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Hereditary and acquired angioedema
Allergy and Asthma Proceedings, 2019Hereditary angioedema (HAE) is an autosomal dominant disorder defined by a deficiency of functional C1 esterase inhibitor (C1-INH). Acquired angioedema is due to either consumption (type 1) or inactivation (type 2) of CI-INH. Both HAE and acquired angioedema can be life-threatening.
Gayatri, Patel, Jacqueline A, Pongracic
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Icatibant for hereditary angioedema
Drugs of Today, 2009Hereditary angioedema (HAE) is an autosomal dominant, potentially life-threatening disease, characterized by recurrent self-limiting bouts of edema mainly involving the extremities, genitalia, face, intestines and airways. The prevalence of HAE in the general population has been estimated to be in the range of 1:10,000 to 1:150,000.
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Treatment of Hereditary Angioedema
JAMA: The Journal of the American Medical Association, 1979To the Editor.— In his letter "Hereditary Angioedema" (240:2155, 1978), Dr Reimann does not mention the use of androgenic steroids for prophylaxis of attacks. Methyltestosterone was first effectively used by Spaulding 1 in 1960. This was followed by reports of effectiveness of less virilizing analogues, fluoxymesterone, oxymetholone, 2 and danazol.
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The pathogenesis of hereditary angioedema
Transfusion and Apheresis Science, 2003Hereditary angioedema (HAE), which is characterized by episodic localized angioedema of the skin or mucosa, results from heterozygous deficiency of the plasma protease inhibitor, C1 inhibitor (C1INH). The most obvious biologic role of C1INH, therefore, is prevention of excessive vascular permeability.
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Journal of Allergy and Clinical Immunology, 2008
Hereditary angioedema is an episodic swelling disorder with autosomal dominant inheritance. Attacks are characterized by brawny, self-limited, nonpruritic edema of the deep dermal layers of the skin that most often involve the hands and feet. They usually begin in childhood and become more severe after puberty.
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Hereditary angioedema is an episodic swelling disorder with autosomal dominant inheritance. Attacks are characterized by brawny, self-limited, nonpruritic edema of the deep dermal layers of the skin that most often involve the hands and feet. They usually begin in childhood and become more severe after puberty.
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Contraception in hereditary angioedema
Fertility and Sterility, 2008To report a case of successful use of a transdermal contraceptive in a patient with hereditary angioedema.Case report.University medical center.A patient who had used oral contraceptives contracted SC and submucosal tumefaction every 1 or 2 months. She was diagnosed with type I hereditary angioedema.
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The pathophysiology of hereditary angioedema
Clinical Immunology, 2005Hereditary angioedema (HAE), characterized by recurrent episodes of angioedema involving the skin, or the mucosa of the upper respiratory or the gastrointestinal tracts, results from heterozygosity for deficiency of the serine proteinase inhibitor (serpin), C1 inhibitor (C1INH).
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