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Successful treatment of provisional cutaneous mastocytosis with interferon alpha
Mastocytosis is a disorder characterized by the clonal proliferation of mast cells and their accumulation in skin, bone marrow, liver, and spleen. Cutaneous mastocytosis presents in children in over 90% of the cases and any cutaneous manifestation in an ...
Andrea Rosario, Ramesh M Bhat
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Cutaneous mastocytosis in childhood. [PDF]
Mastocytoses are characterized by clonal proliferation of mast cells in various tissues. In childhood, cutaneous mastocytosis (CM) occurs almost exclusively. It is confined to the skin, and has a good prognosis. The most common form is the maculopapular cutaneous mastocytosis (MPCM), formerly called urticaria pigmentosa. A distinction is made between a
Nemat K, Abraham S.
europepmc +4 more sources
Mastocytosis is a condition characterized by the disorderly infiltration of mast cells in several tissues and comprises many different clinical situations varying from indolent cutaneous forms to malignant and systemic conditions. Bullous mastocytosis is
Nayak Surajit +3 more
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Avapritinib for Cutaneous Mastocytosis. [PDF]
Lee H +4 more
europepmc +4 more sources
Rare Clinical Image of Cutaneous Mastocytosis
Mastocytosis, a rare condition also referred to as a clonal bone marrow disorder, is characterised by an excessive presence of CD34+ mast cell progenitors and functionally impaired mast cells. This disorder can affect both adults and children, leading to
Shubham Khanke +3 more
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Cutaneous Mastocytosis – Clinical Heterogeneity
Cutaneous mastocytosis (CM) encompasses several distinct patterns of disease which can be distinguished by the type of skin lesions, age of onset, familial occurrence, noncutaneous involvement, associated c-kit mutations, and prognosis. A clear distinction of the type of CM in individual patients has important implications regarding patient management ...
Hartmann, Karin, Henz, Beate M.
openaire +4 more sources
PEDIATRIC MASTOCYTOSIS: AN UPDATE
Mastocytosis is a rare clonal disorder, characterized by excessive proliferation and accumulation of mast cells (MC) in various organs and tissues. Cutaneous mastocytosis (CM), the most common form in children, is defined when MC infiltration is limited ...
Fiorina Giona
doaj +1 more source
Cutaneous Mastocytosis in Children: Is It Just a Skin Disease?
Introduction: Mastocytosis is characterized by the excessive proliferation and accumulation of mast cells in organs such as the spleen, liver, lymph nodes, skin, gastrointestinal tract, and bone marrow.
Tuğba Aktürk +2 more
doaj +1 more source
KIT mutation analysis in mast cell neoplasms: recommendations of the European competence network on mastocytosis [PDF]
Although acquired mutations in KIT are commonly detected in various categories of mastocytosis, the methodologies applied to detect and quantify the mutant type and allele burden in cells and various tissues are poorly defined.
T. Haferlach +79 more
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Systemic Lymphadenopathic Mastocytosis with Eosinophilia
Systemic mastocytosis is a neoplastic proliferation of mast cells that most frequently involves cutaneous sites. Mastocytosis involves various extracutaneous sites, but the lymph node is rare.
Soyoung Im +3 more
doaj +1 more source

