Results 31 to 40 of about 2,748,091 (304)

Leucinosis, or maple syrup urine disease (lecture and a clinical case)

Alʹmanah Kliničeskoj Mediciny, 2020
Maple syrup urine disease (leucinosis, short-chain ketoaciduria, branched-chain disease, branched-chain ketonuria) is an autosomal recessive disorder which is a consequence of the deficient branched-chain alpha ketoacid dehydrogenase complex.
Ju. A. Tsareva, N. I. Zryachkin, M. A. Kuznetsova, E. V. Bogacheva   +3 more
doaj   +1 more source

A pilot, short-term dietary manipulation of branched chain amino acids has modest influence on fasting levels of branched chain amino acids

Food & Nutrition Research, 2016
Background: Elevated fasting levels of branched chain amino acids (BCAAs: valine, isoleucine, leucine) in venous blood are associated with a variety of metabolic impairments, including increased risk of type 2 diabetes (T2D).
Nicole Landa Cavallaro, Jamie Garry, Xu Shi, Robert E. Gerszten, Ellen J. Anderson, Geoffrey A. Walford   +5 more
doaj   +1 more source

Aminosäuren – Leitlinie Parenterale Ernährung, Kapitel 4 [PDF]

, 2009
Protein catabolism should be reduced and protein synthesis promoted with parenteral nutrion (PN). Amino acid (AA) solutions should always be infused with PN. Standard AA solutions are generally used, whereas specially adapted AA solutions may be required
Blumenstein, I, Stein, J, Goeters, C, Working group for developing the guidelines for parenteral nutrition of The German Association for Nutritional Medicine, Schulz, R., Boehles, HJ, Blumenstein, I., Schulz, R, Blumenstein, Irina Ursula, Goeters, Christiane, Boehles, H. J., Goeters, C., Böhles, Hansjosef, Stein, Jürgen, Schulz, Ralf-Joachim, Stein, J.   +15 more
core   +1 more source

The bitterness inhibition effect of ferulic acid and its phenyl ring substituted derivatives on branched chain amino acids

Shipin yu jixie, 2023
Objective: This study aimed to explore the effect of group changes at the third position of the benzene ring of ferulic acid （FA） on the bitterness inhibition effect of branched chain amino acids and their flavor characteristics.
WANG Hao, LI Jiaxing, ZHENG Jianxian
doaj   +1 more source

Dataset describing the amino acid catabolism of Thermoanaerobacter pseudethanolicus

Data in Brief
The dataset depicts the catabolism of branched-chain amino acids by Thermoanaerobacter pseudethanolicus in the presence of thiosulfate under different culture conditions. The results reveal that the strain can degrade all three branched-chain amino acids
Johann Orlygsson, Sean Michael Scully
doaj   +1 more source

Host’s demand for essential amino acids is compensated by an extracellular bacterial symbiont in a hemipteran insect model

Frontiers in Physiology, 2022
Plant sap is a nutritionally unbalanced diet that constitutes a challenge for insects that feed exclusively on it. Sap-sucking hemipteran insects generally overcome this challenge by harboring beneficial microorganisms in their specialized symbiotic ...
Minoru Moriyama, Takema Fukatsu, Takema Fukatsu, Takema Fukatsu   +3 more
doaj   +1 more source

Association of Circulating Branched-Chain Amino Acids with Cardiovascular Diseases: A Mendelian Randomization Study

, 2023
Background: There have been reports linking branched-chain amino acids (BCAAs) to the hazard of various cardiovascular diseases (CVDs); however, the causal role of this relationship is still unclear.
Xuanyang Wang, Ying Li, Huan Xu, Yuntao Zhang, Guannan Geng, Xiaoqing Xu, Lin Liu, Ziqi Wang, Lulu Wang   +8 more
core   +1 more source

Isolated branched-chain amino acid intake and muscle protein synthesis in humans: a biochemical review

Einstein (São Paulo)
Alongside a proper diet, ergogenic aids with potential direct and/or indirect physical performance enhancing effects are sought after for improved adaptation to physical training.
Carina de Sousa Santos, Fabrício Expedito Lopes Nascimento   +1 more
doaj   +1 more source

Dataset reporting BCKDK interference in a BCAA-catabolism restricted environment

Data in Brief, 2016
This data article contains complementary figures to the research article “Mitochondrial response to the BCKDK-deficiency: some clues to understand the positive dietary response in this form of autism” [1]. Herein we present data relative to the effect of
I. Bravo-Alonso, A. Oyarzabal, M. Sánchez-Aragó, M.T. Rejas, B. Merinero, A. García-Cazorla, R. Artuch, M. Ugarte, P. Rodríguez-Pombo   +8 more
doaj   +1 more source

In Vivo Incorporation of Multiple Unnatural Amino Acids [PDF]

, 2009
Unnatural amino acid (UAA) incorporation is an invaluable technique that is seeing increased use. THG73 is an amber suppressor tRNA used to incorporate > 100 residues at the UAG, amber stop codon, in Xenopus oocytes.
Rodriguez, Erik Ali
core   +1 more source