Results 111 to 120 of about 117,459 (333)

Development of a disease-specific quality of life questionnaire for adult patients with hereditary angioedema due to C1 inhibitor deficiency (HAE-QoL): Spanish multi-centre research project [PDF]

, 2012
BACKGROUND: There is a need for a disease-specific instrument for assessing health-related quality of life in adults with hereditary angioedema due to C1 inhibitor deficiency, a rare, disabling and life-threatening disease.
Carmen Gómez-Traseira, Carmen Marcos, Concepción López-Serrano, Dolores Hernández de Rojas, Eduardo Remor, Javier Contreras, Mar Guilarte, María Rubio, Miguel Tejedor-Alonso, Nieves Prior, Rosario Cabañas, Stefan Cimbollek, Teresa Caballero, Teresa González-Quevedo, Victoria Cardona, Ángel Campos   +15 more
core   +1 more source

Biopolymer‐Templated Hierarchical 3D‐Structured Gold Nanoparticle/Graphene Oxide Hybrid Materials for Ultrasensitive Surface‐Enhanced Raman Scattering

Advanced Functional Materials, EarlyView.
A scalable bio‐templated approach using spray‐coating and thermal annealing fabricates cellulose nanofibril (CNF) films loaded with gold nanoparticles (Au NPs) and graphene oxide (GO) hybrids as Surface‐enhanced Raman scattering (SERS) substrates. The 3D CNF network ensures uniform Au NPs distribution, while annealing induces more hotspots, confirmed ...
Yingjian Guo, Guangjiu Pan, Suo Tu, Yusuf Bulut, Jungui Zhou, Arno Jeromin, Thomas F. Keller, Andreas Stierle, Gergely Nemeth, Ferenc Borondics, Benedikt Sochor, Sarathlal Koyiloth Vayalil, L. Daniel Söderberg, Peter Müller‐Buschbaum, Stephan V. Roth   +14 more
wiley   +1 more source

Vasculopathy: a possible factor affecting hereditary angioedema

Bleeding, Thrombosis and Vascular Biology
Hereditary angioedema (HAE) is a rare genetic disorder that causes swelling of tissues in the hands, feet, limbs, face, intestinal tract, or airway. The SERPING1 gene, encoding the C1-INH, determines the wide range of clinical symptoms associated with ...
Anna Laura Colia, Alessandra Ranaldi, Rosa Santacroce, Giovanna D'Andrea, Angela Bruna Maffione, Maurizio Margaglione, Maria D'Apolito   +6 more
doaj   +1 more source

Recurrent Angioedema with Abdominal and Genital Involvement in Childhood: Hereditary Angioedema Type 2 Disease due to C1 Inhibitor Functional Deficiency

İstanbul Medical Journal, 2020
Hereditary angioedema is a rare disorder characterized by recurrent angioedema attacks due to C1 inhibitor antigen or functional deficiency. Here, two cases with recurrent swelling on extremities, genital organs and face that were later diagnosed with C1
Öner Özdemir, Halime Çiçek
doaj   +1 more source

Serum MASP-1 in complex with MBL activates endothelial cells. [PDF]

, 2014
The complement system plays an important role in the induction of inflammation. In this study we demonstrate that the initiation complexes of the lectin pathway, consisting of mannose-binding lectin (MBL) and associated serine proteases (MASPs) elicit ...
Ambrus, Balázs Major, Beinrohr, Dahl, Davis, Degn, Degn, Degn, Degn, Dobó, Dobó, Dobó, Endre Schwaner, Erika Kajdácsi, Gulla, Gál, Hansen, Heja, Heja, Hess, Jensenius, János Rigó, József Dobó, Kidmose, Kocsis, László Cervenak, Matsushita, Matsushita, Matsushita, Megyeri, Megyeri, Márton Megyeri, Møller-Kristensen, Oroszlán, Paréj, Paréj, Péter Gál, Péter K. Jani, Péter Závodszky, Ricklin, Saeed, Skjoedt, Steffen Thiel, Stover, Takahashi, Thiel, Thiel, Thiel, Thiel, Thiel, van der Pol   +50 more
core   +1 more source

A Scalable, Durable, Fire‐Safe All‐Day Passive Radiative Cooling Coating for Sustainable Buildings

Advanced Functional Materials, EarlyView.
This study reports a scalable, durable coating that combines a fire‑retardant copolymer adhesive, hollow glass microspheres, and boron oxide to achieve passive radiative cooling with over 94% solar reflectance and >95% mid‑infrared emissivity. The coating maintains performance after UV and rain exposure and exhibits UL‑94 V‑0 fire resistance, enabling ...
Zhewen Ma, Yuanhao Feng, Alex Y. Song, Toan Dinh, Min Hong, John Bell, Boyou Hou, Pingan Song, Wei Zheng   +8 more
wiley   +1 more source

Binding and Activation of Human C1 by Immune Complexes Effect of Inhibitors [PDF]

, 1978
G.J. Arlaud, Robert B. Sim, A. Reboul, Maurice G. Colomb   +3 more
openalex   +1 more source

Mechanism and therapy of hereditary angioedema typ III and role of the contact system in inflammatory diseases [PDF]

, 2014
Combinations of proinflammatory and procoagulant reactions are associated with a variety of disorders affecting the cardiovascular system. Vascular leakage contributes to the pathology of conditions such as, sepsis, allergy and anaphylactic reactions ...
Björkqvist, Jenny
core   +1 more source

Effect of 2D and 3D ECM and Biomechanical Cues on Human iPSC‐Derived Liver Progenitor Cell Differentiation

Advanced Healthcare Materials, EarlyView.
An engineered microtissue model is developed and optimized to investigate human liver development. Extracellular matrix composition and mechanical forces are tuned using high‐throughput assays. Human induced pluripotent stem cells serve as the cellular source, enabling the observation of de novo patterned differentiation.
Ishita Jain, Brock Grenci, Hyeon Ryoo, Yang Yuan, Salman R. Khetani, Gregory H. Underhill   +5 more
wiley   +1 more source

Acquired C1 inhibitor (C1-INH) deficiency type II. Replacement therapy with C1-INH and analysis of patients' C1-INH and anti-C1-INH autoantibodies. [PDF]

, 1989
Jochem Alsenz, John D. Lambris, Konrad Bork, Michael Loos   +3 more
openalex   +1 more source