Results 91 to 100 of about 4,867,269 (191)
ABSTRACT In endemic regions, markedly elevated Brucella serologic titers with a dynamic decline after treatment support true infection even in the presence of monoclonal gammopathy. Concurrent infectious and malignant processes should be considered in patients presenting with severe renal failure and overlapping systemic symptoms to avoid diagnostic ...
Maryam Ghaffari Rahbar +3 more
wiley +1 more source
Systemic light-chain amyloidosis revealed by progressive nail involvement, diffuse alopecia and sicca syndrome: report of an unusual case with a review of the literature. [PDF]
Immunoglobulin light-chain (AL) amyloidosis is a form of systemic amyloidosis in which the fibrils are derived from monoclonal light chains. We report a case of a 66-year-old woman presenting with nail changes, parchment-like hand changes, progressive ...
Haneke, Eckart +3 more
core +2 more sources
Pulmonary light chain deposition disease: Case series and review of the literature
Pulmonary light chain deposition disease is a rare entity characterized by immunoglobulin deposition within the lung parenchyma with pathologic features distinct from pulmonary amyloidosis.
Tomas V. Gonzalez, MD +3 more
doaj +1 more source
Light-chain cardiac amyloidosis with neuropathy: a case report
Zhan-Wen Xu,1 Ya-Qin Li,1 Li-xia Liu,2 Bing-Juan Zhou3 1Department of Cardiology, 2Department of Ultrasound, Affiliated Hospital of Hebei University, 3Department of Pathology, Baoding First Central Hospital, Baoding, People’s Republic of China ...
Li YQ, Liu LX, Xu ZW, Zhou BJ
core
Localized amyloid light-chain amyloidosis and extramedullary plasmacytoma of the mitral valve
An unusual case of localized amyloid light-chain (AL) amyloidosis and extramedullary plasmacytoma of the mitral valve is described. The worsening of a mitral regurgitation led to investigations and surgery.
Roumy, A. +15 more
core +1 more source
Púrpura: manifestação de amiloidose sistémica primária.
Primary Systemic Amyloidosis (AL) is the most frequent form of systemic amyloidosis and its morbilility is associated with immunoglobulin light chains deposition in vital organs. The mucocutaneous manifestations occur in about 30-40% of the cases and are
Sara Lestre +4 more
doaj +1 more source
In immunoglobulin light-chain (L) amyloidosis the cause of death is most commonly due to cardiac involvement. Cardiac amyloidosis is frequently diagnosed by postmortem examination. There are many reports of diagnoses of cardiac amyloidosis established by
core +1 more source
Introduction Immunoglobulin light chain (AL) amyloidosis presents a clinical spectrum characterized by diverse manifestations and involvement of multiple organs, posing a significant diagnostic challenge for physicians.
Jun Yang +4 more
doaj +1 more source
Amyloidosis is a rare disease characterized by an abnormal accumulation of the amyloid protein in tissues. Amyloidosis can be divided into two main subtypes: transthyretin amyloidosis (ATTR-CA) and immunoglobulin light chain amyloidosis (AL-CA ...
Magdalena Balwierz +2 more
doaj +1 more source
转甲状腺素蛋白心脏淀粉样变(transthyretin cardiac amyloidosis, ATTR-CA)是除外免疫球蛋白轻链心脏淀粉样变(immunoglobulin light chain amyloidosis, AL-CA)最常见的心脏淀粉样变(cardiac amyloidosis, CA)[1]。ATTR-CA患者生活质量差、生存率低[2]。
翟书慧, 王丹, 赵绮旎, 刘龙
doaj

