Results 1 to 10 of about 157 (103)

IgA Pemphigus Showing IgA Antibodies to Desmoglein 1 and 3 [PDF]

open access: yesDermatology Practical and Conceptual, 2016
IgA pemphigus is a rare autoimmune vesiculo-pustular skin disease. Only approximately 70 cases have been reported to date. We report a case of IgA pemphigus with IgA antibodies to desmoglein 1 (Dsg1) and desmoglein 3 (Dsg3).We report the case of an 60-year-old man with intraepidermal neutrophilic IgA pemphigus with IgA antibodies to Dsg1 and Dsg3 ...
Faten Zeglaoui, Aida Khaled
exaly   +5 more sources

Non-classical forms of pemphigus: pemphigus herpetiformis, IgA pemphigus, paraneoplastic pemphigus and IgG/IgA pemphigus [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2014
The pemphigus group comprises the autoimmune intraepidermal blistering diseases classically divided into two major types: pemphigus vulgaris and pemphigus foliaceous. Pemphigus herpetiformis, IgA pemphigus, paraneoplastic pemphigus and IgG/IgA pemphigus are rarer forms that present some clinical, histological and immunopathological characteristics that
Porro, Adriana Maria   +3 more
openaire   +6 more sources

Clinical, Histopathologic, and Immunohistochemical Features of Patients With IgG/IgA Pemphigus

open access: yesBiomedicines, 2022
Pemphigus is an autoantibody-mediated blistering disease. In addition to conventional pemphigus vulgaris and pemphigus foliaceus, several other types have been reported. Among them, IgG/IgA pemphigus is less well defined and seldom reported.
Yih-leong Chang   +2 more
exaly   +3 more sources

IgG/IgA Pemphigus With Differing Regional Presentations

open access: yesJAAD Case Reports, 2022
Hok Fai Cheng, MBBS(HK), MRCP(UK), FHKAM(Medicine)   +4 more
exaly   +5 more sources

IgA Pemphigus

open access: yes, 2015
IgA pemphigus (IGAP) is a rare variant of pemphigus characterized by tissue-bound and circulating autoantibodies exclusively from the IgA class against desmosomal and non-desmosomal proteins of the epidermis. Based on the clinics, histology, direct immunofluorescence and autoantibody profile it is classified in two types: the subcorneal pustulosis ...
Horvath, Barbara, Jonkman, Marcel F.
exaly   +6 more sources

IgA Pemphigus Following COVID-19 Vaccination: A Case Report

open access: yesSAGE Open Medical Case Reports, 2023
A patient presented with pruritic lesions on their back and leg after COVID-19 vaccination. Biopsy and direct immunofluorescence were consistent with IgA pemphigus—likely caused by the COVID-19 vaccine.
Rafael Paolo Lansang
exaly   +2 more sources

Pemphigus foliaceus masquerading as IgA pemphigus and responding to dapsone

open access: yesIndian Journal of Dermatology, 2012
A 14-year-old male presented with seven years history of recurrent episodes of fluid filled, itchy and eroded lesions over the body not responding to oral corticosteroids and azathioprine. Dermatological examination revealed crusted plaques and erosions in a seborrheic distribution.
Manas Chatterjee   +4 more
openaire   +4 more sources

A Case of IgA Pemphigus with Acantholysis in Oral Mucosal Lesions

open access: yesSkin Health and Disease
Abstract IgA pemphigus is an autoimmune bullous disease caused by anti-keratinocyte cell surface IgA autoantibodies. Mucous membrane involvement is rare in IgA pemphigus. We report a case of IgA pemphigus with oral mucosal lesions, in which acantholysis was pathologically confirmed.
Ayumi Yamanishi   +9 more
openaire   +3 more sources

Revisiting the question of pemphigus classification

open access: yesVestnik Dermatologii i Venerologii, 2021
Analysis of various classifications of pemphigus shows that there are no fundamental differences between them. The main distinctions consist in use of diverse terms in naming of some forms of pemphigus and in inclusion or exclusion of certain subtypes ...
Alexey V. Samtsov   +5 more
doaj   +1 more source

Immunofluorescence testing in the diagnosis of autoimmune blistering diseases: overview of 10-year experience [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2014
BACKGROUND: Immunofluorescence testing is an important tool for diagnosing blistering diseases. OBJECTIVE: To characterize the immunofluorescence findings in patients diagnosed with autoimmune blistering skin diseases.
Samia Trigo Arbache   +4 more
doaj   +1 more source

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