Results 71 to 80 of about 20,871 (172)

Dietary Management of the Ketogenic Glycogen Storage Diseases

Journal of Inborn Errors of Metabolism and Screening, 2016
The glycogen storage diseases (GSDs) comprise a group of rare inherited disorders of glycogen metabolism. The hepatic glycogenolytic forms of these disorders are typically associated with hypoglycemia and hepatomegaly.
Kaustuv Bhattacharya MBBS, MRCPCH, FRACP, MD, Jennifer Pontin MBChB, BSc Med, MRCPCH, Sue Thompson BSc (hons), AdvAPD   +2 more
doaj   +1 more source

Glycogen phosphorylase inhibition improves cognitive function of aged mice. [PDF]

Aging Cell, 2023
Drulis-Fajdasz D, Krzystyniak A, Puścian A, Pytyś A, Gostomska-Pampuch K, Pudełko-Malik N, Wiśniewski JŁ, Młynarz P, Miazek A, Wójtowicz T, Włodarczyk J, Duś-Szachniewicz K, Gizak A, Wiśniewski JR, Rakus D.   +14 more
europepmc   +1 more source

The Binding of Glycogen and Phosphorylase

Journal of Biological Chemistry, 1958
N B, MADSEN, C F, CORI
openaire   +2 more sources

Allosteric Regulation of Glycogen Phosphorylase by Order/Disorder Transition of the 250' and 280s Loops. [PDF]

Biochemistry, 2023
Kish M, Subramanian S, Smith V, Lethbridge N, Cole L, Vollmer F, Bond NJ, Phillips JJ.   +7 more
europepmc   +1 more source

Report of an Iranian child with chronic abdominal pain and constipation diagnosed as glycogen storage disease type IX: a case report

Journal of Medical Case Reports
Background Glycogen storage disease type IX is a rare disorder that can cause a wide variety of symptoms depending on the specific deficiency of the phosphorylase kinase enzyme and the organs it affects.
Daniel Zamanfar, Seyed MohammadBagher Hashemi-Soteh, Mobin Ghazaiean, Elham Keyhanian   +3 more
doaj   +1 more source

Analysis of the expression, function and signaling of glycogen phosphorylase isoforms in hepatocellular carcinoma. [PDF]

Oncol Lett, 2022
Jiang L, Liu S, Deng T, Yang Y, Zhang Y.
europepmc   +1 more source

The glycogen phosphorylase/ phosphorylase kinase interaction: effects of mutations in the amino-terminal region of glycogen phosphorylase

, 2018
Glycogen phosphorylase, important for carbohydrate metabolism, is found in. resting muscle as phosphorylase b, which is inactive without bovmd AMP. Phosphorylation by phosphorylase kinase (PhK) produces phosphorylase a, which is active in the absence of AMP.
openaire   +3 more sources

Diagnostic accuracy of glycogen phosphorylase BB for myocardial infarction: A systematic review and meta-analysis. [PDF]

J Clin Lab Anal, 2022
Ghimire A, Giri S, Khanal N, Rayamajhi S, Thapa A, Bist A, Devkota S.   +6 more
europepmc   +1 more source

Effect of Betaine and Arginine on Interaction of αB-Crystallin with Glycogen Phosphorylase b. [PDF]

Int J Mol Sci, 2022
Eronina TB, Mikhaylova VV, Chebotareva NA, Tugaeva KV, Kurganov BI.   +4 more
europepmc   +1 more source

Liver glycogen phosphorylase is upregulated in glioblastoma and provides a metabolic vulnerability to high dose radiation. [PDF]

Cell Death Dis, 2022
Zois CE, Hendriks AM, Haider S, Pires E, Bridges E, Kalamida D, Voukantsis D, Lagerholm BC, Fehrmann RSN, den Dunnen WFA, Tarasov AI, Baba O, Morris J, Buffa FM, McCullagh JSO, Jalving M, Harris AL.   +16 more
europepmc   +1 more source