Results 11 to 20 of about 13,419 (176)

Ichthyosiform mycosis fungoides with alopecia and atypical membranous nephropathy

Indian Journal of Dermatology, Venereology, and Leprology, 2011
We describe here a rare case of variant of mycosis fungoides (MF): ichthyosiform MF with alopecia and atypical membranous nephropathy. The diagnosis was made based on the following findings: generalized ichthyosis-like eruption, alopecia, enlarged superficial lymph nodes, proteinuria, and hematuria, the histological features of the skin biopsy from ...
Zhou, Qiang, Zhu, Kejian, Yu, Haiyan, Cheng, Hao   +3 more
semanticscholar   +5 more sources

Post-Transplant Thrombotic Microangiopathy due to a Pathogenic Mutation in Complement Factor I in a Patient With Membranous Nephropathy: Case Report and Review of Literature

Frontiers in Immunology, 2022
Thrombotic microangiopathy (TMA) is characterized by microangiopathic hemolytic anemia, thrombocytopenia and organ injury occurring due to endothelial cell damage and microthrombi formation in small vessels.
Maryam Saleem, Sana Shaikh, Zheng Hu, Nicola Pozzi, Anuja Java   +4 more
doaj   +4 more sources

Phospholipase A2 receptor-negative membranous nephropathy presenting as a rare renal manifestation of IgG4-related disease [PDF]

SAGE Open Medical Case Reports
IgG4-related disease is a fibroinflammatory condition characterized by dense lymphoplasmacytic infiltrates rich in IgG4-positive plasma cells affecting multiple organs.
Srikar Sama, Alexander Weickhardt, Preethi Subramanian, Pooja Reddy   +3 more
doaj   +3 more sources

A membranous nephropathy variant mimicking minimal change disease [PDF]

The Journal of Pathology: Clinical Research
This study characterizes a novel disease pattern of membranous nephropathy (MN) that exhibits overlapping clinicopathological features with minimal change disease (MCD), termed ‘MCD‐like MN’.
Chuqi Pan, Silin Xiang, Mengya Jiang, Yuan Li, Biao Huang, Tian Ye, Yuanyuan Du, Xuanli Tang, Yuan Yuan   +8 more
doaj   +3 more sources

Case Report: Atypical Manifestations Associated With FOXP3 Mutations. The “Fil Rouge” of Treg Between IPEX Features and Other Clinical Entities?

Frontiers in Immunology, 2022
IntroductionThe Forkhead box protein P3 (FOXP3) is a transcription factor central to the function of regulatory T cells (Treg). Mutations in the FOXP3 gene lead to a systemic disease called immune dysregulation, polyendocrinopathy, and enteropathy, an X ...
Micaela Gentile, Micaela Gentile, Maurizio Miano, Paola Terranova, Stefano Giardino, Maura Faraci, Filomena Pierri, Enrico Drago, Daniela Verzola, Gianmarco Ghiggeri, Enrico Verrina, Andrea Angeletti, Barbara Cafferata, Alice Grossi, Isabella Ceccherini, Gianluca Caridi, Francesca Lugani, Lorenzo Nescis, Enrico Fiaccadori, Enrico Fiaccadori, Luca Lanino, Daniela Fenoglio, Daniela Fenoglio, Edoardo La Porta, Edoardo La Porta   +24 more
doaj   +2 more sources

Application of C5 inhibitors in glomerular diseases in 2021 [PDF]

Kidney Research and Clinical Practice, 2022
The complement pathway is an essential mechanism in innate immunity, but it is also involved in multiple pathologies. For kidney diseases, strong evidence of a dysregulation in the alternative pathway in atypical hemolytic uremic syndrome (aHUS) led to ...
Alexis Werion, Eric Rondeau
doaj   +2 more sources

Primary membranous nephropathy with concomitant IgA nephropathy

Saudi Journal of Kidney Diseases and Transplantation, 2019
Membranous nephropathy (MN), an autoimmune glomerulonephritis which can occur in primary and secondary forms, is one of the most common inflammatory glomerulopathies in elderly patients.
Reza Khorsan, Ramy M Hanna, Khalid Ameen, Farid Arman, Niloofar Nobakht, Huma Hasnain, Ashley Hyunh, Anjay Rastogi   +7 more
doaj   +2 more sources

Deposition of the Membrane Attack Complex in Healthy and Diseased Human Kidneys

Frontiers in Immunology, 2021
The membrane attack complex—also known as C5b-9—is the end-product of the classical, lectin, and alternative complement pathways. It is thought to play an important role in the pathogenesis of various kidney diseases by causing cellular injury and tissue
Jacob J. E. Koopman, Jacob J. E. Koopman, Mieke F. van Essen, Helmut G. Rennke, Aiko P. J. de Vries, Cees van Kooten   +5 more
doaj   +3 more sources

Clinical and pathologic features of primary membranous nephropathy in Turkey: a multicenter study by the Turkish Society of Nephrology Glomerular Diseases Working Group [PDF]

Renal Failure, 2022
Background We aimed to evaluate the features of primary membranous nephropathy (MNP) in Turkish people.Methods This is a retrospective analysis of patients with biopsy-proven primary MNP.
Abdulmecit Yildiz, Sena Ulu, Aysegul Oruc, Ali Riza Ucar, Savas Ozturk, Selma Alagoz, Necmi Eren, Ismail Kocyigit, Simal Koksal Cevher, Ali Burak Haras, Abdullah Sumnu, Turgay Arinsoy, Garip Sahin, Gultekin Suleymanlar, Caner Cavdar, Gizem Kumru Sahin, Ilhan Kurultak, Abdulkadir Unsal, Gulizar Sahin, Sinan Kazan, Erhan Tatar, Mehmet Dıkec, Belda Dursun, Hayriye Sayarlioglu, Kultigin Turkmen, Ayse Serra Artan, Nimet Aktas, Zulfikar Yilmaz, Ahmet Behlul, Hamad Dheir, Sim Kutlay, Nurhan Seyahi   +31 more
doaj   +3 more sources

IgG4-related membranous glomerulonephritis and generalized lymphadenopathy without pancreatitis: a case report [PDF]

BMC Nephrology, 2017
Background IgG4-related disease is a recently described pathologic entity. This is the case of a patient with nephrotic syndrome and lymphadenopathy due to IgG4-related disease.
Justine Huart, Stéphanie Grosch, Christophe Bovy, Michel Moutschen, Jean-Marie Krzesinski   +4 more
doaj   +2 more sources