Monoclonal Gammopathy–Associated Scleromyxedema Presenting as Leonine Facies [PDF]
, 2018 Peer Reviewedhttps://deepblue.lib.umich.edu/bitstream/2027.42/146383/1/art40530.pdfhttps://deepblue.lib.umich.edu/bitstream/2027.42/146383/2/art40530_am ...
Khanna, Dinesh +2 more
core +1 more source
Letter on 'European dermatology forum S1-guideline on the diagnosis and treatment of sclerosing diseases of the skin, Part 2: Scleromyxedema, scleredema and nephrogenic systemic fibrosis' [PDF]
, 2018 We read with interest the guidelines recently published on sclerosing diseases of the skin (Part 2: Scleromyxedema, scleredema and nephrogenic systemic fibrosis)[1, 2].
Blankestijn, Peter +4 more
core +2 more sources
Dupilumab improves itch, but not fibrosis, in a patient with scleromyxedema: A case report [PDF]
SAGE Open Med Case RepScleromyxedema is a rare, chronic mucinosis characterized by widespread skin fibrosis and an associated monoclonal gammopathy. Therapeutic options remain limited.
Peri K +4 more
europepmc +2 more sources
Scleromyxedema without paraproteinemia
International Journal of Dermatology, 2014 AbstractBackgroundScleromyxedema is a rare generalized form of lichen myxedematosus, a chronic cutaneous mucinosis of unknown etiology usually associated with a monoclonal gammopathy and underlying systemic disorders. It is characterized by the presence of lichenoid papules and diffuse indurations of the skin.
Abarzúa, Alvaro A. +3 more
openaire +3 more sources
Clinical Characteristics and Treatment Outcomes of Scleromyxedema: A 10-Year Retrospective Survey
Case Reports in Dermatology, 2022 Scleromyxedema is a rare but important mucinosis disorder of the skin that is presented with dermatological manifestations such as waxy papules, diffuse induration, and nondermatologic involvements like neurological and renal disorders.
Abtin Ansari +6 more
semanticscholar +1 more source
Systemic Sclerosis Mimics [PDF]
, 2019 Many clinical conditions are presenting with sclerosis of the skin and with tissue fibrosis. These conditions may be confused with systemic sclerosis (SSc, scleroderma).
Kodet, Ondřej, Oreská, Sabína
core +2 more sources
Autologous stem cell transplantation in a patient with scleromyxedema
eJHaem, 2022 A 46-year-old male was diagnosed with scleromyxedema on a skin biopsy in 2014. Scleromyxedema is a rare disorder characterized by papular lichenoid eruption with sclerosing skin infiltration due to the deposition of glycosaminoglycan in the papular and ...
S. Nathan, C. Ustun
semanticscholar +1 more source
Sklerosierende Erkrankungen der Haut
JDDG: Journal der Deutschen Dermatologischen Gesellschaft, Volume 23, Issue 10, Page 1282-1303, October 2025.Zusammenfassung Sklerosierende Hautkrankheiten sind eine Gruppe unterschiedlicher dermatologischer Erkrankungen, die durch fibrotische Veränderungen gekennzeichnet sind und die Lebensqualität der Patienten stark einschränken können. Diese Erkrankungen treten häufig mit kutanen Manifestationen auf und können in bestimmten Fällen auch extrakutanes Gewebe
Yasamin Kalantari +4 more
wiley +1 more source
Systemic sclerosis without antinuclear antibodies or Raynaud's phenomenon: a multicentre study in the prospective EULAR Scleroderma Trials and Research (EUSTAR) database [PDF]
, 2017 Objective. To assess patients with SSc who present without circulating ANAs or RP. Methods. Five thousand three hundred and ninety patients who fulfilled the ACR criteria for SSc and were enrolled in the EULAR Scleroderma Trials and Research (EUSTAR ...
Carreira, Patricia E. +9 more
core
Combination of intravenous immunoglobulin, oral prednisone, and methotrexate for managing scleromyxedema: case report and literature discussion. [PDF]
Dermatol Reports, 2023 The generalized and sclerodermic form of lichen myxedematosus, known as scleromyxedema (SMX), is a chronic mucinosis that manifests cutaneously and has multiple systemic comorbidities.
Fasano G +3 more
europepmc +2 more sources