Results 141 to 150 of about 10,911,887 (292)

AA amyloidosis in the four historical monogenic autoinflammatory diseases: Clinical burden and insights from a retrospective referral‐centre study

Journal of Internal Medicine, EarlyView.
Abstract Background AA amyloidosis (AAA) remains a life‐threatening yet largely preventable complication of monogenic autoinflammatory diseases (AIDs). Methods We retrospectively described patients with AAA secondary to one of the four historical monogenic AIDs (familial Mediterranean fever [FMF], cryopyrin‐associated periodic syndrome [CAPS ...
Majdouline El Moussaoui, Léa Savey, Hassina Sofia Aloui‐Belhocine, Jean‐Jacques Boffa, Marion Delplanque, Catherine Grandpeix‐Guyodo, Irina Giurgea, Laurence Cuisset, Guilaine Boursier, Gilles Grateau, David Buob, Sophie Georgin‐Lavialle   +11 more
wiley   +1 more source

Clinical clues for suspecting wild-type transthyretin cardiac amyloidosis in patients with monoclonal gammopathy of undetermined significance: a case report

The Egyptian Heart Journal
Background Myeloproliferative disorders, including monoclonal gammopathy of undetermined significance (MGUS), are often associated with amyloid light-chain (AL)-type cardiac amyloidosis (CA) but occasionally with wild-type transthyretin (ATTR) CA.
Tomoaki Haga, Takahiro Okumura, Yasuhiko Harada, Hiroaki Hiraiwa, Ryota Morimoto, Shinji Kaneko, Nagaaki Kato, Masanori Shinoda, Toyoaki Murohara   +8 more
doaj   +1 more source

Renal and Functional Vulnerability in Hansen Disease: A Framework for Chronic Infectious Disability in Endemic Settings

Tropical Medicine &International Health, EarlyView.
ABSTRACT Objectives Hansen disease is a neglected infectious disease associated with reactional inflammation, neuropathy and long‐term disability. Renal involvement and sarcopenia have been described separately, but their clinical coexistence has received limited attention. This review examines evidence for a hypothesised renal–functional vulnerability
Kleberson de Oliveira, Lucas Maciel de Almeida Corrêa, Isabela Malerba Pinheiro, Alexandre de Assis Barbosa, Maria Eduarda Castro Gonçalves, Lara Lucena Fernandes Filgueiras, Lara Reis Gomes de Mello Queiroz   +6 more
wiley   +1 more source

Epidemiology of Systemic Light-Chain (AL) Amyloidosis

Systemic light-chain (AL) amyloidosis is a challenging, complex and heterogeneous disease. AL amyloidosis is classified under the category of plasma cell neoplasms and other diseases with paraproteins in the fifth edition of the World Health Organization
Rafael Ríos-Tamayo
core   +1 more source

Clinical Outcomes of Colorectal Endoscopic Full‐Thickness Resection Using the Full‐Thickness Resection Device: A Multicenter Study

DEN Open, Volume 7, Issue 1, April 2027.
ABSTRACT Background Endoscopic full‐thickness resection (EFTR) using the full‐thickness resection device (FTRD) is an emerging technique for the management of complex colorectal lesions and early colorectal cancers. Although EFTR offers a minimally invasive alternative to surgery, data on efficacy, safety, and predictors of adverse events (AEs) remain ...
Vicki McGarrigle, Yuto Shimamura, Leonardo Zorron Cheng Tao Pu, Marios Efthymiou, Rhys Vaughan, Cameron Schauer, Anurag Sekra, Erin Horsfall, Alexandra Simpson, Rajvinder Singh, Nicholas Wan, Milan Bassan, Martin Harb, Ben Terkasher, Frank Weilert, Saurabh Gupta, Kwang Chien Yee, Rajan Patel, Ibrahim Hassan, Byron Theron, Sujievvan Chandran   +20 more
wiley   +1 more source

AA Amyloidosis and AL Amyloidosis.

Internal Medicine, 1993
openaire   +3 more sources

Specific therapeutic options for transthyretin amyloidosis

The epidemiology of systemic amyloidosis has recently undergone a spectacular transformation. While light-chain amyloidosis remains a rare disease with a stable incidence, chronic inflammatory disease associated amyloidosis (AA) is diagnosed less ...
Zoltán Pozsonyi
core   +1 more source

POEMS Syndrome: 2026 Update on Diagnosis, Risk‐Stratification, and Management

American Journal of Hematology, Volume 101, Issue 10, Page 2632-2651, October 2026.
ABSTRACT Disease Overview POEMS syndrome is a life‐threatening syndrome due to an underlying plasma cell neoplasm. The major criteria for the syndrome are polyneuropathy, clonal plasma cell disorder (PCD), sclerotic bone lesions, elevated vascular endothelial growth factor, and the presence of Castleman disease.
Angela Dispenzieri
wiley   +1 more source

AL amyloidosis [PDF]

, 2020
openaire   +3 more sources

The Status Que of Leadership Succession Planning at Al al-Bayt University from Faculty Members’ Points of View [PDF]

هدفت الدراسة التعرف إلى واقع التخطيط للتعاقب القيادي في جامعة آل البيت من وجهة نظر أعضاء هيئة التدريس، وأثر متغيرات (الجنس، وسنوات الخدمة، والرتبة الأكاديمية، والكلية). وتكونت عينة الدراسة من (165) عضو هيئة تدريس تم اختيارهم بالطريقة العشوائية ...
Al-Shorofat, Musalm, Al-Hawamdeh, Mohammed, Al-Meqdadi, Mahmoud   +2 more
core   +1 more source