Results 41 to 50 of about 32,506 (196)

Demographic features of patients with AA and ATTR amyloidosis and those without amyloidosis.

, 2022
Demographic features of patients with AA and ATTR amyloidosis and those without amyloidosis.
Yuki Sugiura (200083), Yukako Shintani-Domoto (9073470), Makiko Ogawa (8697648), Takashi Sakatani (13961793), Ryuji Ohashi (724386), Masashi Fukayama (154693), Tetsuo Ushiku (2633257), Hiroyuki Abe (633475), Eiji Sugiyama (440676)   +8 more
core   +1 more source

Multimodality assessments of wild‐type transthyretin cardiac amyloidosis with no ventricular hypertrophy

ESC Heart Failure, 2023
While patients with transthyretin cardiac amyloidosis (ATTR‐CA) typically present with concentric or asymmetric hypertrophy, a small percentage of ATTR‐CA is known to present with ‘atypical’ cardiac morphologies such as eccentric hypertrophy or even no ...
Takuma Iwaya, Atsushi Okada, Emi Tateishi, Yasutoshi Ohta, Yoshiaki Morita, Keiko Ohta‐Ogo, Chisato Izumi   +6 more
doaj   +1 more source

Strong positive light chain immunostaining in a patient with transthyretin amyloidosis

Hematology, 2023
The two most common systemic amyloidosis types are immunoglobulin light chain (AL) and amyloid transthyretin (ATTR) amyloidosis, in which the precursor proteins responsible for amyloidosis are light chain and transthyretin, respectively.
Jiao Chen, Haifei Chen, Lingyun Zhou, Danbo Liu, Fang Du, Hongxian Xiang   +5 more
doaj   +1 more source

Electrophysiological demyelinating features in hereditary ATTR amyloidosis [PDF]

Amyloid, 2019
To elucidate the electrophysiological demyelinating features in patients with hereditary ATTR amyloidosis that may lead to a misdiagnosis of chronic inflammatory demyelinating polyneuropathy (CIDP).In 102 patients with hereditary ATTR amyloidosis (85 Val30Met and 17 non-Val30Met; 37 and 65 from endemic and non-endemic areas, respectively), results of ...
Nobuhiko, Ohashi, Minori, Kodaira, Hiroshi, Morita, Yoshiki, Sekijima   +3 more
openaire   +2 more sources

Amyloid fibrils containing fragmented ATTR may be the standard fibril composition in ATTR amyloidosis.

, 2013
The clinical phenotype of familial ATTR amyloidosis depends to some extent on the particular mutation, but differences exist also within mutations. We have previously described that two types of amyloid fibril compositions exist among Swedish ATTRV30M ...
Ikeda SI, Tasaki M, Benson MD, LEONE, ORNELLA, RAPEZZI, CLAUDIO, QUARTA, CANDIDA CRISTINA, Ueda M, LORENZINI, MASSIMILIANO, Ohshima T, Yamashita T, Obici L, Ihse E, Liepnieks J, Lavatelli F, Jono H, Ando Y, MERLINI, GIOVANNI, Suhr OB, Westermark P.   +18 more
core   +2 more sources

Prevalence and incidence of amyloid transthyretin amyloidosis in the USA: insights from claims databases and electronic health records

Open Heart
Background Amyloid transthyretin (ATTR) amyloidosis is a rare, life-threatening disease frequently manifesting with cardiomyopathy (ATTR-CM), polyneuropathy (ATTR-PN) or both (ATTR-mixed).
Xiaolei Li, Pedro A Laires, Aishwarya M Uday, Candida Cristina Quarta, Ana Martins Silva   +4 more
doaj   +1 more source

Urinary Biomarkers for Kidney Disease in ATTR Amyloidosis [PDF]

, 2014
Aim: The detection and prognosis of nephropathy in transthyretin amyloidosis depends on albuminuria and renal function. Knowing that urinary levels of alpha-1 microglobulin and beta-2 microglobulin reflect tubular dysfunction while urinary alpha-2 ...
Bravo, F., Oliveira, J., Rocha, A., Beirão, I., Vizcaíno, J., Lobato, L.   +5 more
core   +1 more source

Contributions of Animal Models to the Mechanisms and Therapies of Transthyretin Amyloidosis

Frontiers in Physiology, 2019
Transthyretin amyloidosis (ATTR amyloidosis) is a fatal systemic disease caused by amyloid deposits of misfolded transthyretin, leading to familial amyloid polyneuropathy and/or cardiomyopathy, or a rare oculoleptomeningeal amyloidosis.
Ridwan Babatunde Ibrahim, Ridwan Babatunde Ibrahim, Yo-Tsen Liu, Yo-Tsen Liu, Yo-Tsen Liu, Yo-Tsen Liu, Ssu-Yu Yeh, Jin-Wu Tsai, Jin-Wu Tsai   +8 more
doaj   +1 more source

Renal AA-amyloidosis in intravenous drug users - a role for HIV-infection? [PDF]

, 2012
Background: Chronic renal disease is a serious complication of long-term intravenous drug use (IVDU). Recent reports have postulated a changing pattern of underlying nephropathy over the last decades.
Grützmacher, Peter, Oliver Jung, Christoph Stephan, Markus Bickel, Peter Gruetzmacher, Kerstin Amann, Hans Stefan Haack, Jung, Oliver, Haack, Hans Stefan, Büttner, Maike, Stephan, Christoph, Bickel, Markus, Amann, Kerstin, Amann, Kerstin Ute, Betz, Christoph, Maike Buettner, Haack, Hans S., Christoph Betz   +17 more
core   +2 more sources

Non‐cardiac biopsy sites with high frequency of transthyretin amyloidosis

ESC Heart Failure, 2021
Aims Cardiac scintigraphy, a non‐invasive technique for diagnosing ATTR cardiac amyloidosis, lacks specificity in patients with concomitant monoclonal gammopathy (up to 40% of cases).
Surendra Dasari, Angela Dispenzieri, Shareef Mansour, Prasuna Muppa, Paul J. Kurtin, Jason D. Theis, Julie A. Vrana, Martha Grogan, Taxiarchis Kourelis, Morie A. Gertz, Ellen D. McPhail   +10 more
doaj   +1 more source