Exploring Desmin as a Potential Modifier in Duchenne Muscular Dystrophy–Associated Cardiomyopathy
ABSTRACT Aim Duchenne muscular dystrophy (DMD), a rare X‐linked genetic disorder, is affecting skeletal and cardiac muscles due to the loss of the dystrophin protein. Modifier proteins, whose expression is altered in DMD patients, may influence disease progression.
Brice‐Emmanuel Guennec +12 more
wiley +1 more source
Proteomic analysis of nemaline myopathy in infants reveals distinct common dysregulated proteins and cellular pathways. [PDF]
Hedberg-Oldfors C +4 more
europepmc +1 more source
SARCOMERE REMODELING INDUCED BY DISTRACTION
Vincent J. Caiozzo +3 more
openalex +1 more source
Targeted homozygous deletion of M-band titin in cardiomyocytes prevents sarcomere formation [PDF]
Hanny Musa +5 more
openalex +1 more source
ABSTRACT In this study, we developed a piezoelectric‐polydimethylsiloxane (pz‐PDMS) composite by blending poly(vinylidene fluoride‐co‐trifluoroethylene) (P(VDF‐TrFE)) with PDMS to create a biocompatible, mechanoelectrical responsive material. The pz‐PDMS was synthesized with varying piezoelectric concentrations (0%, 1%, 3%, and 5%) and characterized ...
Alexis P. Applequist +3 more
wiley +1 more source
M line–deficient titin causes cardiac lethality through impaired maturation of the sarcomere [PDF]
Stefanie Weinert +4 more
openalex +1 more source
Apical Sarcomere-like Actomyosin Contracts Nonmuscle Drosophila Epithelial Cells.
Jonathan S. Coravos, Adam C. Martin
semanticscholar +1 more source
A Comparison of the Force‐Velocity Relationship of Bonobo and Human Muscle Fibers
ABSTRACT It has been reported that the muscles of chimpanzees and bonobos have “super strength” and it has been suggested that this is attributable to a larger specific tension and specific power of their muscles. To investigate this we compared the force‐velocity relationship in 85 human and 49 bonobo (Pan paniscus) skinned fibers at 15°C. Fibers were
Hans Degens +2 more
wiley +1 more source
Hypergravity Enhances Stretch Sensitivity in Rat Cardiomyocytes via Increased Expression and Activity of Stretch-Activated Channels. [PDF]
Kamkin AG +8 more
europepmc +1 more source

