Results 11 to 20 of about 138,687 (371)

Safety and efficacy of elapegademase in patients with adenosine deaminase deficiency: A multicenter, open‐label, single‐arm, phase 3, and postmarketing clinical study

Immunity, Inflammation and Disease, 2023
Introduction Adenosine deaminase (ADA) deficiency is an ultrarare inherited purine metabolism disorder characterized by severe combined immunodeficiency. Elapegademase‐lvlr is a new pegylated recombinant bovine ADA used in enzyme‐replacement therapy (ERT)
Masafumi Onodera, Toru Uchiyama, Tadashi Ariga, Masafumi Yamada, Takako Miyamura, Hironori Arizono, Tomohiro Morio   +6 more
doaj   +1 more source

Hyperimmunoglobulin E Syndrome with Tortuous and Massively Dilated Thoracic and Abdominal Aorta: An Extremely Rare Cardiac Presentation of an Immunodeficiency Disease

Journal of Tehran University Heart Center, 2020
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Alireza Golbabaei, Behdad Gharib
doaj   +1 more source

Gene deficiency in activating Fcγ receptors influences the macrophage phenotypic balance and reduces atherosclerosis in mice [PDF]

, 2013
Immunity contributes to arterial inflammation during atherosclerosis. Oxidized low-density lipoproteins induce an autoimmune response characterized by specific antibodies and immune complexes in atherosclerotic patients.
Egido, J., Gomez-Guerrero, C., Lazaro, I., Lopez-Franco, O., Lopez-Parra, V., Lutgens, E., Mallavia, B., Oguiza, A., Ortiz-Muñoz, G., Recio, C.   +9 more
core   +22 more sources

Knowledge and clinical practices of orthodontists regarding the treatment of patients with AIDS

Brazilian Journal of Oral Sciences, 2021
Aim: To evaluate orthodontists’ knowledge and clinical practices regarding the treatment of patients with HIV/AIDS. Methods: Cross-sectional study performed with 655 Brazilian orthodontists based on a previously calculated sample size.
Elisabete S. Rocha, Mario Vedovello Filho, Giovana Cherubini Venezian, Carolina Carmo de Menezes, Silvia Amélia Scudeler Vedovello   +4 more
doaj   +1 more source

Disseminated Postnatal Cytomegalovirus Infection in a Preterm Neonate: Autopsy Case Report [PDF]

Neonatal Medicine, 2021
Treatment guidelines for postnatal cytomegalovirus (pCMV) infection in preterm have not been established yet. Neutropenia, thrombocytopenia, hepatitis, colitis, and sepsis-like disease are among the clinical manifestations, which range from moderate to ...
Ka-Young Kim, Ee-Kyung Kim, Sung-Hye Park, Yoo Jinie Kim, Seung-Han Shin, Han-Suk Kim   +5 more
doaj   +1 more source

Pattern and Predictors of Weight Gain During Pregnancy Among HIV-1-Infected Women from Tanzania [PDF]

, 2003
Progression of HIV disease is often accompanied by weight loss and wasting. Gestational weight gain is a strong determinant of maternal and neonatal outcomes; however, the pattern and predictors of weight gain during pregnancy among HIV-positive women ...
Antelman, Gretchen, Fawzi W., Wafaie, Msamanga, Gernard, Peterson E., Karen, Spiegelman, Donna, Villamor, Eduardo   +5 more
core   +1 more source

Characteristics of COVID-19 infection and antibody formation in patients known at a tertiary immunology department

Journal of Translational Autoimmunity, 2021
Background: Knowledge about COVID-19 infections is expanding, although knowledge about the disease course and antibody formation in patients with an auto-immune disease or immunodeficiency is not fully unraveled yet.
Niels A.D. Guchelaar, Jan A.M. van Laar, Maud A.W. Hermans, Tim B. van der Houwen, Sibel Atmaca, Maurits S. van Maaren, Zana Brkic, Paul L.A. van Daele, Virgil A.S.H. Dalm, P. Martin van Hagen, Saskia M. Rombach   +10 more
doaj   +1 more source

Liver transplantation for type IV glycogen storage disease [PDF]

, 1991
TYPE IV glycogen storage disease is a rare autosomal recessive disorder (also called Andersen's disease1 or amylopectinosis) in which the activity of branching enzyme alpha-1, 4-glucan: alpha-1, 4-glucan 6-glucosyltransferase is deficient in the liver as
Andreas Tzakis, Bannayan, Barbara I. Brown, Brown, Eduardo Yunis, Greene, Illingworth, Ishihara, Ishihara, Mazzaferro, McMaster, Reed, Rick Selby, Ross S. Kendall, Schochet, Stand, Starzl, Thomas E. Starzl   +17 more
core   +1 more source

Correlation between Traditional Chinese Medicine Symptom Patterns and the Renal Function, Immunologic Function Index, and Blood Coagulation Index in Patients with Henoch-Schönlein Purpura Nephritis

Evidence-Based Complementary and Alternative Medicine, 2018
Objective We investigate the correlation between the patterns of traditional Chinese medicine (TCM) syndromes and the damage of renal function, immunologic function index, and blood coagulation index in patients with Henoch-Schönlein purpura nephritis ...
Wanyu Dang, Huimin Yan, Xiaoming Wu, Xiaofang Zhen, Linyi Hou   +4 more
semanticscholar   +1 more source

Unbalanced Immune System: Immunodeficiencies and Autoimmunity [PDF]

, 2016
Increased risk of developing autoimmune manifestations has been identified in different primary immunodeficiencies (PIDs). In such conditions, autoimmunity and immune deficiency represent intertwined phenomena that reflect inadequate immune function ...
CAPALBO, DONATELLA, CIRILLO, EMILIA, D'ASSANTE, ROBERTA, De Cataldis, M, Di Giacomo, C, GALLO, VERA, Gaudino, G, GIARDINO, GIULIANA, Lorello, P, PALAMARO, LOREDANA, PIGNATA, CLAUDIO, PRENCIPE, MARIA ROSARIA, ROMANO, ROBERTA   +12 more
core   +2 more sources