Epidermolysis bullosa acquisita [PDF]
Anais Brasileiros De Dermatologia, 2022 Epidermolysis bullosa acquisita is a rare autoimmune disease, characterized by the synthesis of anti-collagen VII autoantibodies, the main component of hemidesmosome anchoring fibrils. The antigen-antibody binding elicits a complex inflammatory response,
Denise Miyamoto +2 more
exaly +10 more sources
Epidermolysis Bullosa Acquisita—Current and Emerging Treatments [PDF]
Journal of Clinical Medicine, 2023 Epidermolysis bullosa acquisita (EBA) is a rare chronic autoimmune subepidermal blistering disease of the skin and mucous membranes, usually beginning in adulthood.
Branka Marinović +1 more
exaly +4 more sources
Epidermolysis Bullosa Acquisita: The 2019 Update [PDF]
Frontiers in Medicine, 2019 Epidermolysis bullosa acquisita (EBA) is an orphan autoimmune disease. Patients with EBA suffer from chronic inflammation as well as blistering and scarring of the skin and mucous membranes.
Hiroshi Koga +2 more
exaly +5 more sources
Inhibition of interferon gamma impairs induction of experimental epidermolysis bullosa acquisita [PDF]
Frontiers in ImmunologyEpidermolysis bullosa acquisita (EBA) is a muco-cutaneous autoimmune disease characterized and caused by autoantibodies targeting type VII collagen (COL7). The treatment of EBA is notoriously difficult, with a median time to remission of 9 months.
Ralf Ludwig +2 more
exaly +5 more sources
Epidermolysis bullosa acquisita [PDF]
Vestnik Dermatologii i Venerologii, 2017 The article describes present-day information on the pathogenesis, clinical picture, treatment and differential diagnostics of epidermolysis bullosa acquisita, an autoimmune skin disease caused by the production of anti-Type VII collagen autoantibodies ...
V. V. Chikin +3 more
doaj +8 more sources
Epidermolysis bullosa acquisita treated with ustekinumab: A case report [PDF]
SAGE Open Medical Case Reports, 2022 Epidermolysis bullosa acquisita is a rare autoimmune disease involving cutaneous blistering and scarring associated with collagen VII autoantibodies.
Connor Prosty +4 more
doaj +3 more sources
Case Report: Biological treatment of epidermolysis bullosa acquisita: report on four cases and literature review [PDF]
Frontiers in Immunology, 2023 Epidermolysis bullosa acquisita (EBA) is a chronic, recurrent autoimmune subepidermal bullous disease characterized by the presence of autoantibodies targeting type VII collagen -- basement membrane zone antigen.
Konrad Szymański
exaly +3 more sources
Case Report: Diagnostic and Therapeutic Challenges in Severe Mechanobullous Epidermolysis Bullosa Acquisita [PDF]
Frontiers in Immunology, 2022 Collagen VII is the main constituent of the anchoring fibrils, important adhesive structures that attach the epidermis to the dermal extracellular matrix.
Franziska Schauer +9 more
doaj +3 more sources
Monocyte populations are involved in the pathogenesis of experimental epidermolysis bullosa acquisita [PDF]
Frontiers in Immunology, 2023 Monocytes play a significant role in the pathogenesis of most inflammatory diseases, including autoimmune diseases. Herein, different subpopulations of monocytes often play differential, partially antagonistic roles, in the regulation of tissue ...
Reza Akbarzadeh +7 more
doaj +3 more sources
Acute renal failure in a patient with epidermolysis bullosa acquisita [PDF]
Anais Brasileiros de Dermatologia, 2017 : Epidermolysis bullosa acquisita is a severe autoimmune subepidermal bullous disease. In this report, we described for the first time a patient with epidermolysis bullosa acquisita who developed acute renal failure.
Guowei Zhao, Qing Yang, Furen Zhang
doaj +3 more sources