Urticaria pigmentosa de presentación atípica en la infancia: Reporte de un caso clínico
La Urticaria Pigmentosa es el tipo más frecuente de mastocitosis cutáneas de inicio en la edad pediátrica, representando el 75% de los casos. Se presenta con máculas y/o pápulas de color amarillo a café-rojizo, usualmente con signo de Darier positivo y ...
Catherina Moll-Manzur +2 more
doaj +2 more sources
The authors describe the clinical observation of a case of the aggressive systemic mastocytosis with skin involvement, the type of generalized urticaria pigmentosa.
E. V. Sokolovskiy +3 more
doaj +2 more sources
Mastocitosis: urticaria pigmentosa [PDF]
La mastocitosis es una enfermedad rara. Se caracteriza por una proliferación benigna o en raras ocasiones maligna de mastocitos en los tejidos. Puede producir alteraciones tanto sistémicas como cutáneas.
Pedro Antonio Díaz Llanio +4 more
doaj +1 more source
Urticaria pigmentosa en el adulto
La urticaria pigmentosa es una de las formas más comunes de las mastocitosis, las cuales corresponden a una serie de procesos caracterizados por un aumento anormal de los mastocitos en diversos órganos y tejidos corporales. En la urticaria pigmentosa
Jhon Alexander Ávila Rueda +4 more
doaj +1 more source
Co-Occurrence of neurofibromatosis-1 with urticaria pigmentosa: A Coincidental association?
Neurofibromatosis-1 (NF-1) is a neuroectodermal abnormality characterized by multiple neurofibromas, café-au-lait macules, axillary freckling, and Lisch nodules.
Nazneen Zulfikar Arsiwala +2 more
doaj +2 more sources
Coexistence of urticaria pigmentosa and thalassemia minor in a young adult [PDF]
Funda Tamer, Haldun Umudum
doaj +2 more sources
Hidden in Plain Sight: Systemic Mastocytosis Manifesting as Isolated Hepatosplenomegaly in the Absence of Cutaneous and Classical Manifestations-A Case Report and Literature Review. [PDF]
ABSTRACT Systemic mastocytosis (SM) is a rare clonal myeloproliferative neoplasm typically characterized by cutaneous lesions and mediator‐release symptoms. Presentations dominated by visceral organ involvement without skin findings are uncommon and pose a significant diagnostic challenge, often mimicking hematologic malignancies.
Sadam Zeb M +9 more
europepmc +2 more sources
Beyond Histamine: Mast Cell-Neuron Communication in Chronic Pruritic and Pain Disorders. [PDF]
ABSTRACT Chronic pruritic and cutaneous pain disorders are increasingly recognized as neuroimmune conditions driven by dynamic interactions between immune and sensory systems. While histamine has historically dominated models of mast cell‐mediated itch, accumulating evidence indicates that non‐histaminergic pathways are central to chronic disease.
Kagan T, Yosipovitch G.
europepmc +2 more sources
A Curious Case of Hyperpigmented Macules with Inducible Wheals
A provisional diagnosis of urticaria pigmentosa was revised to lichen planus pigmentosus with dermatographism, after histopathologic examination of specimen from hyperpigmented patch.
Shreya Deoghare +3 more
doaj +1 more source
Mastocitosis Cutánea y Urticaria Pigmentosa: Estudio de Casos y Actualización Terapéutica [PDF]
Cutaneous mastocytosis is a rare disease with a good prognosis. It is characterized by the invasion of mast cells, in abnormal amount, in the skin.
Burgos, Guillermo
core +2 more sources

