Results 131 to 140 of about 1,002,705 (170)

The glgB-encoded glycogen branching enzyme is essential for glycogen accumulation in Corynebacterium glutamicum

open access: yesMicrobiology, 2011
Corynebacterium glutamicum transiently accumulates glycogen as carbon capacitor during the early exponential growth phase in media containing carbohydrates. In some bacteria glycogen is synthesized by the consecutive action of ADP-glucose pyrophosphorylase (GlgC), glycogen synthase (GlgA) and glycogen branching enzyme (GlgB).
Gerd M, Seibold   +6 more
openaire   +3 more sources

Characterization of the branching patterns of glycogen branching enzyme truncated on the N-terminus

Archives of Biochemistry and Biophysics, 2003
Truncation of 112 amino acids at the N-terminus (Nd(1-112)) changes the chain transfer pattern of the Escherichia coli glycogen branching enzyme (GBE) [Arch. Biochem. Biophys. 397 (2002) 279]. We investigated further the role of the N-terminus by engineering other truncated GBEs and analyzing the branching pattern by high-performance anion-exchange ...
Miguel A Ballicora   +2 more
exaly   +3 more sources

Glycogen branching enzyme (GBE1) mutation causing equine glycogen storage disease IV

open access: yesMammalian Genome, 2004
Comparative biochemical and histopathological evidence suggests that a deficiency in the glycogen branching enzyme, encoded by the GBE1 gene, is responsible for a recently identified recessive fatal fetal and neonatal glycogen storage disease (GSD) in American Quarter Horses termed GSD IV.
Ward, T.   +5 more
openaire   +4 more sources

Human Skeletal Muscle Glycogen Branching Enzyme Activities with Exercise and Training

open access: yesCanadian Journal of Physiology and Pharmacology, 1974
Sixteen healthy male subjects classified as sedentary (8) or active (8), exercised to exhaustion on a bicycle ergometer at a load requiring 70% of their maximal aerobic capacity. Biopsy samples of the vastus lateralis muscle were taken at rest and at the time of fatigue.
A W, Taylor   +4 more
openaire   +3 more sources

Cloning and characterization of the glycogen branching enzyme gene existing in tandem with the glycogen debranching enzyme from Pectobacterium chrysanthemi PY35

Biochemical and Biophysical Research Communications, 2003
The glycogen branching enzyme gene (glgB) from Pectobacterium chrysanthemi PY35 was cloned, sequenced, and expressed in Escherichia coli. The glgB gene consisted of an open reading frame of 2196bp encoding a protein of 731 amino acids (calculated molecular weight of 83,859Da).
Han Dae Yun   +2 more
exaly   +3 more sources

Glycogen Storage Disorder due to Glycogen Branching Enzyme (GBE) Deficiency: A Diagnostic Dilemma

Ultrastructural Pathology, 2015
Glycogen branching enzyme deficiency/Andersen disease can manifest with a spectrum of clinical phenotypes, making the diagnosis difficult. An 11-year-old Pakistani boy presented with a history of progressive weakness and delayed milestones. Echocardiography showed features of dilated cardiomyopathy.
Vaishali Suri   +2 more
exaly   +3 more sources

Glycogen branching enzyme deficiency in adult polyglucosan body disease

open access: yesAnnals of Neurology, 1993
AbstractBranching enzyme activity was assayed in muscle, peripheral nerve, and leukocytes from 2 Ashkenazi‐Jewish patients with adult polyglucosan body disease and 1 African‐American and 3 Caucasian patients with the same clinical and pathological features.
Bruno C.   +9 more
openaire   +3 more sources

Preparation of branched starch by α-amylase and thermophilic glycogen branching enzyme modification

Food Chemistry
Maltogenic α-amylase (MA, EC 3.2.1.133), which shows high thermal stability, can cleave long starch chains linked by α-1,4 glycosidic bonds. And glycogen branching enzyme (GBE, EC 2.4.1.18) can increase the branching degree of starch. At high temperatures, Elevated temperatures enhanced starch solubilization, improving the accessibility of both MA and ...
Jie Long
exaly   +3 more sources

Neonatal type IV glycogen storage disease associated with “null” mutations in glycogen branching enzyme 1

Journal of Pediatrics, 2004
The fatal neonatal form of type IV glycogen storage disease (GSD IV) was diagnosed on light and electron microscopy and by analysis of GBE1 , the gene encoding glycogen branching enzyme. We report two novel truncating mutations, as well as the first genomic mutational analysis of GBE1 using denaturing high performance liquid chromatography.
Andreas Janecke   +2 more
exaly   +4 more sources

Synthesis of Branched Polyglucans by the Tandem Action of Potato Phosphorylase and Deinococcus geothermalis Glycogen Branching Enzyme

open access: yesMacromolecular Rapid Communications, 2008
AbstractAn enzymatic tandem reaction is described in which the enzymes phosphorylase and Deinococcus geothermalis glycogen branching enzyme (Dg GBE) catalyze the synthesis of branched polyglucans from glucose‐1‐phosphate (G‐1‐P). Phosphorylase consumes G‐1‐P and polymerizes linear amylose while Dg GBE introduces branching points on the α‐(1 → 6 ...
Vlist, J. van der   +5 more
openaire   +3 more sources

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