Results 231 to 240 of about 204,699 (375)

New cases expand the genotype, phenotype and therapeutic landscape of H syndrome

British Journal of Haematology, EarlyView.
Clément Triaille, Julie Beauchemin, Philippe M. Campeau, Hugo Chapdelaine, Julie Dery, Maria Kondyli, Grant Mitchell, Julie Powell, Sophie Turpin, Guilhem Cros, Fabien Touzot   +10 more
wiley   +1 more source

Multi‐omic analysis identifies biological processes underlying progressive interstitial lung disease in systemic sclerosis

The FEBS Journal, EarlyView.
Systemic sclerosis (SSc) is a rare autoimmune disease, and lung complications (ILD) are the main cause of death. This study compared SSc patients with and without lung disease to healthy volunteers. We found increased inflammation, specific proteins, and higher triglyceride levels linked to lung disease progression. These findings suggest triglycerides
Selena Bouffette, Perrine Soret, Alice Cole, Emmanuel Nony, Pierre Barbier Saint Hilaire, Grégory Leclerc, Lamine Alaoui, Audrey Aussy, Isabelle Wehrle, Aude Le Gall, Mark Coulon, Marc Pallardy, Voon Ong, Jeanne Allinne, Philippe Moingeon, David Abraham, Christopher P. Denton   +16 more
wiley   +1 more source

Aberrant Wnt/β-Catenin Pathway Activation in Idiopathic Pulmonary Fibrosis [PDF]

, 2003
Marco Chilosi, Venerino Poletti, Alberto Zamò, Maurizio Lestani, Licia Montagna, P Piccoli, Serena Pedron, Manuela Bertaso, Aldo Scarpa, Bruno Murer, Alessandra Cancellieri, Roberta Maestro, Gianpietro Semenzato, Claudio Doglioni   +13 more
openalex   +1 more source

Lung organoids as a human system for Mycobacteria infection modeling and drug testing

The FEBS Journal, EarlyView.
Mycobacterial infections, including tuberculosis (TB) and infections by nontuberculous mycobacteria (NTM), are still public health issues. In 2023, TB caused 1.25 million deaths, while NTM remain a clinical challenge for patients with cystic fibrosis (CF).
Stephen Adonai Leon‐Icaza, Romain Vergé, Raoul Mazars, Laurence Berry, Céline Cougoule   +4 more
wiley   +1 more source

Serum vesicle biomarkers reflect the disease activity of idiopathic pulmonary fibrosis. [PDF]

J Transl Med
Shirai Y, Enomoto T, Takeda Y, Edahiro R, Takahashi-Itoh M, Noda Y, Adachi Y, Nakayama M, Kawasaki T, Koba T, Futami Y, Yoshimura H, Amiya S, Hara R, Yamamoto M, Nakatsubo D, Suga Y, Naito M, Masuhiro K, Matsuki T, Hirata H, Iwahori K, Nagatomo I, Miyake K, Koyama S, Fukushima K, Shiroyama T, Naito Y, Futami S, Natsume-Kitatani Y, Ose N, Funaki S, Nojima S, Shichino S, Yanagawa M, Shintani Y, Nogami-Itoh M, Adachi J, Inoue Y, Tomonaga T, Okada Y, Mizuguchi K, Kumanogoh A.   +42 more
europepmc   +1 more source

GPNMB immunohistochemistry is a useful ancillary tool for the diagnosis of pulmonary lymphangioleiomyomatosis

Histopathology, EarlyView.
We evaluated the diagnostic utility of GPNMB immunohistochemistry in LAM. GPNMB showed strong expression in LAM cells, while the differential diagnostic mimics showed no or only low expression. Based on its 100% sensitivity and specificity in our cohort, GPNMB is a highly reliable immunohistochemical marker for the diagnosis of LAM.
Fatime Szalai, Judit Pápay, Katalin Dezső, Levente Kuthi, Anna Sebestyén, András Khoór, Ildikó Krencz   +6 more
wiley   +1 more source

Fatty Acids Dysregulation Correlates with Lung Function in Idiopathic Pulmonary Fibrosis. [PDF]

Lung
Scialò F, Pagliaro R, Gelzo M, Matera MG, D'Agnano V, Zamparelli SS, Castaldo G, Cazzola M, Bianco A, Perrotta F.   +9 more
europepmc   +1 more source

Epstein–Barr virus and wild p53 in idiopathic pulmonary fibrosis

, 2001
She Lok, James P. Stewart, B. Kelly, P S Hasleton, J. Egan   +4 more
openalex   +1 more source

The Therapeutic Effect of Angiotensin II Receptor Antagonist in Idiopathic Pulmonary Fibrosis [PDF]

, 2003
Duck Soo Woo, Won Jong Seol, Sun Young Kyung, Young Hee Lim, Chang Hyeok An, Jeong Woong Park, Sung Hwan Jeong, Jae Woong Lee   +7 more
openalex   +1 more source

Living with idiopathic pulmonary fibrosis [PDF]

The Lancet Respiratory Medicine, 2021
openaire   +3 more sources