Results 221 to 230 of about 133,034 (264)

Measurement of propionate turnover in vivo using sodium [2H5]propionate and sodium [13C]propionate

Clinica Chimica Acta, 1989
The outcome for children with inherited disorders of propionate metabolism is poor. To facilitate development of improved treatment in these conditions, we described techniques for the estimation of the rate of production and removal of propionate in vivo.
K Bartlett, J H Walter, G N Thompson
exaly   +3 more sources

The enol of propionic acid

Chemical Communications, 2023
We demonstrate the gas-phase synthesis of prop-1-ene-1,1-diol, the hitherto unreported higher energy tautomer of propionic acid.
Akkad Danho, Artur Mardyukov, Peter R. Schreiner   +2 more
openaire   +2 more sources

Sources of propionate in inborn errors of propionate metabolism

Metabolism, 1990
Amino acids are widely regarded as the most important sources of propionate in disorders of propionate metabolism. Propionate production was measured in the fasting state by continuous infusion of sodium [1-13C]propionate in three children with methylmalonic acidemia (MMA) and three with propionic acidemia (PA).
G N, Thompson, J H, Walter, J L, Bresson, G C, Ford, S L, Lyonnet, R A, Chalmers, J M, Saudubray, J V, Leonard, D, Halliday   +8 more
openaire   +2 more sources

Survey of baked goods for propionic acid and propionates

Food Additives and Contaminants, 1996
One hundred and thirty samples comprising bread (64), hamburger buns (33), pittas (16), cakes (9) and Christmas puddings (8) from various retail outlets in the UK, have been analysed for the preservative propionic acid. Only one sample of bread, two samples of hamburger buns and three samples of pitta contained propionic acid in excess of 1000 mg/kg ...
M J, Scotter, S A, Thorpe, S L, Reynolds, L A, Wilson, P R, Strutt   +4 more
openaire   +2 more sources

The pathway of propionate oxidation

Biochimica et Biophysica Acta, 1953
Abstract 1. 1. The oxidation of labelled propionate in the presence of large pools of unlabelled l -lactate, d -lactate and pyruvate gives rise to the appearance of label in these pools. The appearance of label suggests that the compounds mentioned are in equilibrium with the actual intermediates.
H R, MAHLER, F M, HUENNEKENS
openaire   +2 more sources

Cardiomyopathy in propionic acidaemia

European Journal of Pediatrics, 1993
Following the death of a patient with propionic acidaemia with a cardiomyopathy we reviewed 19 patients with the same disorder for evidence of cardiomyopathy. Six patients were found to meet the diagnostic criteria. Three patients died and in the other three the cardiac disease resolved completely.
A F, Massoud, J V, Leonard
openaire   +2 more sources

Methylmalonic and propionic aciduria

American Journal of Medical Genetics Part C: Seminars in Medical Genetics, 2006
AbstractMethylmalonic and propionic aciduria (PA) are the most frequent forms of branched‐chain organic acidurias. These autosomal recessive disorders result from deficient activity of methylmalonyl‐CoA mutase and propionyl‐CoA carboxylase, respectively.
Federica, Deodato, Sara, Boenzi, Filippo M, Santorelli, Carlo, Dionisi-Vici   +3 more
openaire   +2 more sources

The Reaction Rates of Propionic and Acetic Propionic Anhydrides

The Journal of Chemical Physics, 1936
The infrared absorption spectra of mixtures of water and acetic propionic and of propionic anhydrides have been measured in the region from 5μ to 6.4μ. The intensity of the bands was found to decrease with time. By using the relative intensity of the anhydride band the reaction rate was calculated for three concentrations.
E. S. Barr, E. K. Plyler
openaire   +1 more source

Inborn errors of propionate metabolism: Methylmalonic and propionic acidaemias

Journal of Paediatrics and Child Health, 1992
openaire   +2 more sources

Impact of electron scavenging during electric current generation from propionate by a Geobacter co-culture

Chemical Engineering Journal, 2021
Pier-Luc Tremblay, Tian Zhang
exaly