Hereditary angioedema (HAE) in children and adolescents—a consensus on therapeutic strategies [PDF]
Hereditary angioedema due to C1 inhibitor (C1 esterase inhibitor) deficiency (types I and II HAE-C1-INH) is a rare disease that usually presents during childhood or adolescence with intermittent episodes of potentially life-threatening angioedema. Diagnosis as early as possible is important to avoid ineffective therapies and to properly treat swelling ...
Wahn, Volker +11 more
openaire +7 more sources
2010 International consensus algorithm for the diagnosis, therapy and management of hereditary angioedema [PDF]
Background We published the Canadian 2003 International Consensus Algorithm for the Diagnosis, Therapy, and Management of Hereditary Angioedema (HAE; C1 inhibitor [C1-INH] deficiency) and updated this as Hereditary angioedema: a current state-of-the-art ...
Bowen Tom +59 more
doaj +2 more sources
WAO Guideline for the Management of Hereditary Angioedema [PDF]
Hereditary Angioedema (HAE) is a rare disease and for this reason proper diagnosis and appropriate therapy are often unknown or not available for physicians and other health care providers.
Timothy Craig, DO +17 more
doaj +2 more sources
The hereditary angioedema burden of illness study in Europe (HAE-BOIS-Europe): background and methodology [PDF]
Hereditary angioedema (HAE) is a rare but serious disease marked by swelling attacks in the extremities, face, trunk, airway, or abdominal areas that can be spontaneous or the result of trauma and other triggers. It can be life-threatening due to the risk of asphyxiation.
Bygum, Anette +7 more
openaire +7 more sources
Malignancy and immune disorders in patients with hereditary angioedema
Background Hereditary angioedema (HAE) is an inherited condition manifesting as recurrent angioedema episodes which is caused by deficiency or dysfunction of C1 inhibitor.
Peter Stepaniuk, Amin Kanani
doaj +2 more sources
A patient with hereditary angioedema and systemic lupus erythematosus: Coincidence or coexistence?
Angioedema is classified into two major groups: mast cell-mediated (histaminergic) and bradykinin-mediated angioedema. Hereditary angioedema and acquired angioedema are well-defined groups of bradykinin-mediated angioedema. Both hereditary angioedema and
Gokhan Aytekin +3 more
doaj +2 more sources
The International/Canadian Hereditary Angioedema Guideline
This is an update to the 2014 Canadian Hereditary Angioedema Guideline with an expanded scope to include the management of hereditary angioedema (HAE) patients worldwide.
Stephen Betschel +43 more
doaj +2 more sources
Management of hereditary angioedema in pregnant women: a review
Teresa Caballero,1,2 Julio Canabal,1 Daniela Rivero-Paparoni,1 Rosario Cabañas1 1Hospital La Paz Institute for Health Research, (IdiPaz) 2Biomedical Research Network on Rare Diseases-U754 (CIBERER), Madrid, Spain Abstract: Three types of ...
Caballero T +3 more
doaj +1 more source
Transitioning Patients From Second- to First-Line Prophylaxis in Hereditary Angioedema [PDF]
Modern targeted prophylaxis is recommended for patients with hereditary angioedema (HAE), but many remain on attenuated androgens. EMJ spoke to two HAE experts who explain how they help patients to make the switch.
Caroline E Cross
doaj +2 more sources
Hereditary angioedema classification: Expanding knowledge by genotyping and endotyping
Hereditary angioedema (HAE) encompasses a group of diseases characterized by recurrent, genetically mediated angioedema associated with increased vascular permeability primarily due to bradykinin.
Pedro Giavina-Bianchi, MD, PhD +6 more
doaj +2 more sources

