Reduced ADAMTS13 activity during TTP remission is associated with stroke in TTP survivors.
Blood, 2019 With timely and effective treatment, most patients with thrombotic thrombocytopenic purpura (TTP) survive their acute episode. In addition to the risk of relapse, TTP survivors have higher all-cause mortality than the general population and increased ...
H. Upreti +12 more
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Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor-cleaving protease activity [PDF]
, 2002 Koichi Kokame +11 more
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D-dimer, Von Willibrand factor, and ADAMTS13 in renal transplant recipients
Journal of Medicine in Scientific Research, 2018 Introduction Chronic kidney disease and renal transplants are associated with activation of coagulation. Microvascular thrombosis and fibrinolytic disorders have been recognized as main causes of allograft rejection in renal transplant recipients.
Azza A I. Elmenyawi, Ahmed Hassan
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Deficiency of ADAMTS13 and thrombotic thrombocytopenic purpura [PDF]
, 2002 Han‐Mou Tsai
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Atypical Hemolytic Uremic Syndrome: Differential Diagnosis from TTP/HUS and Management
Turkish Journal of Hematology, 2014 Atypical hemolytic uremic syndrome (aHUS) is a rare form of thrombotic microangiopathy (TMA). It has an unfavorable outcome with death rates as high as 25% during the acute phase and up to 50% of cases progressing to end-stage renal failure. Uncontrolled
Mustafa N. Yenerel
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ADAMTS13 activity in thrombotic thrombocytopenic purpura–hemolytic uremic syndrome: relation to presenting features and clinical outcomes in a prospective cohort of 142 patients [PDF]
, 2003 Sara K. Vesely +6 more
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Blood Advances, 2019 : Immune thrombotic thrombocytopenic purpura (iTTP) is primarily caused by immunoglobulin G (IgG)–type autoantibodies that bind and inhibit plasma ADAMTS13 activity and/or accelerate its clearance from circulation. Approximately 50% of patients with iTTP
Jingrui Sui +9 more
doaj
ADAMTS13 autoantibody detection by quantitative immunoblotting [PDF]
, 2003 Katalin Váradi +7 more
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Congenital thrombotic thrombocytopenic purpura in association with a mutation in the second CUB domain of ADAMTS13 [PDF]
, 2003 John E. Pimanda +5 more
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ADAMTS13 gene mutation in congenital thrombotic thrombocytopenic purpura with previously reported normal VWF cleaving protease activity [PDF]
, 2003 Süreyya Savaşan +3 more
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