Results 91 to 100 of about 1,017,855 (122)

Innovative Use of Denver Shunt in a Child With Generalized Lymphatic Anomaly

Journal of Laparoendoscopic and Advanced Surgical Techniques - Part A, 2017
Denver® shunts have traditionally been used for palliation of refractory malignant and chylous peritoneal and pleural collections. We describe an innovative use of the Denver shunt in a child with generalized lymphatic anomaly.Retrospective chart review of a 6-year-old girl with generalized lymphatic anomaly, who presented with refractory lymphorrhea ...
Sheena Pimpalwar, Ionela Iacobas, Ashwin Pimpalwar   +2 more
exaly   +3 more sources

Generalized Lymphatic Anomaly Successfully Treated With Long-Term, Low-Dose Sirolimus

Pediatric Dermatology, 2018
AbstractGeneralized lymphatic anomaly is a rare, complex, lymphatic anomaly generally involving soft tissues, spleen, and bones. It can lead to focal skeletal fragility and pathologic effusions. A recent prospective trial of sirolimus for complicated vascular anomalies showed partial response in seven patients with generalized lymphatic anomaly treated
Veronika Dvorakova, Alan D. Irvine
exaly   +3 more sources

Somatic NRAS mutation in patient with generalized lymphatic anomaly

Angiogenesis, 2018
Generalized lymphatic anomaly (GLA or lymphangiomatosis) is a rare disease characterized by a diffuse proliferation of lymphatic vessels in skin and internal organs. It often leads to progressive respiratory failure and death, but its etiology is unknown. Here, we isolated lymphangiomatosis endothelial cells from GLA tissue.
Eugenia, Manevitz-Mendelson, Gil S, Leichner, Ortal, Barel, Inbal, Davidi-Avrahami, Limor, Ziv-Strasser, Eran, Eyal, Itai, Pessach, Uri, Rimon, Aviv, Barzilai, Abraham, Hirshberg, Keren, Chechekes, Ninette, Amariglio, Gideon, Rechavi, Karina, Yaniv, Shoshana, Greenberger   +14 more
openaire   +2 more sources

Generalized Lymphatic Anomaly: A Case Report and Review of Literature

Journal of Cutaneous Pathology
AbstractGeneralized lymphatic anomaly (GLA), previously known as lymphangiomatosis, is a rare developmental disease characterized by abnormal proliferation of lymphatic vascular structures that may involve the dermis, soft tissue, bone, and visceral parenchyma.
Asmaâ M Ahmed, Eman R M Hofny, Alaa Ghazally   +2 more
exaly   +3 more sources

Gorham-Stout disease and generalized lymphatic anomalies

Seminars in Arthritis and Rheumatism, 2013
We postulate that there exist two distinct lymphatic malformation disorders that affect bones and cause significant morbidity and mortality. Gorham-Stout disease (G-SD) is characterized by the progressive disappearance of trabecular and cortical bone.
Cameron C. Trenor, Matthew L. Warman
openaire   +1 more source

Craniofacial CT findings of Gorham–Stout disease and generalized lymphatic anomaly

Neuroradiology, 2016
The present study aimed to assess the craniofacial CT imaging features for differentiating between Gorham-Stout disease (GSD) and generalized lymphatic anomaly (GLA).Seven patients with GSD and four patients with GLA were included in this study. All patients underwent CT examinations that encompassed the craniofacial bones.
Hiroki, Kato, Michio, Ozeki, Toshiyuki, Fukao, Masayuki, Matsuo   +3 more
openaire   +2 more sources

Gorham-Stout Disease and Generalized Lymphatic Anomaly—Clinical, Radiologic, and Histologic Differentiation

Skeletal Radiology, 2013
Gorham-Stout disease (GSD) is a rare vascular disorder of lymphatic origin characterized by progressive osteolysis. Generalized lymphatic anomaly (GLA) is a multisystem disorder that also commonly affects bone. We hypothesized that Gorham-Stout disease is different from other osseous lymphatic anomalies.
Steven J Fishman, Shailee V Lala, Ahmad I. Alomari   +2 more
exaly   +3 more sources

Sirolimus Therapy in Generalized Lymphatic Anomaly With Tuberculosis: A Case Report

Pediatric Pulmonology
ABSTRACT We report the case of a critically sick previously healthy 14‐year‐old girl who presented with subacute dry cough, respiratory distress, chest pain, hepatosplenomegaly, lytic bone lesions, splenic involvement, and bilateral chylothorax.
Kamal K, Singhal, Piali, Mandal, Varinder, Singh, Sonica, Singh, Pooja, Abbey, Vikas, Yadav, Pratap Singh, Yadav   +6 more
openaire   +2 more sources

First International Conference on Generalized Lymphatic Anomaly and Gorham–Stout Syndrome

IBMS BoneKEy, 2013
Gorham–Stout syndrome (GSS) is a rare disease of unknown etiology characterized by intraosseous lymphatic vessels and massive osteolysis. Generalized Lymphatic Anomaly (GLA, also known as lymphangiomatosis) is a related disease that features an increase in the number of lymphatic vessels in affected tissues and commonly affects bones.
Michael T Dellinger, Nupur Garg, Tiffany Ferry, Jack Kelly, Bjorn R Olsen   +4 more
openaire   +1 more source

Peritoneovenous shunt as a palliative option in generalized lymphatic anomaly

Pediatrics International, 2021
Noriko Fuke, Sae Nishisho, Aya Tanaka, Ryuichi Shimono, Takashi Kusaka   +4 more
openaire   +2 more sources