Amyloidosis is a disease caused by the deposition of proteins with an unstable tertiary structure, which coagulate and accumulate in tissues as glycoprotein fibrils.
Nikita S. Averkin +4 more
doaj +1 more source
Advances in cardiac devices and bioelectronics augmented with artificial intelligence
Abstract figure legend Interfaces between the human heart, diagnostic bioelectronics, artificial intelligence, and clinical care. From left to right: Human heart and biosensor interface; representative waveforms of common diagnostic bioelectronic sensing modalities.
Charles Stark +3 more
wiley +1 more source
The frequency of cardiac amyloidosis in 182 patients receiving carpal tunnel release surgery [PDF]
Frederikke Hansen +14 more
openalex +1 more source
ABSTRACT Amyloidosis, characterized by the deposition of abnormal protein fibrils in organs, is classified as systemic or localized. Amyloid light chain (AL)‐type localized amyloidosis is uncommon, particularly when confined to the gastrointestinal tract.
Shunsuke Kojimahara +7 more
wiley +1 more source
Amyloidosis presenting as bilateral transudative pleural effusions with normal cardiac investigations: a case report [PDF]
A 66-year-old man with a diagnosis of monoclonal gammopathy of unknown significance was referred for investigation of bilateral transudative pleural effusions by the cardiology team.
James H Briggs +4 more
core +1 more source
Transthyretin Cardiac Amyloidosis Presenting as Bradycardia, Renal Failure, Atrioventricular-Nodal Blockade, Shock, and Hyperkalemia (BRASH) Syndrome: A Case Report [PDF]
Nazima Khatun +5 more
openalex +1 more source
This exploratory analysis of data from the NEURO‐TTRansform trial evaluated sex‐specific responses in patients with ATTRv‐PN who had received eplontersen in NEURO‐TTRansform versus a historical placebo. Eplontersen can lead to substantial decreases in percentage serum TTR levels, arrest neuropathy impairment, and improve patient quality of life ...
Márcia Waddington Cruz +11 more
wiley +1 more source
Afectación cardiovascular en la amiloidosis. Revisón de la literatura y puesta al día [PDF]
La amiloidosis es una enfermedad infiltrativa provocada por el depósito extracelular de material proteico fibrilar en los tejidos, existiendo formas localizadas y sistémicas. En esta última, destacan por su frecuencia la amiloidosis AL o primaria, que es
Rodrigo Manjón, Alejandro
core
Human Inborn Errors of Immunity: 2019 Update of the IUIS Phenotypical Classification. [PDF]
Since 2013, the International Union of Immunological Societies (IUIS) expert committee (EC) on Inborn Errors of Immunity (IEI) has published an updated phenotypic classification of IEI, which accompanies and complements their genotypic classification ...
Ailal, Fatima +18 more
core
Cardiac T1 Mapping and Extracellular Volume (ECV) in clinical practice: a comprehensive review. [PDF]
Cardiovascular Magnetic Resonance is increasingly used to differentiate the aetiology of cardiomyopathies. Late Gadolinium Enhancement (LGE) is the reference standard for non-invasive imaging of myocardial scar and focal fibrosis and is valuable in the ...
A Gulati +58 more
core +3 more sources

