Results 1 to 10 of about 1,188 (177)

IgG4-related disease presenting with combined pulmonary fibrosis and emphysema (CPFE) [PDF]

Respiratory Medicine Case Reports, 2018
A 64-year-old man was admitted to our hospital with an abnormal chest shadow. The patient was a current-smoker and had a past illness of autoimmune pancreatitis with a high serum level of IgG4, 348 mg/dL.
Masato Kono, Yutaro Nakamura, Yoshiyuki Oyama, Go Saito, Yu Koyanagi, Koichi Miyashita, Akari Tsutsumi, Yasunori Enomoto, Takeshi Kobayashi, Yoshihiro Miki, Dai Hashimoto, Noriyuki Enomoto, Thomas V. Colby, Takafumi Suda, Hidenori Nakamura   +14 more
doaj   +5 more sources

Combined Pulmonary Fibrosis and Emphysema (CPFE) Clinical Features and Management [PDF]

International Journal of COPD, 2021
René Hage,1,2 Fiorenza Gautschi,1,2 Carolin Steinack,1,2 Macé M Schuurmans1,2 1University Hospital Zurich, Division of Pulmonology, Zurich, Switzerland; 2University of Zurich, Faculty of Medicine, Zurich, SwitzerlandCorrespondence: Ren ...
Hage R, Gautschi F, Steinack C, Schuurmans MM   +3 more
doaj   +9 more sources

Serum Levels of Surfactant Proteins in Patients with Combined Pulmonary Fibrosis and Emphysema (CPFE). [PDF]

PLoS ONE, 2016
Emphysema and idiopathic pulmonary fibrosis (IPF) present either per se or coexist in combined pulmonary fibrosis and emphysema (CPFE). Serum surfactant proteins (SPs) A, B, C and D levels may reflect lung damage.
Andriana I Papaioannou, Konstantinos Kostikas, Effrosyni D Manali, Georgia Papadaki, Aneza Roussou, Aris Spathis, Argyro Mazioti, Ioannis Tomos, Ilias Papanikolaou, Stelios Loukides, Kyriakos Chainis, Petros Karakitsos, Matthias Griese, Spyros Papiris   +13 more
doaj   +11 more sources

Combined Pulmonary Fibrosis and Emphysema (CPFE): A “New” Smoking-Related Interstitial Lung Disease (ILD) [PDF]

Biomedicines
Background: Combined Pulmonary Fibrosis and Emphysema (CPFE) is a distinct syndrome characterized by upper-lobe emphysema and lower-lobe fibrosis, predominantly in older male smokers. Despite often preserved spirometric volumes, patients exhibit severely
Carina Adina Afloarei, Tudor Birladeanu, Adriana Loredana Pintilie, David Toma, Dragos Traian Marius Marcu, Andreea Zabara Antal, Mihai Zabara, Radu Crisan Dabija   +7 more
doaj   +4 more sources

Combined Pulmonary Fibrosis and Emphysema: Pulmonary Function Testing and a Pathophysiology Perspective

Medicina, 2019
Combined pulmonary fibrosis and emphysema (CPFE) has been increasingly recognized over the past 10−15 years as a clinical entity characterized by rather severe imaging and gas exchange abnormalities, but often only mild impairment in spirometric ...
Diana E. Amariei, Neal Dodia, Janaki Deepak, Stella E. Hines, Jeffrey R. Galvin, Sergei P. Atamas, Nevins W. Todd   +6 more
doaj   +4 more sources

Combined pulmonary fibrosis and emphysema: a narrative review [PDF]

Frontiers in Medicine
Combined pulmonary fibrosis and emphysema (CPFE) is defined as a clinical-radiological-physiological syndrome characterized by upper-lobe emphysema and fibrosis predominantly in the lower lobes.
Wenjing Zeng, Binmiao Liang, Xuemei Ou
doaj   +2 more sources

An increased risk of lung cancer in combined pulmonary fibrosis and emphysema patients with usual interstitial pneumonia compared with patients with idiopathic pulmonary fibrosis alone: a systematic review and meta-analysis

Therapeutic Advances in Respiratory Disease, 2021
Background: Lung cancer is an important complication of combined pulmonary fibrosis and emphysema (CPFE). Whether the risk of lung cancer is higher in CPFE patients with usual interstitial pneumonia (UIP) than those with idiopathic pulmonary fibrosis ...
Qianqian Chen, Ping Liu, Hong Zhou, Hui Kong, Weiping Xie   +4 more
doaj   +2 more sources

Prognosis of combined pulmonary fibrosis and emphysema: comparison with idiopathic pulmonary fibrosis alone

Therapeutic Advances in Respiratory Disease, 2019
Background: Combined pulmonary fibrosis and emphysema (CPFE) is a syndrome characterized by the coexistence of upper lobe emphysema and lower lobe fibrosis.
Chun-guo Jiang, Qiang Fu, Chun-ming Zheng   +2 more
doaj   +2 more sources

The prevalence and unique clinical features of CPFE among patients with connective tissue disease–associated interstitial lung disease: a retrospective, real-world study [PDF]

Therapeutic Advances in Respiratory Disease
Background: Combined pulmonary fibrosis and emphysema (CPFE) is a distinct yet clinically underrecognised syndrome. Interstitial pneumonia is a common pulmonary manifestation of connective tissue diseases (CTDs), and some CTD-interstitial lung disease ...
Shuwan Huang, Aiyuan Zhou, Wei Cheng, Qing Song, Xiyan Zhang, Wenzhong Peng, Yanan Wang, Haiyuan Tang, Rongli Lu, Ruoxi He, Pinhua Pan   +10 more
doaj   +2 more sources

Single-cell RNA sequencing elucidates potential mechanisms of endothelial cells in lung region-specific repair and remodeling in combined pulmonary fibrosis and emphysema [PDF]

Respiratory Research
Background Combined pulmonary fibrosis and emphysema (CPFE) is a severe and progressive lung disease with limited therapeutic options and poor prognosis. CPFE manifests as emphysema and fibrosis in different lung regions and is frequently associated with
Huiyuan Hu, Zhuangjie Guo, Jin Zhang, Yidan Gao, Xuehan Jiang, Haoshuai Yang, Yufei Hu, Hong Zhang, Wanlu Song, Chaoyang Liang, Peiran Yang, Chen Wang   +11 more
doaj   +2 more sources