Results 181 to 190 of about 181,705 (382)

Brief Report: Amyloidosis Associated with Cyclic Neutropenia in the Dog [PDF]

, 1968
N. F. Cheville
openalex   +1 more source

Nonbiopsy Diagnosis of Cardiac Transthyretin Amyloidosis

Circulation, 2016
J. Gillmore, M. Maurer, R. Falk, G. Merlini, T. Damy, A. Dispenzieri, A. Wechalekar, J. Berk, C. Quarta, M. Grogan, H. Lachmann, S. Bokhari, Adam Castaño, S. Dorbala, Geoff B. Johnson, A. Glaudemans, T. Rezk, M. Fontana, G. Palladini, P. Milani, P. Guidalotti, Katarina Flatman, T. Lane, Frederick W. Vonberg, C. Whelan, J. Moon, F. Ruberg, E. Miller, D. Hutt, B. Hazenberg, C. Rapezzi, P. Hawkins   +31 more
semanticscholar   +1 more source

Skeletal muscle and subcutaneous fat quantity as prognostic indicators in cardiac amyloidosis

European Journal of Heart Failure, EarlyView.
Aims Disease‐related changes in body composition are associated with worse outcomes in chronic heart failure. In cardiac amyloidosis (CA), the prognostic value of direct body composition measures is understudied. Methods and results We identified 160 consecutive patients with CA (transthyretin [ATTR] or light chain [AL]) diagnosed between 2001 and 2021
Joshua Longinow, Saeid Mirzai, Po‐Hao Chen, Mazen Hanna, W.H. Wilson Tang   +4 more
wiley   +1 more source

Improving genetic testing pathways for transthyretin amyloidosis in France: challenges and strategies

Orphanet Journal of Rare Diseases
Transthyretin amyloidosis (ATTR) is a severe and rare disease characterized by the progressive deposition of misfolded transthyretin proteins, causing irreversible organ damage.
Bérénice Hebrard, Marie-Lise Babonneau, Philippe Charron, Emilie Consolino, Benjamin Dauriat, Delphine Dupin-Deguine, Dominique Fargeaud, Agnès Farrugia, Anna-Gaëlle Giguet-Valard, Damien Guijarro, Jocelyn Inamo, Julien Jeanneteau, Jean-Michaël Mazzella, Claire-Cécile Michon, Gilles Millat, Frédéric Mouquet, Silvia Oghina, Yann Pereon, Vianney Poinsignon, Julie Pompougnac, Julie Proukhnitzky, Elise Schaefer, Franck Sturtz, Mathilde Trosdorf, Anne Auguste, Giorgia Canali, Alexandre Combes, Benoît Funalot, Thibaud Damy   +28 more
doaj   +1 more source

ASNC/AHA/ASE/EANM/HFSA/ISA/SCMR/SNMMI expert consensus recommendations for multimodality imaging in cardiac amyloidosis: Part 1 of 2—evidence base and standardized methods of imaging

Journal of Nuclear Cardiology, 2019
S. Dorbala, Y. Ando, S. Bokhari, Angela Dispenzieri, Rodney H. Falk, Victor A. Ferrari, M. Fontana, O. Gheysens, J. Gillmore, A. Glaudemans, Mazen Hanna, B. Hazenberg, A. Kristen, Raymond Y. Kwong, M. S. Maurer, G. Merlini, Edward J Miller, James C. Moon, Venkatesh L Murthy, C. Quarta, C. Rapezzi, F. Ruberg, Sanjiv J. Shah, R. Slart, H. Verberne, J. Bourque   +25 more
semanticscholar   +1 more source

Clinical and plasma proteomic characterization of heart failure with supranormal left ventricular ejection fraction: An emerging entity of heart failure

European Journal of Heart Failure, EarlyView.
Heart failure (HF) with supranormal ejection fraction (HFsnEF) is an unnoticed but emerging entity in HF. This study showed that HFsnEF carries a similarly increased cardiovascular risk as HF with reduced ejection fraction (HFrEF) and distinct structural and proteomic characteristics from HFrEF, warranting a further comprehensive understanding and ...
Yasuhiko Sakata, Kotaro Nochioka, Satoshi Yasuda, Koichi Ishida, Takashi Shiroto, Jun Takahashi, Shintaro Kasahara, Ruri Abe, Shinsuke Yamanaka, Takahide Fujihashi, Hideka Hayashi, Shintaro Kato, Katsunori Horii, Kanako Teramoto, Tsutomu Tomita, Satoshi Miyata, Koichiro Sugimura, Iwao Waga, Masao Nagasaki, Hiroaki Shimokawa   +19 more
wiley   +1 more source

Long‐term efficacy of tafamidis in patients with transthyretin amyloid cardiomyopathy by National Amyloidosis Centre stage

European Journal of Heart Failure, EarlyView.
Long‐term efficacy of tafamidis in patients with ATTR‐CM in ATTR‐ACT and its LTE by NAC stage at ATTR‐ACT baseline. ATTR‐ACT, Tafamidis in Transthyretin Cardiomyopathy Clinical Trial; ATTR‐CM, transthyretin amyloid cardiomyopathy; NAC, National Amyloidosis Centre.
Thibaud Damy, Rong Wang, Mathew S. Maurer, Julian D. Gillmore, Marianna Fontana   +4 more
wiley   +1 more source

Familial Mediterranean fever in northwest of Iran (Ardabil): The first global report from Iran [PDF]

Familial Mediterranean fever (FMF), which is the prototype of the hereditary periodic fever syndromes, is common in the countries around the Mediterranean Sea. Considering its geographical position in the northwest of Iran, with its population of Turkish
امامی, دینا, براک, منوچهر, بشردوست, بهمن, جستان, مارینا, حبیب زاده, شهرام, خلفی, جعفر, ذولفقاری, علی اصغر, صالح زاده, فرهاد, عظیمی, هرمز, فیضی, ایرج, یزدانبد, عباس   +10 more
core  

Amyloidosis in paraplegia [PDF]

, 1963
Alessia Maglio, P Potenza
openalex   +1 more source

Sex‐based differences in heart failure management and outcomes: Insights from the French‐DataHF cohort

European Journal of Heart Failure, EarlyView.
Sex differences in heart failure (HF) management and outcomes in the French‐DataHF cohort. CI, confidence interval; HFH, heart failure hospitalization; HR, hazard ratio; IPW, inverse probability weighting; KM, Kaplan–Meier; LD, loop diuretic; RAS, renin–angiotensin system; RASi, renin–angiotensin system inhibitor.
Guillaume Baudry, Ouarda Pereira, François Roubille, Marc Villaceque, Thibaud Damy, Kevin Duarte, Philippe Tangre, Nicolas Girerd   +7 more
wiley   +1 more source