Results 11 to 20 of about 119,784 (210)

Spectrum of diagnosis of hereditary angioedema: Seven case reports

Indian Journal of Allergy Asthma and Immunology, 2020
Hereditary angioedema (HAE) is a potentially life-threatening disorder, due to a mutation in complement one-inhibitor (C1-INH) gene, which blocks the activity of various components of complement – fibrinolytic and bradykinin control system.
P C Kathuria, Manisha Rai, Neelam Kathuria   +2 more
doaj   +1 more source

Hereditary angioedema: Diagnostic algorithm and current treatment concepts

Indian Dermatology Online Journal, 2021
Hereditary angioedema (HAE) is an uncommon disorder with a global prevalence of approximately 1 in 10,000 to 1 in 50,000 population. This disease is grossly underrecognized in India because of lack of awareness and/or lack of diagnostic facilities ...
Ankur Kumar Jindal, Anuradha Bishnoi, Sunil Dogra   +2 more
doaj   +1 more source

Hereditary angioedema (HAE) in children and adolescents : a consensus on therapeutic strategies [PDF]

, 2012
Hereditary angioedema due to C1 inhibitor (C1 esterase inhibitor) deficiency (types I and II HAE-C1-INH) is a rare disease that usually presents during childhood or adolescence with intermittent episodes of potentially life-threatening angioedema ...
Aberer, Werner, Eberl, Wolfgang, Faßhauer, Maria, Kreuz , Wolfhart, Kurnik, Karin, Kühne, Thomas, Magerl, Markus, Martinez Saguer, Inmaculada, Meyer-Olson, Dirk, Späth, Peter J., Staubach-Renz, Petra, Wahn, Volker   +11 more
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The effects of continuous venovenous hemofiltration on coagulation activation [PDF]

, 2006
INTRODUCTION: The mechanism of coagulation activation during continuous venovenous hemofiltration (CVVH) has not yet been elucidated. Insight into the mechanism(s) of hemostatic activation within the extracorporeal circuit could result in a more rational
Bouman, Catherine S. C., de Pont, Anne-Cornélie J. M., Meijers, Joost C. M., Bakhtiari, Kamran, Roem, Dorina, Zeerleder, Sacha, Wolbink, Gertjan, Korevaar, Johanna C., Levi, Marcel, de Jonge, Evert   +9 more
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C1-Inhibitor protects from focal brain trauma in a cortical cryolesion mice model by reducing thrombo-inflammation

Frontiers in Cellular Neuroscience, 2014
Traumatic brain injury (TBI) induces a strong inflammatory response which includes blood-brain barrier damage, edema formation and infiltration of different immune cell subsets.
Christiane eAlbert-Weissenberger, Stine eMencl, Michael K. Schuhmann, Irmak eSalur, Eva eGöb, Friederike eLangenhauser, Sarah eHopp, Nelli eHennig, Sven G Meuth, Sven G Meuth, Marc W. Nolte, Anna-Leena eSirén, Christoph eKleinschnitz   +12 more
doaj   +1 more source

Activation of coagulation factor XI, without detectable contact activation in dengue haemorrhagic fever [PDF]

, 2001
A prospective cohort study was performed in 50 patients with dengue haemorrhagic fever (DHF) to determine the potential role of the contact activation system and factor XI activation (intrinsic pathway) in the coagulation disorders in DHF.
Bajzar, Bhamarapravati, Broze, Broze, Broze, Broze, Chetaille, Davie, Gailani, Groen, Jansen, Levi, Meijers, Minnema, Minnema, Minnema, Mosnier, Naito, Perez-Rigau, Pixley, Srichaikul, Ten Cate, Van der Poll, Van Gorp, Van Gorp, Von dem Borne, Von dem Borne, Wang, World Health Organization., Wuillemin   +29 more
core   +2 more sources

Optimum Use of Acute Treatments for Hereditary Angioedema: Evidence-Based Expert Consensus

Frontiers in Medicine, 2018
Acute treatment of hereditary angioedema due to C1 inhibitor deficiency has become available in the last 10 years and has greatly improved patients’ quality of life.
Hilary Longhurst
doaj   +1 more source

Hereditary angioedema: approaches to diagnosis and treatment, analysis of a clinical family case

Медицинский совет, 2021
Hereditary angioedema belongs to the group of rare, orphan, genetically determined defects that represent a significant medical and social problem due to the pronounced impact on the quality of life and potential mortality, as well as the emerging ...
O. V. Skorohodkina, A. V. Luntsov, A. A. Vasileva, O. A. Bareycheva   +3 more
doaj   +1 more source

Quantification of C1 esterase inhibitor in human serum by enzyme-linked immunosorbent assay: Correlation with turbidimetric immunoassay

Медицинская иммунология, 2023
C1 inhibitor of serine proteases (C1-INH) performs a regulatory function in the complement system and vascular permeability. Deficiency of C1-INH leads to various forms of angioedema, including hereditary angioedema (HAE).
N. P. Gorbunov, A. V. Zhakhov, I. N. Gorbunova, A. M. Milichkina, I. V. Drozd, A. V. Gubanova, E. M. Danilova, R. N. Kuznecova, T. V. Savin, A. G. Burtseva, N. V. Pigareva, A. M. Ischenko, Areg A. Totolian   +12 more
doaj   +1 more source

The hereditary angioedema burden of illness study in Europe (HAE-BOIS-Europe) : background and methodology [PDF]

, 2012
Background: Hereditary angioedema (HAE) is a rare but serious disease marked by swelling attacks in the extremities, face, trunk, airway, or abdominal areas that can be spontaneous or the result of trauma and other triggers.
Aygören-Pürsün, Emel, Beusterien, Kathleen, Boysen, Henrik B., Bygum, Anette, Caballero, Teresa, Gholizadeh, Shadi, Musingarimi, Patience, Wait, Suzanne   +7 more
core   +2 more sources