Results 41 to 50 of about 9,012 (189)
Multicentric reticulohistiocytosis: a case report
BMC Research Notes, 2018 Background Multicentric reticulohistiocytosis is a rare form of non-langerhans cell histiocytosis presenting with skin changes and erosive arthritis. Infiltration of histiocytes and multinucleated giant cells are typical histological findings and confirm
Azadèh Farokhi +3 more
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Langerhans' cell histiocytosis: Possible association with malignant germ cell tumour [PDF]
, 1995 A rare case of adult onset Langerhans' cell histiocytosis associated with dysgerminoma in a 35 year old Chinese woman is reported. The patient had a history of dysgerminoma of left ovary 15 years previously and had undergone surgery followed by ...
Lam, KY, Ng, IOL, Ng, WK
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MEK Inhibition with Trametinib in Patients with Non-Langerhans Cell Histiocytosis
Blood, 2019 Background: Activation of the MAPK pathway through BRAF mutations or other molecular alterations is a hallmark of the non-Lagerhans cell histiocytosis (non-LCH) such Erdheim-Chester disease (ECD) or Rosai-Dorfman disease (RDD). Conventional clinical molecular testing of tumor tissue fails to identify targetable molecular alteration in about one third ...
Aaron M. Goodman +5 more
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Laryngeal involvement with fatal outcome in progressive nodular histiocytosis: A rare case report
Indian Dermatology Online Journal, 2016 Progressive nodular histiocytosis (PNH) represents a very rare type of non-Langerhans cell histiocytosis. It is characterized by progressive appearance of papules and nodules without spontaneous resolution.
Aarti Salunke +3 more
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Erdheim-Chester Disease Involving Lymph Nodes and Liver Clinically Mimicking Lymphoma: A Case Report [PDF]
Journal of Pathology and Translational Medicine, 2018 Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis and multisystem disease. First described in 1930, there are no more than 750 cases reported.
Yeoun Eun Sung +3 more
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An unusual case of intertrigo in an adult caused by purely cutaneous Langerhans cell histiocytosis [PDF]
, 2016 We report a case of persistent intertrigo in an adult, eventually diagnosed as cutaneous Langerhans cell histiocytosis (LCH). It is known that LCH has a predilection for intertriginous areas, however purely cutaneous disease as in our case, is uncommon ...
Baldacchino, Godfrey +3 more
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Langerhans cell histiocytosis with oral manifestations: a rare and unusual case report [PDF]
, 2012 Langerhans cell histiocytosis (LCH), is a rare, proliferative disorder in which the accumulation of pathologic Langerhans cells leads to local tissue infiltration and destruction.
Agarwal, Manjushree +2 more
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European Journal of Case Reports in Internal Medicine, 2021 Eosinophilic granuloma is a localized, non-invasive form of Langerhans cell histiocytosis. It usually develops in the long bones and is more frequent in children under the age of 10 years. It is very rare in adults.
Tatiana Pires +5 more
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A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]
, 2018 Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M. +3 more
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Solving a Mystery . . . 8 Years Later
Journal of Investigative Medicine High Impact Case Reports, 2018 Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multisystem involvement and insidious symptoms. In this article, we describe an interesting case of Erdheim-Chester disease that was eventually diagnosed 8 years after symptoms ...
Hayan Jouni MD +2 more
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