Results 1 to 10 of about 66,314 (265)

Urticaria pigmentosa and systemic mastocytosis [PDF]

Clinical Case Reports, 2023
Key Clinical Message Additional investigations for systemic involvement should be initiated once the diagnosis of cutaneous mastocytosis has been established in an adult patient.
Jonathan Keow, Benjamin Chin‐Yee, Cyrus C. Hsia, Kara Robertson   +3 more
doaj   +4 more sources

Systemic Mastocytosis - a Diagnostic Challenge [PDF]

Revista Brasileira de Hematologia e Hemoterapia, 2014
Mastocytosis refers to a group of disorders characterized by the infiltration of clonally derived mast cells to the skin or extracutaneous tissues resulting in a heterogeneous clinical picture. It is a rare hematologic disorder in all its forms.
Galzerano, A, Lladó, AC, Mihon, C, Silva, M   +3 more
core   +9 more sources

Phenotypic and genotypic characteristics of mastocytosis according to the age of onset. [PDF]

PLoS ONE, 2008
Adult's mastocytosis is usually associated with persistent systemic involvement and c-kit 816 mutation, while pediatrics disease is mostly limited to the skin and often resolves spontaneously.
Fanny Lanternier, Annick Cohen-Akenine, Fabienne Palmerini, Frédéric Feger, Ying Yang, Yael Zermati, Stéphane Barète, Beatrix Sans, Cédric Baude, David Ghez, Felipe Suarez, Richard Delarue, Philippe Casassus, Christine Bodemer, Adeline Catteau, Frédérique Soppelsa, Katia Hanssens, Michel Arock, Hagay Sobol, Sylvie Fraitag, Danièle Canioni, Alain Moussy, Jean Marie Launay, Patrice Dubreuil, Olivier Hermine, Olivier Lortholary, AFIRMM network   +26 more
doaj   +9 more sources

Adult mastocytosis: a review of the Santo António Hospital 's experience and an evaluation of World Health Organization criteria for the diagnosis of systemic disease [PDF]

Anais Brasileiros de Dermatologia, 2014
BACKGROUND: Mastocytosis is a clonal disorder characterized by the accumulation of abnormal mast cells in the skin and/or in extracutaneous organs. OBJECTIVES: To present all cases of mastocytosis seen in the Porto Hospital Center and evaluate the ...
Iolanda Conde Fernandes, Maria dos Anjos Teixeira, Ines Freitas, Manuela Selores, Rosario Alves, Margarida Lima   +5 more
doaj   +4 more sources

Systemic Lymphadenopathic Mastocytosis with Eosinophilia

Diagnostics, 2022
Systemic mastocytosis is a neoplastic proliferation of mast cells that most frequently involves cutaneous sites. Mastocytosis involves various extracutaneous sites, but the lymph node is rare.
Soyoung Im, Jeong-A Kim, Gyeongsin Park, Uiju Cho   +3 more
doaj   +3 more sources

Fire ant-venom anaphylaxis prevalence in the general population and patients with systemic mastocytosis [PDF]

Frontiers in Allergy
BackgroundStinging Hymenoptera can induce fatal anaphylaxis, especially in patients with systemic mastocytosis. Fire ants, Solenopsis invicta and S. richteri, from South America have recently colonized three continents.
Jeremy C. McMurray, Jeremy C. McMurray, Brandon J. Schornack, Brandon J. Schornack, Karla E. Adams, Robert L. McCoy, Amanda K. Marshall, Janet A. Brunader, Irina Maric, Dean D. Metcalfe, Nathan A. Boggs, Nathan A. Boggs   +11 more
doaj   +2 more sources

Systemic Mastocytosis with Smoldering Multiple Myeloma: Report of a Case [PDF]

Case Reports in Oncological Medicine, 2016
Systemic mastocytosis (SM) is a disease characterized by a clonal infiltration of mast cells affecting various tissues of the body. It is grouped into six different subtypes according to the World Health Organization classification. It is called indolent
Sassine Ghanem, Gwenalyn Garcia, Liu Ying, Matthew Hurford, Marcel Odaimi   +4 more
doaj   +2 more sources

Mastocytosis. General concepts, view on patient management, examples of clinical course of the disease

Zdorovʹe Rebenka, 2022
Background. Mastocytosis is a disease characterized by the presence of mast cells in various organs. The skin is affected most often. Almost every patient diagnosed with mastocytosis has skin lesions.
O.L. Statkevych, T.V. Sviatenko
doaj   +1 more source

Targeted therapy for advanced forms of systemic mastocytosis in real clinical practice

Онкогематология, 2023
Background. Mastocytosis is a heterogeneous group of diseases that are characterized by excessive proliferation and accumulation of clonal (neoplastic) mast cells in one or more organs.
D. I. Shikhbabaeva, O. Yu. Vinogradova, A. L. Neverova, M. M. Pankrashkina, M. V. Chernikov, E. O. Detkina, Yu. N. Kobzev, S. G. Malakho, V. V. Ptushkin   +8 more
doaj   +1 more source

SWATH-MS identification of CXCL7, LBP, TGFβ1 and PDGFRβ as novel biomarkers in human systemic mastocytosis

Scientific Reports, 2022
Mastocytosis is a rare myeloproliferative disease, characterised by accumulation of neoplastic mast cells in one or several organs. It presents as cutaneous or systemic.
R. L. J. Graham, A. A. McMullen, G. Moore, N. C. Dempsey-Hibbert, B. Myers, C. Graham   +5 more
doaj   +1 more source