Results 261 to 270 of about 98,834 (305)

Angioedema due to acquired C1-inhibitor deficiency without hematological condition: a multicenter French cohort study of 34 patients.

Journal of Allergy and Clinical Immunology: In Practice
BACKGROUND Angioedema (AE) due to acquired C1-inhibitor deficiency (AAE-C1-INH) is a rare disease associating recurrent edema of mucosa and skin.
R. Stammler, F. Defendi, M. Aubineau, Beatrice Bibes, I. Boccon-Gibod, L. Bouillet, Y. Crabol, Marie-Caroline Dalmas, C. de Moreuil, Aurélien Delluc, Claire Dingremont, A. Du-Thanh, J. Hadjadj, Pierre-Yves Jeandel, Galith Kalmi, M. Lacoste, Ludovic Martin, Chloé Mc Avoy, C. Blanchard-Delaunay, M. Taquet, O. Fain, D. Gobert   +21 more
semanticscholar   +1 more source

Comorbidities in Angioedema due to C1-inhibitor deficiency: an Italian survey.

Journal of Allergy and Clinical Immunology: In Practice
BACKGROUND Hereditary angioedema due to C1-inhibitor deficiency (HAE) is characterized by unpredictable recurrent episodes of swelling affecting the skin and the mucosa tissues, including gastrointestinal tract and/or oro-pharyngeal-laryngeal mucosae ...
A. Zanichelli, R. Senter, Andrea Merlo, A. Gidaro, V. P. Janu, C. Cogliati, M. Cancian   +6 more
semanticscholar   +1 more source

The importance of recognizing and managing a rare form of angioedema: hereditary angioedema due to C1-inhibitor deficiency

Postgraduate medicine, 2021
The majority of angioedema cases encountered in clinical practice are histamine-mediated (allergic); however, some cases are bradykinin-related (non-allergic) and do not respond to standard anti-allergy medications.
J. Jacobs, T. Neeno
semanticscholar   +1 more source

The metabolism of C1 inhibitor and C1q in patients with acquired C1-inhibitor deficiency

Journal of Allergy and Clinical Immunology, 1986
The metabolism of 125I-labeled C1 inhibitor (C1INH) and C1q was studied in five patients with B cell lymphoproliferative disorders, C1INH deficiency, and angioedema. C1INH catabolism was markedly accelerated in these patients. The fractional catabolic rate (FCR) was 0.053 of the plasma pool per hour compared to that of normal subjects (0.025) or ...
J, Melamed, C A, Alper, M, Cicardi, F S, Rosen   +3 more
openaire   +4 more sources

Angioedema associated with C1 inhibitor deficiency

Clinical Reviews in Allergy & Immunology, 1999
Angioedema associated with C1 INH deficiency requires diagnosis as soon as the first symptoms of the disease are manifest, and laboratory measurement of complement component levels at the least suspicion, in order to institute preventive and curative treatments.
J, Laurent, M T, Guinnepain
openaire   +2 more sources

A follow‐up survey of patients with acquired angioedema due to C1‐inhibitor deficiency

Journal of Internal Medicine, 2020
Acquired angioedema due to C1‐inhibitor deficiency (C1‐INH‐AAE) is a rare form of bradykinin‐mediated angioedema. It is diagnosed by complement testing; its treatment consists of the management of angioedema (AE) attacks and of underlying disease.
Zs Pólai, Zsuzsanna Balla, Noémi Andrási, K. V. Kőhalmi, G. Temesszentandrási, S. Benedek, Lilian Varga, Henriette Farkas   +7 more
semanticscholar   +1 more source

Danazol® and C1 Esterase Inhibitor Deficiency

Annals of Internal Medicine, 1978
Excerpt To the editor: We write to confirm the findings of Hauptmann and associates (1) on the therapy of acquired C1 esterase inhibitor (C1 INH) deficiency with Danazol®.
S H, Cohen, S M, Koethe
openaire   +2 more sources

C1 inhibitor deficiency: diagnosis.

Clinical and Experimental Dermatology, 2005
This is the first of two articles on C1 inhibitor deficiency based on a recent UK consensus document covering diagnosis and management of the disorder in both adults and children. This paper focuses on diagnosis of this disorder.
M M, Gompels, R J, Lock
openaire   +2 more sources

Acute consumption of C1 inhibitor in a patient with acquired C1-inhibitor deficiency syndrome

Journal of Allergy and Clinical Immunology, 1991
Acquired C1-inhibitor (C1 INH) deficiency is usually found in association with an underlying disease that is believed to be responsible for increased C1 INH catabolism, ultimately leading to the development of C1 INH deficiency. We report a remarkable patient with acquired C1 INH deficiency in whom a unique progression of complement- and contact-system
B L, Zuraw, L C, Altman
openaire   +2 more sources

Treatment of Acquired C1-Inhibitor Deficiency with Danazol

Annals of Internal Medicine, 1977
Excerpt Hereditary angioedema is characterized by a marked deficiency of the inhibitor of activated first component of complement (C1 inhibitor).
G, Hauptmann, S, Mayer, J M, Lang, F, Oberling, G, Mayer   +4 more
openaire   +2 more sources