Results 221 to 230 of about 71,281 (314)

Biology and genetics of prions causing neurodegeneration.

Annual Review of Genetics, 2013
S. Prusiner
semanticscholar   +1 more source

Letter to the Editor Regarding Kortazar‐Zubizarreta et al. ‘The Risk of Transmission of Genetic Prion Diseases Is Greater Than 50%’

European Journal of Neurology, Volume 33, Issue 3, March 2026.
Akin Nihat, Tze How Mok, Eric Vallabh Minikel, John Collinge, Simon Mead   +4 more
wiley   +1 more source

Prion and Prion Diseases

, 2020
This review article provides the main information regarding a specific category of infectious diseases of animals and humans, the so-called transmissible spongiform encephalopathies, or prion infections. In a brief introduction explains the need for lighting issues in relation to environmental, veterinary public health importance in traffic and the ...
openaire   +1 more source

Infecting human brain organoids with FFI or sCJD preserves prion traits regardless of host genotype. [PDF]

NPJ Dement
Groveman BR, Foliaki ST, Williams K, Orrù CD, Race B, Zanusso G, Haigh CL.   +6 more
europepmc   +1 more source

Transmission of multiple system atrophy prions to transgenic mice

Proceedings of the National Academy of Sciences of the United States of America, 2013
J. Watts, K. Giles, Abby Oehler, L. Middleton, D. Dexter, S. Gentleman, S. DeArmond, S. Prusiner   +7 more
semanticscholar   +1 more source

Transmission Ratio Distortion in Genetic Prion Diseases: Clarifying Methodological Considerations

European Journal of Neurology, Volume 33, Issue 3, March 2026.
Izaro Kortazar‐Zubizarreta, Africa Manero‐Azua, Hasier Eraña, Joaquín Castilla, Guiomar Perez de Nanclares   +4 more
wiley   +1 more source

Mutant knock-in mice display enhanced susceptibility to pure prion protein fibrils. [PDF]

J Gen Virol
Walsh DJ, Standke H, Kraus A, Watts JC, Supattapone S.   +4 more
europepmc   +1 more source

Contrasting roles of autophagy in cellular prion infection. [PDF]

Autophagy
Abdulrahman B, Heiseke A, Aguib Y, Lu L, Abdelaziz D, Ansari M, Thapa S, Taguchi Y, Gilch S, Schätzl HM.   +9 more
europepmc   +1 more source

Post-conversion sialylation of prions in lymphoid tissues

Proceedings of the National Academy of Sciences of the United States of America, 2015
S. Srivastava, N. Makarava, E. Katorcha, Regina S. Savtchenko, R. Brossmer, I. Baskakov   +5 more
semanticscholar   +1 more source

Yeast Prions: Discovery, Nature, Cellular Manipulation and Implication. [PDF]

J Microbiol Biotechnol
Son M.
europepmc   +1 more source