Results 111 to 120 of about 197,953 (330)

Pediatric hereditary angioedema [PDF]

, 2015
Hereditary angioedema (HAE) is a lifelong illness characterized by recurrent swelling of the skin, intestinal tract, and, ominously, the upper airway.
MacGinnitie, Andrew J
core   +1 more source

Membranous nephropathy in a patient with hereditary angioedema: a case report

Journal of Medical Case Reports, 2008
Introduction Hereditary angioedema is the commonest inherited disorder of the complement system and has been associated with several immune glomerular diseases.
Majoni Sandawana W, Smith Steven R
doaj   +1 more source

Diagnosis and Treatment of Bradykinin-Mediated Angioedema: Outcomes from an Angioedema Expert Consensus Meeting [PDF]

, 2015
Several types of angioedema exist beyond hereditary angioedema (HAE) types I/II; however, the diagnostic and treatment needs of these conditions are not well understood.
Bernstein JA, Boccon-Gibod I, Bouillet L, Craig TJ, Farkas, Henriette   +4 more
core   +1 more source

Secreted phospholipases A2 in hereditary angioedema with C1-inhibitor deficiency [PDF]

, 2018
BackgroundHereditary angioedema (HAE) caused by deficiency (type I) or dysfunction (type II) of the C1 inhibitor protein (C1-INH-HAE) is a disabling, potentially fatal condition characterized by recurrent episodes of swelling. We have recently found that
Andrea Zanichelli, Angelica Petraroli, Anne Lise Ferrara, Chiara Suffritti, Francesco Borriello, Francesco Borriello, Francescopaolo Granata, Gianni Marone, Gianni Marone, Gilda Varricchi, Gérard Lambeau, Henriette Farkas, Marco Cicardi, Maria Bova, Maria Rosaria Galdiero, Nóra Veszeli, Stefania Loffredo   +16 more
core   +3 more sources

Canadian hereditary angioedema guideline [PDF]

Allergy, Asthma & Clinical Immunology, 2014
Hereditary angioedema (HAE) is a disease which is associated with random and often unpredictable attacks of painful swelling typically affecting the extremities, bowel mucosa, genitals, face and upper airway. Attacks are associated with significant functional impairment, decreased Health Related Quality of Life, and mortality in the case of laryngeal ...
S. Betschel, J. Badiou, K. Binkley, J. Hébert, A. Kanani, P. Keith, G. Lacuesta, B. Yang, E. Aygören-Pürsün, J. Bernstein, K. Bork, T. Caballero, M. Cicardi, T. Craig, H. Farkas, H. Longhurst, B. Zuraw, H. Boysen, R. Borici-Mazi, T. Bowen, K. Dallas, J. Dean, K. Lang-Robertson, B. Laramée, E. Leith, S. Mace, C. Mccusker, B. Moote, M. Poon, B. Ritchie, D. Stark, G. Sussman, S. Waserman   +32 more
openaire   +5 more sources

Revealing the Diverse Allergenic Protein Repertoire of Six Widely Consumed Crab Species: A Species‐Specific Allergen in King Crab

Allergy, EarlyView.
This study comprehended the allergen profiles of six edible crab species using proteomic and transcriptomic analyses and identified 11 putative allergens. King crab has a distinct protein and allergen profile, with the discovery of malate dehydrogenase as a novel king crab‐specific allergen registered as Para c 11.
Shanshan Li, Jingyuan Bian, Qing Xiong, Brian Shing‐Hei Wong, Stephen Kwok‐Wing Tsui, Kin‐Ming Kwan, Nicki Yat‐Hin Leung, Ting‐Fan Leung, Patrick S. C. Leung, Ka‐Hou Chu, Xiaojun Xiao, Christine Yee‐Yan Wai   +11 more
wiley   +1 more source

HLA‐A*02:01 Presents Penicillin‐Modified Cysteinylated Peptides for T Cell Recognition

Allergy, EarlyView.
We describe, for the first time, HLA presentation of benzylpenicillin‐modified peptides incorporating a cysteine‐benzylpenicillin conjugate (CysBP), disulfide linked to an in‐chain cysteine. A dominant HLA‐A*02:01 restricted benzylpenicillin‐specific T cell clone, TRAV3/TRBV20‐1 (BP‐TCR), was identified within PBMCs of a penicillin‐hypersensitive ...
Shawn J. R. Goh, Hovey H. W. Lu, Katherine E. Scull, Kirti Pandey, Mohammadreza Dorvash, Kirsten Deckert, Robert Puy, Robyn E. O'Hehir, Anthony W. Purcell, Nicole A. Mifsud, Patricia T. Illing   +10 more
wiley   +1 more source

Social costs of icatibant self-administration vs. health professional-administration in the treatment of hereditary angioedema in Spain [PDF]

, 2013
Background: Icatibant is the only subcutaneous treatment for acute Type I and Type II hereditary angioedema with C1-esterase inhibitor deficiency (HAE-C1-INH) licensed for self-administration in Europe.
Blasco, Antonio J., Caballero, Teresa, Guilarte, Mar, Lázaro, Pablo   +3 more
core   +1 more source

Diagnosis, management and the burden of symptoms of mastocytosis from the physician's perspective: A nationwide study

British Journal of Haematology, EarlyView.
Summary Mastocytosis is categorized into cutaneous mastocytosis (CM), mast cell sarcoma and systemic mastocytosis (SM). Within SM, indolent SM (ISM) is the more frequent subtype. Adult patients with CM but without an extracutaneous biopsy are classified as having mastocytosis in the skin (MIS), a provisional diagnosis.
Julien Rossignol, Laurence Bouillet, Cristina Bulai‐Livideanu, Stéphane Barete, Julie Bruneau, Clément Gourguechon, Laura Polivka, Angèle Soria, Olivier Lortholary, Trevor Stanbury, Benoit Bouquillon, Cedric Sauvage, Rose Marie Javier, Olivier Hermine, Michel Arock, the CEREMAST Network   +15 more
wiley   +1 more source

Characteristics of Patients with Hereditary Angioedema Who Reduced Lanadelumab Treatment Administration Frequency: A Retrospective Observational Study of US Claims Data

Drugs - Real World Outcomes
Background Lanadelumab is the only long-term prophylaxis indicated for reduced administration frequency in patients with hereditary angioedema who have been well controlled for > 6 months.
Nicole Princic, Kristin A. Evans, Chintal H. Shah, Krystal Sing, Salomé Juethner, Bob G. Schultz   +5 more
doaj   +1 more source