Results 11 to 20 of about 12,150 (217)
Omalizumab for Pediatric Cutaneous Mastocytosis: Case Report and Review. [PDF]
ABSTRACT We report an 11‐month‐old boy with diffuse cutaneous mastocytosis whose severe pruritus and steroid dependence resolved following off‐label treatment with omalizumab. A literature review identified five additional pediatric cases in which omalizumab led to complete symptom resolution in an average of 2 months and permitted discontinuation of ...
Chang J, King A, Byrne A, Liy-Wong C.
europepmc +2 more sources
Review on cutaneous mastocytosis, with data on clinics, pathology, and involved genes.
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Clinical Cases: Diagnostic Errors of Mastocytosis Cutaneous Forms in Children
Background. Mastocytosis refers to the group of rare diseases with pathological mast cells accumulation in tissues. Although diagnosis of cutaneous mastocytosis is not usually difficult for experienced physicians, misdiagnosis is possible.Clinical cases ...
Lianna K. Aslamazyan +4 more
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Mastocytosis is a heterogeneous group of disorders in which mast cells exhibit clonal proliferation that infiltrates one or more organs. In cutaneous mastocytosis, the mast cells infiltrate the skin only, whereas systemic mastocytosis is diagnosed when ...
Awni Alshurafa +4 more
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PEDIATRIC MASTOCYTOSIS: AN UPDATE
Mastocytosis is a rare clonal disorder, characterized by excessive proliferation and accumulation of mast cells (MC) in various organs and tissues. Cutaneous mastocytosis (CM), the most common form in children, is defined when MC infiltration is limited ...
Fiorina Giona
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Cutaneous Mastocytosis in Children: Is It Just a Skin Disease?
Introduction: Mastocytosis is characterized by the excessive proliferation and accumulation of mast cells in organs such as the spleen, liver, lymph nodes, skin, gastrointestinal tract, and bone marrow.
Tuğba Aktürk +2 more
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Systemic Lymphadenopathic Mastocytosis with Eosinophilia
Systemic mastocytosis is a neoplastic proliferation of mast cells that most frequently involves cutaneous sites. Mastocytosis involves various extracutaneous sites, but the lymph node is rare.
Soyoung Im +3 more
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Pseudoxanthomatous diffuse cutaneous mastocytosis in a child [PDF]
Abnormal accumulation of mast cells in the skin is called cutaneous mastocytosis. Diffuse cutaneous mastocytosishas two clinical variants, pseudoxanthomatous/xanthelasmoid and bullous type. Childhood disease is mostly self limiting. This may sometimes be
Ritu Gujarati Vishwanath +2 more
doaj
Urticaria pigmentosa and systemic mastocytosis
Key Clinical Message Additional investigations for systemic involvement should be initiated once the diagnosis of cutaneous mastocytosis has been established in an adult patient.
Jonathan Keow +3 more
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Differential Diagnoses of Systemic Mastocytosis in Routinely Processed Bone Marrow Biopsy Specimens: A Review [PDF]
Diagnosis of systemic mastocytosis (SM) is mainly based on the morphological demonstration of compact mast cell infiltrates in various tissue sites. In almost all patients such infiltrates are detected in the bone marrow.
Horny, H. -P., Sotlar, K., Valent, P.
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