Results 81 to 90 of about 5,095,980 (121)

Localized amyloid light-chain amyloidosis and extramedullary plasmacytoma of the mitral valve

, 2013
An unusual case of localized amyloid light-chain (AL) amyloidosis and extramedullary plasmacytoma of the mitral valve is described. The worsening of a mitral regurgitation led to investigations and surgery.
Roumy, A., Kurtin, Paul, von Segesser, L.K., Schäfer, Stephan, von Segesser, Ludwig K., Niclauss, Lars, de Leval, Laurence, Niclauss, L., Ruchat, P., Kurtin, P., Dogan, A., Schaefer, S.C., Ruchat, Patrick, Roumy, Aurélien, Dogan, Ahmet, de Leval, L., de Leval L, Dogan A, Roumy A, Schaefer SC, Kurtin P, von Segesser LK, Niclauss L, Ruchat P   +23 more
core   +1 more source

Light-chain cardiac amyloidosis with neuropathy: a case report

, 2015
Zhan-Wen Xu,1 Ya-Qin Li,1 Li-xia Liu,2 Bing-Juan Zhou3 1Department of Cardiology, 2Department of Ultrasound, Affiliated Hospital of Hebei University, 3Department of Pathology, Baoding First Central Hospital, Baoding, People’s Republic of China ...
Li YQ, Liu LX, Xu ZW, Zhou BJ
core  

Systemic Amyloidosis Presented with Persistent Cough: A Case Report and Review of Literature

, 1970
Key words: systemic amyloidosis; immunoglobulin light chain-derived amyloidosis (AL); respiratory amyloidosis; coughsDOI: 10.3329/jcmcta.v21i1.7683 Journal of Chittagong Medical College Teachers' Association 2010: 21(1):70 ...
Md Abu Sayeed, Sujat Paul, Dilruba Siraji, Uzzwal Kanti Das, Md Abdus Sattar   +4 more
core   +1 more source

Free light chain testing for the diagnosis, monitoring and prognostication of AL amyloidosis

, 2016
The disease causing agent in systemic AL amyloidosis is a monoclonal immunoglobulin free light chain, or fragments thereof, circulating in the blood. It is not surprising, therefore, that measurement of serum free light chains plays a central role in the
Mollee, P., Mollee, Peter, Merlini, Giampaolo   +2 more
core   +1 more source

Two cases of monoclonal nodular pulmonary amyloidosis and review of the literature [PDF]

, 2016
Nodular pulmonary amyloidosis (NPA) is an uncommon pathology of insoluble protein depositing in pulmonary parenchyma. This localized pulmonary form of amyloidosis is most often found to contain combinations of kappa and lambda immunoglobulin light chain ...
Hynes, Conor, Endicott, Kendal, Edina Paal, Hsieh, Cindy M., Gregory Trachiotis, Kendal M. Endicott, Conor F. Hynes, Paal, Edina, Cindy M. Hsieh, Trachiotis, Gregory D.   +9 more
core   +1 more source

Novel challenges in the management of immunoglobulin light chain amyloidosis: from the bench to the bedside

, 2020
Introduction: Immunoglobulin light chain (AL) amyloidosis is one of the most frequent systemic amyloidosis in Western countries. It is caused by a B-cell clone producing a misfolded light chain (LC) that deposits in organs.
Nuvolone M., Palladini G., Basset M., Merlini G.   +3 more
core   +1 more source

A patient with AL amyloidosis presenting with refractory tuberculosis, chest tightness and hypotension: case report

BMC Pulmonary Medicine
Introduction Immunoglobulin light chain (AL) amyloidosis presents a clinical spectrum characterized by diverse manifestations and involvement of multiple organs, posing a significant diagnostic challenge for physicians.
Jun Yang, Mohamed Fahim Fathima Farhath, Huohuan Tian, Linhui Yang, Dan Liu   +4 more
doaj   +1 more source

Budd-Chiari syndrome as the presenting feature of systemic immunoglobulin light chain amyloidosis [PDF]

Budd-Chiari syndrome (BCS), characterised by hepatic venous outflow obstruction, is frequently associated with hypercoagulable states. Systemic immunoglobulin light chain (AL) amyloidosis, on the other hand, commonly presents with bleeding complications.
Leonor Silva, Adriana Guedes, João Luís Miranda, Catarina Salvado, Francisca Carmo, Tiago Guimarães Costa, Albina Moreira   +6 more
core   +1 more source

Apolipoprotein A-IV Cardiac Amyloidosis

JACC: Case Reports
Cardiac amyloidosis is most commonly caused by transthyretin or immunoglobulin light-chain deposition, and contemporary diagnostic algorithms rely on monoclonal protein assessment and technetium-labeled bone scintigraphy to identify these subtypes ...
Irfan Helmy, MD, Varun Sundaram, MD, PhD, MSc, Imran Rashid, MD, PhD, Mohammed Najeeb Osman, MD, Scott Janus, MD, Marc K. Halushka, MD, PhD, Mohamad Karnib, MD, MSc   +6 more
doaj   +1 more source

Cardiac amyloidosis

Annales Academiae Medicae Silesiensis
Amyloidosis is a rare disease characterized by an abnormal accumulation of the amyloid protein in tissues. Amyloidosis can be divided into two main subtypes: transthyretin amyloidosis (ATTR-CA) and immunoglobulin light chain amyloidosis (AL-CA ...
Magdalena Balwierz, Bartosz Gruchlik, Katarzyna Mizia-Stec   +2 more
doaj   +1 more source