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Scleroderma with Nodular Scleroderma
Case Reports in Dermatology, 2016 Background: Nodular scleroderma is a rare variant of scleroderma which can occur in connection with systemic sclerosis or morphea. A biopsy from the lesion can demonstrate the scleroderma pattern, i.e., keloid pattern or mixed type.Chutika Srisuttiyakorn, Kobkul Aunhachoke +1 moredoaj +2 more sourcesAntiphospholipid Antibodies and Systemic Scleroderma
Turkish Journal of Hematology, 2013 Objective: Antiphospholipid antibodies (APLs) could be associated with an increased risk of vascular pathologies in systemic scleroderma. The aim of our study was to search for APLs in patients affected by systemic scleroderma and to evaluate their ...Awa Oumar Touré, Fatimata Ly, Abibatou Sall, Alassane Diatta, Macoura Gadji, Moussa Seck, Blaise Faye, Tandakha Dieye, Saliou Diop +8 moredoaj +2 more sourcesDIAGNOSTIC VALUE OF CERULOPLASMIN IN SYSTEMIC SCLERODERMA
Медицинская иммунология, 2019 Objective of study: refining immune diagnostics of systemic scleroderma through determining ceruloplasmin antibodies, its amount and enzymatic activity, as well as control of effectiveness of therapy with ceruloplasmin-based immobilized ...O. I. Emelyanova, I. P. Gontar, O. A. Rusanova, I. A. Zborovskaya +3 moredoaj +3 more sourcesBarriers to care in juvenile localized and systemic scleroderma: an exploratory survey study of caregivers' perspectives. [PDF]
Pediatr Rheumatol Online J, 2023 BACKGROUND: Juvenile localized scleroderma (LS) and systemic sclerosis (SSc) are rare pediatric conditions often associated with severe morbidities. Delays in diagnosis are common, increasing the risk for permanent damage and worse outcomes.Stubbs LA, Ferry AM, Guffey D, Loccke C, Wade EM, Pour P, Ardalan K, Chira P, Ganske IM, Glaser D, Higgins G, Luca N, Moore KF, Sivaraman V, Stewart K, Vasquez-Canizares N, Hunt RD, Maricevich RS, Torok KS, Li SC, Childhood Arthritis, Rheumatology Research Alliance (CARRA) Scleroderma Workgroup. +21 moreeuropepmc +2 more sourcesErectile dysfunction is frequent in systemic sclerosis and associated with severe disease: a study of the EULAR Scleroderma Trial and Research group [PDF]
, 2012 INTRODUCTION: Erectile dysfunction (ED) is common in men with systemic sclerosis (SSc) but the demographics, risk factors and treatment coverage for ED are not well known.Smith, Vanessa, Alan Tyndall, Garcia de la Peña Lefebvre, Paloma, Edoardo Rosato, Vanessa Smith, Jean Sibilia, Ingo Tarner, Gabriela Riemekasten, Ulrich A. Walker, Walid Abdel Atty Mohamed, Himsel, Andrea, Piotr Wiland, Rednic, Simona, Morović-Vergles, Jadranka, Andrea Himsel, Jose Pereira Da Silva, Allanore, Yannick, Jadranka Morovic Vergles, Anna T. Onken, Starovojtova M. Nikolaevna, Walker, Ulrich A., Farge-Bancel, Dominique, Dominique Farge Bancel, Tarner, Ingo, Mohamed, Walid Ahmed Abdel Atty, Paloma De La Pena Lefebvre, Paolo Airo, Riemekasten, Gabriela, Walker, Ulrich A, Onken, Anna Theresa, Tyndall, Alan, de la Peña Lefebvre, Paloma G., Chingching Foocharoen, Onken, Anna T, Stamenkovic, Bojana, Caramaschi, Paola, Rosato, Edoardo, Airó, Paolo, Dominique Farge-Bancel, Simona Rednic, Wiland, Piotr, Pereira da Silva, José António, Sibilia, Jean, Nikolaevna, Starovojtova M, Paola Caramaschi, Nikolaevna, Starovojtova M., Bojana Stamenkovic, Foocharoen, Chingching, Hachulla, Eric, Thomas Hugle, Distler, Oliver, Ulrich A Walker, Yannick Allanore, Stamenkovic, Bojan, Abdel Atty Mohamed, Walid A., Hügle, Thomas, Jadranka Morović-Vergles, et al, Pereira da Silva, José A., Starovojtova M Nikolaevna, Eric Hachulla, Anna T Onken, Oliver Distler +62 morecore +1 more sourceApplication and performance of disease activity indices proposed for patients with systemic sclerosis in an international cohort of patients with juvenile systemic sclerosis [PDF]
, 2023 Funding Information: The author(s) disclosed receipt of the following financial support for the research, authorship and/or publication of this article: the inception cohort project is supported by an unrestricted grant from the Joachim Herz Stiftung ...Adrovic, Amra, Santos, Maria Jose, Torok, Kathryn S., Stanevicha, Valda, Kostik, Mikhail, Bica, Blanca, Kallinich, Tilmann, Nielsen, Susan, Sakamoto, Ana Paula, Marrani, Edoardo, Sifuentes-Giraldo, Alberto, Avcin, Tadej, Brunner, Juergen, Kasapcopur, Ozgur, Anton, Jordi, Torok, Kathryn S, Terreri, Maria Teresa, Appenzeller, Simone, Helmus, Nicola, Harel, Liora, Sztajnbok, Flavio, Katsicas, Maria, Eleftheriou, Despina, Nemcova, Dana, Feldmann, Brian, Brunner, Jürgen, Klotsche, Jens, Patwardhan, Anjali, Horneff, Gerd, Minden, Kirsten, Berntson, Lillemor, Battagliotti, Cristina, Foeldvari, Ivan +32 morecore +1 more sourceSystemic Scleroderma with Linear Scleroderma.
Nishi Nihon Hifuka, 2002 53歳の女性にみられた線状強皮症を伴った全身性強皮症の1例を報告した。1975年頃より間質性肺炎と手指の硬化があり,当院呼吸器科で全身性強皮症としてプレドニンの内服治療を受けていた。数年前より手指の硬化が著明になると共に前胸部に皮下硬結を自覚。数ヵ月前より皮下硬結の延長が認められたため当科を受診した。初診時,前胸部に淡紅色の線状を呈する皮下硬結が認められた。血液検査所見では,抗核抗体が320倍と陽性,KL-6も643 U/mlと上昇していた。胸部X線·CT像では,間質性肺炎が認められた。前胸部の皮下硬結よりの皮膚生検で真皮の膠原線維の増生と真皮血管周囲の軽度リンパ球浸潤がみられた。以上の所見より,線状強皮症を伴った全身性強皮症と診断した ...YAMAMURA, Mahiro, OYAMA, Zuiei, SEISHIMA, Mariko +2 moreopenaire +1 more sourceThe systemic lupus erythematosus IRF5 risk haplotype is associated with systemic sclerosis [PDF]
, 2013 Systemic sclerosis (SSc) is a fibrotic autoimmune disease in which the genetic component plays an important role. One of the strongest SSc association signals outside the human leukocyte antigen (HLA) region corresponds to interferon (IFN) regulatory ...Schuerwegh, A. J., Alexander Kreuter (592), Herrick Ariane, Martín J., Carmona, F.D., Jacob M van Laar, Madelon C Vonk, Voskuyl AE, Denton C, Mónica Fernández-Castro, Martin Jose-Ezequiel, Hunzelmann Nicolas, Airó Paolo, Ariane Herrick (214049), Claudio Lunardi (12868), Paul Shiels (276244), Witte, T. de, Camps, M. T., Voskuyl Alexandre E., Distler, J.H., Riemekasten, Gabriela, H W Distler, Egurbide, María Victoria, Mónica Fernández-Castro (276238), Radstake TR, Camps, M.T., Egurbide, M. V., Simeón, C.P., Carreira, Patricia E., Airó, P., Kreuter, Alexander, Camps María Teresa, Airó, Paolo, Scorza, Raffaella, Martín, Javier, the Spanish Scleroderma Group, Nicolas Hunzelmann, Beltrán Emma, Madelon C. Vonk (213950), Torsten Witte, Javier Martín (2584444), Sáez-Comet, Luis, van Laar, J.M., María Teresa Camps, Callejas, J.L., Carmen Fonseca (214061), Airó P, Martin, J.E., Madhok, Rajan, Fernández Castro M, Kreuter, A., Herrick A, Carmen P. Simeón (5650816), Riemekasten Gabriela, Beltrán E, Radstake, T. R., Shiels, Paul G., Alexandre E. Voskuyl (213961), Carreira, P.E., Vonk, M.C., Lorenzo Beretta, Carreira PE, Hunzelmann N, Kreuter A, Patricia E. Carreira (276236), Beltrán, Emma, Carmona F. David, Rajan Madhok, Worthington J, Gabriela Riemekasten, Scorza R, Vonk MC, Simeón Carmen P., Witte, Torsten, Camps, María Teresa, Carmona FD, Herrick, A., Schuerwegh AJ, Paolo Airó, Distler, Jörg H W, Radstake Timothy R. D. J., Distler, J.H.W., Alexandre E Voskuyl, et al., José Luis Callejas (276237), Schuerwegh, Annemie J, Jane Worthington, Laar, Jacob M. van, Madhok R, Callejas, José Luis, Martín, J. E., Jacob M. van Laar (177818), Vonk Madelon C., Javier Martín, Beretta, Lorenzo, Emma Beltrá, Timothy R. D. J. Radstake (168224), Shiels Paul, Jörg H. W. Distler (3196062), Madhok Rajan, Callejas JL, Beltrán, E., Martin, Jose Ezequiel, Schuerwegh, A.J., Witte Torsten, Distler, J.H. W., Raffaella Scorza, Voskuyl, Alexandre E., Carmen P Simeón, Carmona, F David, Spanish Scleroderma, Claudio Lunardi, Rajan Madhok (23535), Group ", Voskuyl, A.E., Worthington, Jane, Egurbide, M.V., Jörg H W Distler, Saez-Comet, L., Callejas-Rubio, José Luis, Voskuyl, Alexandre E, van Laar JM, Simeón, Carmen P., Gabriela Riemekasten (276243), Denton, Christopher, Schuerwegh Annemie J., Camps MT, Paolo Airó (5650819), Witte T, Carmona, Francisco David, Denton, C., Lunardi, C., Fernández-Castro Mónica, Simeón, Carmen P, Riemekasten G, Luis Sáez-Comet (276239), Fonseca Carmen, Fernández-Castro, M., Herrick, Ariane, Timothy R D J Radstake, Scorza, R., Madhok, R., Denton Christopher, Fonseca, Carmen, Beretta L, Christopher Denton, Luis Sá Ez-Comet, Worthington, J., José Luis Callejas, Beretta, L., Annemie J Schuerwegh, Kreuter Alexander, Simeón CP, Nicolas Hunzelmann (213980), Lunardi Claudio, Jane Worthington (23502), Torsten Witte (32240), Emma Beltrán (276240), Lunardi, Claudio, Shiels, P., Carreira Patricia E., Fonseca C, Sáez Comet L, Shiels, Paul, Martín, J., Carmen Fonseca, F. David Carmona (276235), Riemekasten, G., Witte, T., Luis Sáez-Comet, Radstake, Timothy R. D. J., Jö Rg, van Laar, Jacob M., Egurbide María Victoria, Distler, Jörg H. W., Fernández-Castro, Monica, Radstake, T.R.D.J., van Laar Jacob M., Ariane Herrick, Emma Beltrán, Christopher Denton (276245), Alexander Kreuter, Martín Javier, Mó Nica Ferná Ndez-Castro, Shiels P, Vonk, Madelon C, Carreira, Patricia E, Fonseca, C., Paul Shiels, Callejas José Luis, Carmen P Simeó N, Martin JE, Lorenzo Beretta (214056), Egurbide MV, Distler Jörg H. W., Raffaella Scorza (214013), Vonk, Madelon C., María Victoria Egurbide, Hunzelmann, Nicolas, Carmona, F. David, Schuerwegh, Annemie J., Jose-Ezequiel Martin, Beretta Lorenzo, Distler, J. H., Patricia E Carreira, María Teresa Camps (276241), Scorza Raffaella, Annemie J. Schuerwegh (213966), Sáez-Comet Luis, F David Carmona, María Victoria Egurbide (276242), Laar, J.M. van, Hunzelmann, N., Worthington Jane, Martin, Jose-Ezequiel, van Laar, Jacob M, Spanish Scleroderma Group, Jose-Ezequiel Martin (213926), Distler JH, Radstake, Timothy R D J +219 morecore +1 more source