Results 141 to 150 of about 114,902,985 (177)

Comparative study on incorporation of three recombinant human α-galactosidase A drugs (agalsidases) into cultured fibroblasts and organs/tissues of Fabry mice. [PDF]

Mol Genet Metab Rep
Tsukimura T, Shiga T, Togawa T, Sakuraba H.   +3 more
europepmc   +1 more source

Mechanistic Insights into Dibasic Iminosugars as pH-Selective Pharmacological Chaperones to Stabilize Human α-Galactosidase. [PDF]

JACS Au
Li HY, Lin HY, Chang SK, Chiu YT, Hou CC, Ko TP, Huang KF, Niu DM, Cheng WC.   +8 more
europepmc   +1 more source

Misfolding of Lysosomal α-Galactosidase a in a Fly Model and Its Alleviation by the Pharmacological Chaperone Migalastat. [PDF]

Int J Mol Sci, 2020
Braunstein H, Papazian M, Maor G, Lukas J, Rolfs A, Horowitz M.   +5 more
europepmc   +1 more source

Safety evaluation of the food enzyme α-galactosidase from the genetically modified <i>Saccharomyces cerevisiae</i> strain CBS 615.94. [PDF]

EFSA J
EFSA Panel on Food Contact Materials, Enzymes and Processing Aids (CEP), Lambré C, Barat Baviera JM, Bolognesi C, Cocconcelli PS, Crebelli R, Gott DM, Grob K, Lampi E, Mengelers M, Mortensen A, Rivière G, Steffensen IL, Tlustos C, Van Loveren H, Vernis L, Zorn H, Roos Y, Aguilera J, Andryszkiewicz M, Kovalkovicova N, Liu Y, Marini E, Chesson A.   +24 more
europepmc   +1 more source

Influence of diet nutrient density and a multicarbohydrase containing α-galactosidase on performance, carcass characteristics, breast myopathies, and nutrient utilization of broilers reared from 1 to 42 days of age. [PDF]

Poult Sci
Gulizia JP, Vargas JI, Bonilla SM, Hernandez JR, Almeida LM, Soster P, Thuekeaw S, Hutson B, Llamas-Moya S, Duong T, Pacheco WJ.   +10 more
europepmc   +1 more source

α-Galactosidase and Sucrose-Kinase Relationships in a Bi-functional AgaSK Enzyme Produced by the Human Gut Symbiont Ruminococcus gnavus E1. [PDF]

Front Microbiol, 2020
Lafond M, Tauzin AS, Bruel L, Laville E, Lombard V, Esque J, André I, Vidal N, Pompeo F, Quinson N, Perrier J, Fons M, Potocki-Veronese G, Giardina T.   +13 more
europepmc   +1 more source

Lysosomal Storage-Independent Fabry Disease Variants with α-Galactosidase A Misprocessing-Induced ER Stress and the Unfolded Protein Response.

Nephron
Živná M, Živná M, Lenders M, Kmoch S.   +3 more
europepmc   +1 more source

Rats deficient in α-galactosidase A develop ocular manifestations of Fabry disease. [PDF]

Sci Rep, 2019
Miller JJ, Aoki K, Reid CA, Tiemeyer M, Dahms NM, Kassem IS.   +5 more
europepmc   +1 more source

Inhibition of Mitochondrial Complex I Impairs Release of α-Galactosidase by Jurkat Cells. [PDF]

Int J Mol Sci, 2019
Lambert JRA, Howe SJ, Rahim AA, Burke DG, Heales SJR.   +4 more
europepmc   +1 more source