, 2018 Thrombotic thrombocytopenic purpura (TTP) is a life-threatening thrombotic microangiopathic (TMA) disorder characterized by severe thrombocytopenia, haemolytic anemia and severe organ failure. The pathophysiology of TTP is linked to a deficiency in the haemostatic multi-domain protease ADAMTS13 (A Disintegrin And Metalloprotease domain with ...
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Complement activation in thrombotic thrombocytopenic purpura [PDF]
, 2014 Alvarez-Larran +28 more
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The Effect of IL-6-Primed Platelets on ADAMTS13-Mediated Clearance of Platelet-Bearing ULVWF and Its Mechanism [PDF]
, 2021 Hyun‐Jeong Kim +4 more
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Acquired thrombotic thrombocytopenic purpura and HIV infection: a case report and review of the literature. [PDF]
Ann HematolRao S +6 more
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Increased Complement Activation and Decreased ADAMTS13 Activity Are Associated with Genetic Susceptibility in Patients with Preeclampsia/HELLP Syndrome Compared to Healthy Pregnancies: An Observational Case-Controlled Study [PDF]
Theodora-Maria Venou +14 more
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Addition of ADAMTS13 testing to cryptogenic stroke evaluation: index case and single-center screening initial experience. [PDF]
Blood AdvBoothby A +9 more
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Kinetic modeling of the plasma pharmacokinetic profiles of ADAMTS13 fragment and its Fc-fusion counterpart in mice [PDF]
Heechun Kwak +7 more
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