Systemic retinoids for treatment of recalcitrant IgA pemphigus [PDF]
Orphanet Journal of Rare Diseases, 2018 IgA pemphigus is an exceedingly rare autoimmune blistering disorder, caused by IgA autoantibodies against desmosomal proteins. No treatment option has been found to be universally effective.
Franziska Schauer +2 more
doaj +2 more sources
An Updated Review of Pemphigus Diseases
Medicina, 2021 Clinicians may encounter a variety of skin conditions that present with vesiculobullous lesions in their everyday practice. Pemphigus vulgaris, pemphigus foliaceus, IgA pemphigus, and paraneoplastic pemphigus represent the spectrum of autoimmune bullous ...
Ali M. Malik +5 more
doaj +2 more sources
A case of IgA pemphigus, with a poor response to dapsone, successfully treated with adalimumab [PDF]
Clinical Case ReportsKey Clinical Message IgA pemphigus is usually treated by Dapsone. Recalcitrant cases may be treated by Colchicine, Sulfapyridine, or Acitretin. Some patients with recurrent severe disease may not respond to the aforementioned medications.
Saman Al‐Zahawi +2 more
doaj +2 more sources
IgG/IgA-pemphigus — extremely rare blistering autoimmune diseases [PDF]
Vestnik Dermatologii i Venerologii, 2020 Purpose. To present a clinical case of IgG/IgA pemphigus in a 32-year-old woman. Material and methods. Clinical and laboratory examinations were performed to diagnose the disease: cytological examination of an impression smear from the bottom of the ...
Arfenya E. Karamova +4 more
doaj +5 more sources
The importance of direct immunofluorescence in pemphigus herpetiformis diagnosis [PDF]
Anais Brasileiros de Dermatologia, 2017 Pemphigus herpetiformis is an autoimmune bullous disease, that combines clinical features of dermatitis herpetiformis and linear IgA bullous dermatosis and immunological characteristics of pemphigus, which makes this disease peculiar and this diagnosis ...
Paula Carolina Pessanha de Faria +5 more
doaj +2 more sources
Therapeutic Options for IgA Pemphigus in Patients Refractory to Dapsone
JEADV Clinical PracticeIgA pemphigus is a rare autoimmune blistering disorder with limited therapeutic guidance available due to its rarity and complex presentation. This comprehensive analysis evaluates the therapeutic outcomes of 67 published patients, emphasising the ...
Lorenz Frasheri +2 more
doaj +2 more sources
A Unified Concept of Skin Failure: Primary and Secondary Forms [PDF]
Int Wound JInternational Wound Journal, Volume 23, Issue 10, October 2026.
Anna B. Chapman, Christopher B. Bunker
wiley +2 more sources
Case Report: A rare co-occurrence of IgA pemphigus and pyoderma gangrenosum associated with IgA-κ type monoclonal gammopathy of undetermined significance: a 19-year diagnostic and therapeutic journey [PDF]
Frontiers in ImmunologyWe report a complex case of neutrophilic dermatosis (ND) in a 61-year-old woman with a 19-year history of recurrent, pruritic, and painful vesiculopustular eruptions.
You Xie +9 more
doaj +2 more sources
European S2k guidelines on management of autoimmune blistering diseases in children and adolescents [PDF]
Journal of the European Academy of Dermatology and Venereology, Volume 40, Issue 7, Page 1137-1161, July 2026.Autoimmune blistering disorders (AIBDs) in children are rare, challenging to diagnose and treat and often require immunosuppressants. Until now, no paediatric care guidelines existed. The EADV Task Force for AIBDs has developed the consensus‐based recommendations, enabling physicians to adopt a uniform, tailored treatment strategy to improve outcomes ...
A. Nanda +31 more
wiley +2 more sources
Unraveling the autoimmune architecture of pemphigus: from B-cell depletion to network-based immune engineering [PDF]
Frontiers in ImmunologyPemphigus encompasses autoimmune blistering diseases driven by autoantibodies to desmosomal proteins. Disruption of keratinocyte adhesion produces acantholysis and epidermal fragility.
Pedram Shafiei-Jahani +10 more
doaj +2 more sources