Results 1 to 10 of about 17,175,483 (375)
Some of the next articles are maybe not open access.
Orphanet Journal of Rare Diseases, 2012 Definition of the disease AL amyloidosis results from extra-cellular deposition of fibril-forming monoclonal immunoglobulin (Ig) light chains (LC) (most commonly of lambda isotype) usually secreted by a small plasma cell clone.
Desport Estelle +13 more
doaj +10 more sources
Misdiagnosis of hereditary amyloidosis as AL (Primary) amyloidosis [PDF]
New England Journal of Medicine, 2002 Background: Hereditary, autosomal dominant amyloidosis, caused by mutations in the genes encoding transthyretin, fibrinogen A -chain, lysozyme, or apolipoprotein A-I, is thought to be extremely rare and is not routinely included in the differential ...
Booth, D.R. +7 more
core +8 more sources
Management of AL amyloidosis in 2020. [PDF]
Hematology, 2020 In amyloid light chain (AL) amyloidosis, a small B-cell clone, most commonly a plasma cell clone, produces monoclonal light chains that exert organ toxicity and deposit in tissue in the form of amyloid fibrils.
G. Palladini, P. Milani, G. Merlini
semanticscholar +9 more sources
Biomarkers in AL Amyloidosis [PDF]
International Journal of Molecular Sciences, 2021 Systemic AL amyloidosis is a rare complex hematological disorder caused by clonal plasma cells which produce amyloidogenic immunoglobulins. Outcome and prognosis is the combinatory result of the extent and pattern of organ involvement secondary to ...
D. Fotiou +2 more
semanticscholar +4 more sources
Epidemiology of AL amyloidosis: a real-world study using US claims data
Blood Advances, 2018 : Amyloid light-chain (AL) amyloidosis is a rare disease caused by extracellular deposition of misfolded immunoglobulin light chains. This study aimed to provide an up-to-date estimate of prevalence and incidence of AL amyloidosis in the United States ...
Tiffany P. Quock +4 more
doaj +2 more sources
A RARE PRESENTATION OF SYSTEMIC AL AMYLOIDOSIS; PULMONARY AL AMYLOIDOSIS
Hematology, Transfusion and Cell Therapy, 2022 Objective: Involvement of the lung is common in systemic AL amyloidosis in post-mortem series. However, the diagnosis is challenging. Histology is the gold standard but may result in bleeding. Consequently, diagnosis during life is rare.
Simge ERDEM +4 more
doaj +2 more sources
Chronic Viral Infections and Al Amyloidosis: An Uncommon Association [PDF]
Clinical Case ReportsAL‐amyloidosis is caused by deposition of pathological insoluble proteins in organs and tissues. HIV infection is a multi‐system disorder causing chronic inflammation.
Alberto Palladini +7 more
doaj +2 more sources