Results 81 to 90 of about 29,456 (167)

Efficient transmission and characterization of creutzfeldt-jakob disease strains in bank voles.

PLoS Pathogens, 2006
Transmission of prions between species is limited by the "species barrier," which hampers a full characterization of human prion strains in the mouse model.
Romolo Nonno, Michele A Di Bari, Franco Cardone, Gabriele Vaccari, Paola Fazzi, Giacomo Dell'Omo, Claudia Cartoni, Loredana Ingrosso, Aileen Boyle, Roberta Galeno, Marco Sbriccoli, Hans-Peter Lipp, Moira Bruce, Maurizio Pocchiari, Umberto Agrimi   +14 more
doaj   +2 more sources

Wariant Choroby Creutzfeldta-Jakoba: aktualny stan wiedzy

Aktualności Neurologiczne, 2011
Choroby wywoływane przez priony obejmują: chorobę Creutzfeldta-Jakoba (Creutzfeldt-Jakob disease, CJD), kuru, chorobę Gerstmanna-Sträusslera-Scheinkera (GSS), śmiertelną rodzinną bezsenność (fatal familial insomnia, FFI) u człowieka, scrapie (polska ...
James W. Ironside
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Prion protein amyloidosis with divergent phenotype associated with two novel nonsense mutations in PRNP [PDF]

, 2009
Stop codon mutations in the gene encoding the prion protein (PRNP) are very rare and have thus far only been described in two patients with prion protein cerebral amyloid angiopathy (PrP-CAA).
Casper Jansen, Piero Parchi, Sabina Capellari, Ad J. Vermeij, Patrizia Corrado, Frank Baas, Rosaria Strammiello, Willem A. van Gool, John C. van Swieten, Annemieke J. M. Rozemuller, H Braak, V Campana, S Capellari, S Capellari, B Chesebro, U Finckh, P Gambetti, B Ghetti, B Ghetti, B Ghetti, B Ghetti, G Giaccone, F Gray, C Haass, J Hardy, SI Ikeda, JW Ironside, C Keohane, GR Mallucci, M Mohr, R Nitrini, S Notari, C Paquet, P Parchi, P Parchi, P Piccardo, T Revesz, F Tagliavini, J Tateishi, DR Thal, HV Vinters, S Vogelgesang, J Woulfe, M Yamada   +43 more
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Does Improvement in Case Ascertainment Explain the Increase in Sporadic Creutzfeldt-Jakob Disease Since 1970 in the United Kingdom? [PDF]

, 2017
The aim of this study was to quantify the improvements in case ascertainment which are considered to explain the rise in the incidence of sporadic Creutzfeldt-Jakob disease.
Cohen, Carine H.
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Neuroimagen estructural y funcional en las enfermedades priónicas humanas [PDF]

, 2011
INTRODUCTION: Prion diseases are neurodegenerative disorders resulting from the accumulation of a misfolded isoform of the cellular prion protein (PrPc). They can occur as acquired, sporadic or hereditary forms. Although prion diseases show a wide range
Arbizu, J. (Javier), Carmona-Abellan, M. (M.), Dominguez-Prado, I. (Inés), Luquin, M.R. (María Rosario), Ortega-Cubero, S. (Sara), Pagola, I. (I.), Riverol, M. (Mario)   +6 more
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Creutzfeldt-Jakob disease

Chinese Journal of Contemporary Neurology and Neurosurgery, 2013
Creutzfeldt⁃Jakob disease (CJD) is a degenerative central nervous system (CNS) disease caused by infection of prion protein (PrP), with clinical features including short course, rapid development and 100% mortality.
Lin WANG, Jian-rong LIU
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Complicated symptomatology and diagnosis of Creuzfeld-Jakob disease on a basis of clinical case

Quality in Sport
Creutzfeldt-Jakob disease (CJD) is a rare condition. In this study we describe the diagnosis of the disease in a 73-year old female, presenting dementia. Diagnostic tests unveiled characteristic features of CJD. The diagnosis of CJD was confirmed. It is
Marta Jurga, Katarzyna Kuśmierczyk, Patrycja Karkos, Hanna Gruszczyńska, Natalia Kuderska, Kacper Jurga, Ewa Okowińska, Aleksandra Cieślik, Klaudia Wojtyła, Jakub Lambrinow   +9 more
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BSE: Risk, Uncertainty, and Policy Change [PDF]

, 2002
The authors discuss how, in our risk society, a range of potential risks and uncertainties are associated with new technologies and new diseases, such as BSE.
Cummins, Enda, Grace, Pat, McDonnell, Kevin, Ward, Shane   +3 more
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Degeneração cortico-estriato-medular: relato de um caso com achados clínicos e patológicos sugestivos de doença de Creutzfeldt-Jakob Cortico-striate-spinal degeneration: report of a case with clinical and pathological findings suggestive of Creutzfeldt-Jakob disease

Arquivos de Neuro-Psiquiatria, 1976
É apresentado caso sugestivo de doença de Creutzfeldt-Jakob em adulto jovem. O estudo anátomo-patológico revelou alteração difusa no córtice cerebral, núcleos da base e medula, constituídas por degeneração neuronal, gliose, espongiose e infiltração ...
Osvaldo J. M. Nascimento, Marcos R. G. de Freitas   +1 more
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Mathematical Models for Estimating the Risk of vCJD Transmission [PDF]

, 2009
We present two different simple models for vCJD transmission by blood transfusion. Both models indicate that transfusions alone are unlikely to cause more than a few infections, unless the number of primary cases increases.
Anvari, V., Atapour, M., Bourouiba, L., Caudillo Mata, L. A., Collinson, S., Johnson, A., Madras, N., Miasnikof, P., Ramirez Ramirez, L. L., Sanchez-Bravo, I.   +9 more
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