source
Selecting β‐thalassemia Patients for Gene Therapy: A Decision‐making Algorithm
This expert opinion originally developed by a panel of the Italian Society of Thalassemias and Hemoglobinopathies (SITE), reviewed and adopted by the European Hematology Association (EHA) through the EHA Scientific Working Group on Red Cells and Iron, has been developed as priority decision‐making algorithm on evidence and consensus with the aim to ...
Donatella Baronciani +13 more
wiley +1 more source

