Results 31 to 40 of about 1,292 (153)

Pemphigoid diseases in infancy and childhood. A review of the literature

Przegląd Dermatologiczny, 2023
Bullous pemphigoid is an autoimmune blistering disease that very rarely affects children. Clinical differences in locations of skin lesions led to the distinction of infantile versus childhood pemphigoid. Mucous membranes can be affected.
Magdalena Jałowska, Julia Jałowska, Marian Dmochowski   +2 more
doaj   +1 more source

Familial epidermolysis bullosa acquisita

Dermatology Online Journal, 2008
Epidermolysis bullosa acquisita (EBA) is an acquired blistering skin disorder caused by IgG autoantibodies directed against type VII collagen. In contrast to the genetic forms of epidermolysis bullosa, EBA is usually an acquired, sporadic disease. In this report, we describe a family with two cases of EBA in an uncle-nephew pair, and a third family ...
Noe, Megan H, Chen, Mei, Woodley, David T, Fairley, Janet A   +3 more
openaire   +4 more sources

Epidermolysis Bullosa (EB) Acquisita in an Adult Patient with Previously Unrecognized Mild Dystrophic EB and Biallelic COL7A1 Mutations

Acta Dermato-Venereologica, 2018
Circulating anti-type VII collagen autoantibodies are frequently detected in patients with recessive dystrophic epidermolysis bullosa (RDEB). However, evidence supporting their pathogenic role in inducing epidermolysis bullosa acquisita (EBA) has been ...
Liliana Guerra, Angelo Giuseppe Condorelli, Paola Fortugno, Valentina Calabresi, Cristina Pedicelli, Giovanni Di Zenzo, Daniele Castiglia   +6 more
doaj   +1 more source

Epidermólise bolhosa adquirida inflamatória: relato de caso Inflammatory epidermolysis bullosa acquisita: case report

Anais Brasileiros de Dermatologia, 2009
Apresenta-se caso de epidermólise bolhosa adquirida inflamatória. Paciente do sexo masculino, 53 anos, há seis meses com erupção vesicobolhosa pruriginosa sobre base eritematosa no tronco, axilas e membros.
Marcelo D'Ambrosio Fernandes, Mariana Discacciati Chiminazzo, Antonio José Tebcherani, Valéria Aoki, Ana Paula Galli Sanchez   +4 more
doaj   +1 more source

EndoS reduces the pathogenicity of anti-mCOL7 IgG through reduced binding of immune complexes to neutrophils. [PDF]

PLoS ONE, 2014
Endo-β-N-acetylglucosaminidase (EndoS) has been shown to act as a potent pathogen-derived immunomodulatory molecule in autoimmune diseases. Here we investigated how EndoS treatment reduces the pathogenicity of rabbit anti-mCOL7 IgG using different ...
Xinhua Yu, Junfeng Zheng, Mattias Collin, Enno Schmidt, Detlef Zillikens, Frank Petersen   +5 more
doaj   +1 more source

Lip swelling and constipation: Pretest probability of cutaneous signs for crohn's disease in the absence of typical gastrointestinal symptoms

Clinical Dermatology Review, 2020
We describe a female child in the first decade patient admitted to a children's hospital for lip swelling and constipation who was ultimately diagnosed with Crohn's disease.
Maggie L Chow, Minnelly Luu
doaj   +1 more source

Epidermolysis Bullosa Acquisita Occuring In A Patient With Systemic Lupus Erythematosus

Saintika Medika, 2019
Epidermolysis Bullosa Acquisita (EBA) is a rare, chronic autoimmune subepidermal bullous disease and has been noted to be associated with systemic lupus erythematosus (SLE). The incidence of EBA and SLE in one patient within the period of 1980-1990 found
Lita setyowatie, Yustian Devika Rahmawati, Arif Widiatmoko, Diah Prabawati Retnani   +3 more
doaj   +1 more source

Bullous Pemphigoid and Other Pemphigoid Dermatoses

Medicina, 2021
The pemphigoid family of dermatoses is characterized by autoimmune subepidermal blistering. The classic paradigm for pemphigoid, and the most common member, is bullous pemphigoid.
Valeryia Pratasava, Vikram N. Sahni, Aishwarya Suresh, Simo Huang, Abhirup Are, Sylvia Hsu, Kiran Motaparthi   +6 more
doaj   +1 more source

Excellent response to rituximab in a patient with recalcitrant epidermolysis bullosa acquisita: a case report

Journal of the Egyptian Women’s Dermatologic Society
Epidermolysis Bullosa Acquisita is a rare, chronic autoimmune blistering disorder characterized by vesicles and bullae on the skin and mucous membranes.
Fahad Alrashidi, Khalid Nabil Nagshabandi, Ruaa Alharithy   +2 more
doaj   +1 more source

Porphyria Cutanea Tarda Masquerading as Epidermolysis Bullosa Acquisita: A Report of Two Cases

Case Reports in Dermatology, 2015
Porphyria cutanea tarda (PCT) is the most common type of porphyria worldwide and is often initially diagnosed when cutaneous manifestations arise.
Kristyn Deen, Jason Wu
doaj   +1 more source