Results 51 to 60 of about 28,186 (243)

Benign Recurrent Intrahepatic Cholestases [PDF]

, 2001
Benign recurrent intrahepatic cholestasis (BRIC) or idiopathic recurrent intrahepatic cholestasis is a rare case. It is a familial and autosomal recessive. The etiology of BRIC is still unknown. We report the case of a patient with BRIC who suffered from
Akbar, F. N. (Femmy), Budihusodo, U. (Unggul), Lesmana, L. A. (L), Marwoto, W. (Wirasmi), Noer, S. (Sjaifoellah)   +4 more
core   +1 more source

A Randomized, Controlled, Phase 2 Study of Maralixibat in the Treatment of Itching Associated With Primary Biliary Cholangitis. [PDF]

, 2019
Primary biliary cholangitis (PBC) is typically associated with elevated serum bile acid levels and pruritus, but pruritus is often refractory to treatment with existing therapies.
Apostol, George, Bacon, Bruce, Bowlus, Christopher L, Dorenbaum, Alejandro, Gu, Joan, Hirschfield, Gideon M, Jones, David, Kennedy, Ciara, Levy, Cynthia, Luketic, Velimir, Mayo, Marlyn J, Medendorp, Sharon, Novak, Patricia, Patanwala, Imran, Pockros, Paul J, Vuppalanchi, Raj   +15 more
core   +2 more sources

Benign recurrent intrahepatic cholestasis (BRIC): Evidence of genetic heterogeneity and delimitation of the BRIC locus to a 7-cM interval between D18S69 and D18S64 [PDF]

, 1997
Benign recurrent intrahepatic cholestasis (BRIC) is an autosomal recessive liver disease characterized by multiple episodes of cholestasis without progression to chronic liver disease.
Amstel, H.K.P. van, Berge Henegouwen, G.P. (Gerard) van, Berger, R. (Ruud), Bijleveld, C.M.A. (Charles M.), Bull, I.D. (Ian), Carlton, V.E.H. (Victoria E.), Delhaas, T. (Tammo), Freimer, N.B. (Nelson), Hattum, J. (Jan) van, Houwen, R.H.J. (Roderick), Juijn, J.A. (Jenneke), Keller, K.M. (Klaus), Knol, I.E. (Irma), Pearson, P.L., Sinaasappel, M. (Maarten), Sinke, R.J. (Richard)   +15 more
core   +4 more sources

Bile Acid Receptor Therapeutics Effects on Chronic Liver Diseases [PDF]

, 2020
In the past ten years, our understanding of the importance of bile acids has expanded from fat absorption and glucose/lipid/energy homeostasis into potential therapeutic targets for amelioration of chronic cholestatic liver diseases.
Alpini, Gianfranco, Francis, Heather, Kennedy, Lindsey, Kundu, Debjyoti, Meadows, Vik   +4 more
core   +1 more source

DIFFERENCES OF BIRTH WEIGHT AND ONSET OF ACHOLIC STOOL BETWEEN EXTRAHEPATIC AND INTRAHEPATIC CHOLESTASIS

Indonesian Midwifery and Health Sciences Journal
Background: Biliary atresia (extrahepatic cholestasis) and neonatal hepatitis (intrahepatic cholestasis) are two main causes of cholestasis. It is important to distinguish the type of cholestasis for determine management.
Bagus Setyoboedi, Lasmauli Situmorang, Rendi Aji Prihaningtyas, Sjamsul Arief   +3 more
doaj   +1 more source

Recent advances in the exploration of the bile salt export pump (BSEP/ABCB11) function [PDF]

, 2016
ntroduction: The bile salt export pump (BSEP/ABCB11), residing in the apical membrane of hepatocyte, mediates the secretion of bile salts into the bile.
Homolya, László, Telbisz, Ágnes Mária   +1 more
core   +1 more source

Assessment of aspartate aminotransferase to Platelet Ratio Index and Fibrosis-4 Index score on women with intrahepatic cholestasis of pregnancyAJOG Global Reports at a Glance

AJOG Global Reports
BACKGROUND: Intrahepatic cholestasis of pregnancy is a pregnancy-related liver condition that is characterized by elevated liver function tests and/or bile acids in the presence of pruritis.
Maria Cemortan, PhD, Corina Iliadi-Tulbure, PhD, Irina Sagaidac, PhD, Olga Cernetchi, PhD   +3 more
doaj   +1 more source

Clinical Presentation, Cholangiographic Features, Natural History, and Outcome: A Series of 16 Cases [PDF]

, 2015
Secondary sclerosing cholangitis in critically ill patients (SSC-CIP) is an important differential diagnosis in patients presenting with cholestasis and PSC-like cholangiographic changes in endoscopic retrograde cholangiography (ERC).
Adler, Andreas, Eurich, Dennis, Faber, Wladimir, Leonhardt, Silke, Neuhaus, Peter, Schott, Eckart, Seehofer, Daniel, Veltzke-Schlieker, Wilfried   +7 more
core   +1 more source

A genome-wide association study identifies a susceptibility locus for biliary atresia on 2p16.1 within the gene EFEMP1 [PDF]

, 2018
Biliary atresia (BA) is a rare pediatric cholangiopathy characterized by fibrosclerosing obliteration of the extrahepatic bile ducts, leading to cholestasis, fibrosis, cirrhosis, and eventual liver failure.
Bailey-Wilson, Joan E, Chen, Ying, Devoto, Marcella, Gilbert, Melissa A, Grochowski, Christopher M, Hakonarson, Hakon, Llewellyn, Jessica, Loomes, Kathleen M, Mceldrew, Deborah, Russo, Pierre, Spinner, Nancy B, Waisbourd-Zinman, Orith, Wells, Rebecca G   +12 more
core   +2 more sources

The debut of benign recurrent intrahepatic cholestasis in acute hepatitis A

Трансплантология (Москва)
Background. Benign recurrent intrahepatic cholestasis is a rare inherited disorder characterized by recurrent episodes of severe hyperbilirubinemia and pruritus that resolve spontaneously.
K. Yu. Kokina, Yu. O. Malinovskaya, O. V. Sumtsova, A. O. Grigorevskaya, Ya. G. Moysyuk   +4 more
doaj   +1 more source