Results 11 to 20 of about 23,719 (217)
Hereditary angioedema type III (estrogen-dependent) report of three cases and literature review* [PDF]
Anais Brasileiros de Dermatologia, 2013 In this article, three cases of hereditary angioedema (HAE) type III (estrogen-dependent or with normal C1 inhibitor) are reported. The HAE was initially described in women of the same family in association with high-leveled estrogenic conditions such as
Amanda Rodrigues Miranda +5 more
doaj +1 more source
Frontiers in Immunology, 2021 It has been hypothesized that low levels of C1 esterase inhibitor (C1-INH), a key inhibitor of the complement pathway, may play a role in the occurrence of adverse events (AEs) associated with intravenous immunoglobulin (IVIG) therapy.
Isaac R. Melamed +3 more
doaj +1 more source
Physician awareness and understanding of hereditary angioedema: A web‐based study in Japan
Journal of Cutaneous Immunology and Allergy, 2022 Objectives Hereditary angioedema (HAE) is a rare disease with acute attacks in the skin and mucosa throughout the body including life‐threatening laryngeal edema and abdominal attacks with severe pain.
Atsushi Fukunaga +6 more
doaj +1 more source
Optimum Use of Acute Treatments for Hereditary Angioedema: Evidence-Based Expert Consensus
Frontiers in Medicine, 2018 Acute treatment of hereditary angioedema due to C1 inhibitor deficiency has become available in the last 10 years and has greatly improved patients’ quality of life.
Hilary Longhurst
doaj +1 more source
The World Allergy Organization Journal, 2022 Hereditary Angioedema (HAE) is a rare and disabling disease. Early diagnosis and appropriate therapy are essential. This update and revision of the global guideline for HAE provides up-to-date consensus recommendations for the management of HAE.
M. Maurer +58 more
semanticscholar +1 more source
International Journal of Emergency Medicine, 2021 A 14-year-old African American female presented to the emergency department with spontaneous, sudden-onset lip swelling for 1 h. On examination, there was significant water-bag edema of the upper lip extending to the philtrum and premaxilla ...
Helen Lesser, Jason E. Cohn
semanticscholar +1 more source
Hereditary Angioedema: Diagnosis, Clinical Implications, and Pathophysiology
Advances in Therapy, 2023 Hereditary angioedema (HAE) is an autosomal dominant disorder caused by a mutation in the C1 esterase inhibitor gene. HAE affects 1/50,000 people worldwide. Three main types of HAE exist: type I, type II, and type III.
Evan S Sinnathamby +9 more
semanticscholar +1 more source
Abstracts of 11th C1-inhibitor Deficiency & Angioedema Workshop
Allergy, Asthma & Clinical Immunology, 2019 s of 11th C1-inhibitor Deficiency & Angioedema Workshop Hungary, 23–26 May 2019 Published: 13 August 2019 © The Author(s) 2019. This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http ...
Edward Duckworth +20 more
semanticscholar +1 more source
Angioedema--assessment and treatment.
Tidsskrift for Den Norske Laegeforening, 2012 BACKGROUND Angioedema has numerous hereditary, acquired and iatrogenic causes. A number of studies show that angioedema is inadequately assessed and treated during its acute phase as well as in the follow-up period.
Eva Rye Rasmussen +2 more
semanticscholar +1 more source
Acta Médica Portuguesa, 2019 Introduction: Hospitalizations due to angioedema are important especially in debilitating or life-threatening situations. The aim of this study was to evaluate the frequency and etiology of angioedema without urticaria in hospital admissions.
Joana Cosme +3 more
doaj +1 more source