Dermatologica Sinica, 2010 Paraneoplastic pemphigus (PNP) is a life-threatening autoimmune mucocutaneous blistering disease associated with malignancy, particularly lymphoproliferative neoplasms.
Sang Eun Lee, Soo-Chan Kim
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Paraneoplastic pemphigus with airway involvement [PDF]
Respiratory Medicine Case ReportsWe report a case of paraneoplastic pemphigus presenting with acute hypoxemic respiratory failure due to bronchiolitis obliterans which improved with high dose systemic corticosteroids, rituximab, niacinamide and doxycycline.
Oscar A. Estrada Paz, Timothy J. Young
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ECMO Support in Paraneoplastic Pemphigus With Respiratory Failure: A Case Report With Immune Cell Monitoring. [PDF]
Clin Case RepABSTRACT Paraneoplastic pemphigus (PNP) is a life‐threatening autoimmune blistering disease with a mortality rate of 70%–90%, driven largely by respiratory complications such as bronchiolitis obliterans. Managing respiratory failure in these patients remains exceptionally difficult.
Li L, Chen D, Jin L, Shu Q, He J, Li Y.
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Autoantibody repertoire analysis in paraneoplastic pemphigus reveals novel targets linked to mucocutaneous blistering and bronchiolitis obliterans [PDF]
Communications MedicineBackground Paraneoplastic autoimmunity develops as consequences of immune reactions to cancer and exhibits a wide range of clinical manifestations.
Daniel Eriksson +12 more
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Case Report: A middle-aged woman with mediastinal follicular dendritic cell sarcoma complicated by paraneoplastic pemphigus [PDF]
Frontiers in OncologyAs a relatively rare malignant entity, follicular dendritic cell sarcoma (FDCS) of the mediastinum currently suffers from insufficient clinical characterization, warranting more comprehensive studies to optimize therapeutic strategies.
Yongchun Wang +6 more
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Coexistence of Discoid Lupus Erythematosus and Paraneoplastic Pemphigus: A Case Report and Literature Review [PDF]
Clinical, Cosmetic and Investigational Dermatology, 2022 Wasin Saowaluksakul,1 Chutima Seree-aphinan,1 Suthinee Rutnin,1 Kochawan Boonyawat,2 Kumutnart Chanprapaph1 1Division of Dermatology, Department of Medicine, Faculty of Medicine, Ramathibodi Hospital, Mahidol University, Bangkok, Thailand; 2Division of ...
Saowaluksakul W +4 more
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Pulmonary small lymphocytic lymphoma combined with paraneoplastic pemphigus and bronchiolitis obliterans: a case report [PDF]
BMC Pulmonary MedicineBackground Paraneoplastic pemphigus is a rare autoimmune mucocutaneous disease often associated with neoplasms. When complicated with bronchiolitis obliterans, it can lead to irreversible pulmonary dysfunction and carries a high risk of mortality.
Shulei Sun +5 more
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Paraneoplastic pemphigus: Diagnostic mimics, confounders and management challenges in a series of five long‐term survivors from a single centre [PDF]
Skin Health and Disease, 2023 We present a series of five cases who presented to our institution with treatment‐refractory mucosal ulceration, all of whom were subsequently diagnosed with paraneoplastic pemphigus (PNP).
Jonathan S. Emerson +10 more
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Multidisciplinary Management of Paraneoplastic Pemphigus Associated with B-Cell Lymphoma: A Case Report [PDF]
International Medical Case Reports JournalLoulwah Alothman,1,* Azizah Bin Mubayrik,1,* Nuha Alfurayh,2,* Sara Aldosary,1,* Hend M Alotaibi,2,* Abdulmajeed Alajlan2,* 1Oral Medicine and Diagnostic Science Department, College of Dentistry, King Saud University, Riyadh, Saudi Arabia; 2Department of
Alothman L +5 more
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Frontiers in Medicine, 2022 Paraneoplastic pemphigus (PNP) is a rare mucocutaneous autoimmune disease. It has multiple clinical accompanied symptoms by affecting various types of epithelia, including the gastrointestinal and respiratory tract.
Xiao Du +21 more
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