Results 71 to 80 of about 138,095 (212)

Standardized T2* map of a normal human heart to correct T2* segmental artefacts; Myocardial iron overload and fibrosis in thalassemia intermedia versus thalassemia major patients and electrocardiogram changes in thalassemia major patients RID A-6953-2008

, 2008
Studies of the standardized, 3D, 16-segments map of the circumferential distribution of T2* values, Of cardiovascular magnetic resonance (CMR) in thalassemia major (TM) and thalassemia intermedia (TI) patients and of electrocardiogram (ECG) changes ...
De Marchi D, G Derchi, M Pili, Filosa A, Cianciulli P, Formisano F, Maggio A, Pitrolo L, Ramazzotti A, Forni G, Landini L, Santarelli MF, Lombardi M, Positano V, Capra M, Derchi G, Pepe A, Scattini B, Borgna Pignatti C, Lai M E, BORGNA, Caterina, Lai ME, LANDINI, LUIGI, Borgna-Pignatti C, Santarelli M F, Prossomariti L, Keilberg P, Lombardi M., Pili M   +28 more
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Asymtomatic essential thrombocythemia in a child: a rare case report

International Journal of Hematology-Oncology and Stem Cell Research, 2013
Essential thrombocythemia is a rare myeloproliferative disorder in pediatrics. This myeloproliferative disorder is charactherized by thrombocytosis and hyperplasia of megakaryocytes in the bone marrow. Other cell lines are not involved.JAK2V617Fmutations
Majid Vafaie, Kaveh Jaseb, Majid Ghanavat, Mohamad Pedram, Tooran Rahiminia   +4 more
doaj  

Epidemiological and comorbidity burden in transfusion-dependent patients with thalassemia and sickle cell disease in Greece

Annals of Hematology
TDT and SCD are hereditary hemoglobinopathies that require lifelong red blood cell transfusions. Modern treatment has increased survival, exposing patients to transfusion-related problems such iron excess.
Sophia Delicou, Aikaterini Xydaki, Vassiliki Kamposou, Sabrina Goga, Anthimos Papadopoulos, Christina Rina, Maria Moraki   +6 more
doaj   +1 more source

Thailand's Emerging Role in the Cell and Gene Therapy Revolution: A Review of Progress and Potential

Clinical and Translational Science
This Perspective examines Thailand's role in cell and gene therapy, focusing on regulatory development and early clinical experience. These therapies are used in Thailand for β‐thalassemia, or blood cancer, together with the evolving ATMP regulatory ...
Vip Viprakasit, Warut Tulalamba, Thidarat Suksangpleng, Supachai Ekwattanakit   +3 more
doaj   +1 more source

Causes of Hospitalizations in Pediatric Patients with Thalassemia under the National Health Coverage Scheme in Thailand

Thalassemia is a hereditary hemolytic anemia that is prevalent in Southeast Asia. The primary treatment for severe thalassemia involves red cell transfusion, iron chelation, and the treatment of long-term complications, leading to frequent hospital ...
Panya Seksarn, Patcharee Komvilaisak, Kaewjai Thepsuthummarat, Kitti Torcharus, Pimlak Charoenkwan   +4 more
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The emerging role of non-coding RNAs in the pathogenesis of infantile hemangioma

Cancer Cell International
Infantile hemangioma (IH) is a common benign tumor that occurs in children, affecting both blood vessels and soft tissues. Its pathological features include abnormal proliferation of endothelial cells and an irregular vascular structure.
Najmaldin Saki, Narjes Sadat Sadati, Zeinab Deris Zayeri, Masoud Kargar   +3 more
doaj   +1 more source

Structural and functional characterization of CSDA protein complexes involved in the modulation of fetal globin gene expression [PDF]

, 2009
Impaired switching from fetal hemoglobin (HbF) to adult globin gene expression leads to hereditary persistence of fetal hemoglobin (HPFH) in adult life.
Gaudino, Sara
core   +1 more source

Pregnancy in women with thalassemia: challenges and solutions

, 2016
George Petrakos, Panagiotis Andriopoulos, Maria Tsironi Department of Nursing, University of Peloponnese, Sparta, Greece Abstract: Advances in treatment of thalassemia have led to the aging of thalassemic patients, and consequently concern about ...
Andriopoulos P, Petrakos G, Tsironi M
core  

Enhanced induction of fetal hemoglobin by the combination of decitabine with RN-1 in β-thalassemia/HbE erythroid progenitor cells

Molecular Medicine
Background Fetal hemoglobin (HbF; α2γ2) induction is a well-established approach for β-hemoglobinopathies, including sickle cell disease (SCD) and β-thalassemia.
Tiwaporn Nualkaew, Phitchapa Pongpaksupasin, Thongperm Munkongdee, Nattrika Buasuwan, Kittiphong Paiboonsukwong, Orapan Sripichai, James Douglas Engel, Suradej Hongeng, Suthat Fucharoen, Natee Jearawiriyapaisarn   +9 more
doaj   +1 more source

Frequency of musculoskeletal and otorhinolaryngologic manifestations in children with B-thalassemia [PDF]

, 2015
Background: Beta-thalassaemias have a wide variety of musculoskeletal system manifestations. Spinal involvement related to disease course and treatment is common in patients with thalassemia syndromes. Also, a high frequency sensorineural hearing loss is
Elsaeed, W, Kelani, H, Atta, D, Hassan, M, Hesham, M, Ezzeldin, N, Elsoaud, A Abo, Mortada, M   +7 more
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