Systemic autoinflammatory diseases
Journal of Autoimmunity, 2020 Systemic autoinflammatory diseases (SAIDs) are a growing group of disorders caused by a dysregulation of the innate immune system leading to episodes of systemic inflammation.
Julie Krainer +2 more
semanticscholar +3 more sources
Systemic disease or periodontal disease? Distinguishing causes of gingival inflammation: a guide for dental practitioners. Part 1: immune-mediated, autoinflammatory, and hereditary lesions [PDF]
British Dental Journal, 2019 Periodontitis and gingivitis remain two of the most common diseases that affect the oral cavity. As they are caused by plaque, effective oral hygiene, elimination of plaque-retentive factors and successful periodontal treatment will result in resolution of gingival and periodontal inflammation.
Josefine, Hirschfeld +5 more
openaire +3 more sources
Hereditary Autoinflammatory Diseases; Diagnosis and Management
Nihon Naika Gakkai Zasshi, 2014 Kiyoshi Migita +2 more
openaire +3 more sources
First report from the Czech national registry of inborn errors of immunity (2012–2025) [PDF]
Frontiers in ImmunologyIntroductionCongenital immune system defects represent an ever-growing group of diseases characterized by increased susceptibility to infections and association with autoimmune, autoinflammatory, allergic and malignant complications. Here, we provide the
Zita Chovancova +32 more
doaj +2 more sources
Systemic autoinflammatory disorders [PDF]
Clinical and Experimental Pediatrics, 2023 Inflammation is a physiologic defense mechanism against an out-side attack. Usually, it resolves after the removal of noxious causes, but systemic autoinflammatory disorders (SAIDs) have recurrent or repeated acute inflammation through uncontrolled gene ...
Dae Chul Jeong
doaj +1 more source
Designation of Autoinflammatory Skin Manifestations With Specific Genetic Backgrounds
Frontiers in Immunology, 2020 “Autoinflammatory disease (AiD)” has first been introduced in 1999 when the responsible gene for the familial Hibernean fever or autosomal dominant-type familial Mediterranean fever-like periodic fever syndrome was reportedly identified as tumor necrosis
Nobuo Kanazawa
doaj +1 more source
Multidisciplinary Approach to Complex Lower Extremity Limb Salvage in Pyogenic Arthritis, Pyoderma Gangrenosum, and Acne (PAPA) Syndrome: A Case Report. [PDF]
MicrosurgeryABSTRACT Limb salvage using free tissue transfer in patients with rare autoinflammatory syndromes is poorly described, and the safety of microvascular reconstruction in this population remains uncertain. Hereditary pyogenic arthritis, pyoderma gangrenosum, and acne (PAPA) syndrome is characterized by dysregulated inflammation, pathergy, and impaired ...
Talanker MM +9 more
europepmc +2 more sources
PSTPIP1-associated incomplete PAPA syndrome. Case report [PDF]
Consilium Medicum, 2022 PAPA syndrome (Pyogenic sterile arthritis, pyoderma gangrenosum, and acne syndrome) is a rare disease even among infrequent systemic autoinflammatory diseases.
Dali Sh. Macharadze +1 more
doaj +1 more source
Muckle Wells syndrome as an example of hereditary systemic autoinflammatory disease [PDF]
, 2014 Bertomeu Tomàs, Andrea +1 more
openaire +3 more sources
Frontiers in Medicine, 2021 Objectives:NLRP3-associated autoinflammatory disease (NLRP3-AID) and Behçet's syndrome (BS) both belong to autoinflammatory diseases and rarely co-occur.
Jinjing Liu +22 more
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