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A anemia das células falciformes (SCA) é uma anemia hemolítica hereditária de transmissão autossómica recessiva devida à mutação HBB:c.20A>T no gene da β-globina que dá origem à hemoglobina S (HbS). A HbS quando em desoxigenação polimeriza no glóbulo vermelho, conferindo-lhe a forma de foice e tornando-o rígido e frágil.
openaire +1 more source
Is Intraoperative Blood Cell Salvage Effective in Hip Surgery? [PDF]
Nunes NG +5 more
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Brazilian Guidelines of Hypertension - 2020. [PDF]
Barroso WKS +97 more
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[Vitamin D in children and adolescents with sickle cell disease: an integrative review]. [PDF]
de Oliveira JF +3 more
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LXII Congreso Nacional de la SEHH, XXXVI Congreso Nacional de la SETH Virtual, 26-30 de octubre, 2020. [PDF]
The Authors.
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Doppler velocimetry of the orbital arteries in patients with sickle cell anemia: relationship with biomarkers of hemolysis. [PDF]
Ferrão TO +6 more
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[Infectious complications after surgical splenectomy in children with sickle cell anemia disease]. [PDF]
Monaco Junior CP, Fonseca PB, Braga JA.
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