Results 231 to 240 of about 56,657 (298)

Understanding the Phenotypic Heterogeneity Within the Sporadic Creutzfeldt–Jakob Disease MV1 Subtype

Neuropathology and Applied Neurobiology, Volume 52, Issue 3, June 2026.
We present the clinical, pathological and prion biophysical features of three atypical cases of the MV1 subtype of sporadic Creutzfeldt–Jakob disease (sCJD). We propose that these heterozygous cases exist on a spectrum ranging from MM1‐like to VV1‐like phenotypes and recommend that subtyping be performed at pH 6.9 to avoid missing atypical or mixed ...
Satish K. Nemani, Leonardo M. Cortez, Jennifer Myskiw, Ignazio Cali, Stephanie A. Booth, Gerard H. Jansen, Valerie L. Sim   +6 more
wiley   +1 more source

Effect of primary structural variation on cervid prion protein in flexibility, stability, and spontaneous misfolding propensity. [PDF]

Neurobiol Dis
Díaz-Domínguez CM, Eraña H, Peccati F, Vidal E, Charco JM, Sampedro-Torres-Quevedo C, Pérez-Castro MA, Lorenzo NL, Giler S, Telling GC, Geijo M, Requena JR, Jiménez-Osés G, Castilla J.   +13 more
europepmc   +1 more source

Partial Deletion of the Carboxyl-Terminal Signal Sequence of the Cellular Prion Protein Alters Protein Expression via Endoplasmic Reticulum-Associated Degradation. [PDF]

FASEB J
Yoo M, Lee S, Kim J, Cha S, Lee MY, Hwang YJ, Ko WR, Kim T, Kim AR, Trinh THT, Kim YM, Cheon YP, Ryou C.   +12 more
europepmc   +1 more source

Strain-Dependent Susceptibility to Prion Infection Encoded by Arg171 and Lys176 Sheep Prion Protein Polymorphic Variants. [PDF]

J Infect Dis
Espinosa JC, Fernández-Borges N, Marín-Moreno A, Canoyra S, Aguilar-Calvo P, Pintado B, Pericuesta E, Benestad SL, Nonno R, Andréoletti O, Torres JM.   +10 more
europepmc   +1 more source

The structure of complexes between zinc(ii) cations and histidine-rich repeats from the unstructured N-terminal domain of human prion protein. [PDF]

RSC Adv
Nowakowski M, Wolak J, Gielnik M, Piotrowski A, Zhukov I, Żygowska J, Szymańska A, Wiśniewska MD, Bal W, Wärmländer SKTS, Kozak M, Kwiatek WM.   +11 more
europepmc   +1 more source

Cyclin D1/CDK coordination with the cellular prion protein upregulated cell proliferation signaling and preserved neurological function in acute IS rats. [PDF]

Int J Biol Sci
Lin KC, Chen KH, Chiang JY, Chai HT, Huang CR, Chen YL, Wang YT, Guo J, Yip HK.   +8 more
europepmc   +1 more source

Proteins, Prions and Memories

, 2020
openaire   +2 more sources

Prion protein regulates invasiveness in glioblastoma stem cells. [PDF]

BMC Cancer
Prado MB, Coelho BP, Iglesia RP, Alves RN, Boccacino JM, Fernandes CFL, Melo-Escobar MI, Ayyadhury S, Cruz MC, Santos TG, Beraldo FH, Fan J, Ferreira FM, Nakaya HI, Prado MAM, Prado VF, Duennwald ML, Lopes MH.   +17 more
europepmc   +1 more source

Canadian 2021 H-type Bovine Spongiform Encephalopathy case associated with a novel E211K polymorphism in prion protein gene. [PDF]

Prion
Tahir W, Dudas S, Anderson R, Yang J, Bogart S, Santiago-Mateo K, Fang Y, Quaghebeur R.   +7 more
europepmc   +1 more source

NMR structure of the human prion protein with the pathological Q212P mutation reveals unique structural features. [PDF]

, 2010
Legname, G, Giachin, G, Jaremko, Łukasz, Jaremko, Mariusz   +3 more
core