Adult onset of xanthelasmoid mastocytosis: Report of a rare entity
Xanthelasmoid or pseudoxanthomatous mastocytosis is an extremely rare variant of diffuse cutaneous mastocytosis. Herein, we describe an adult male with cutaneous mastocytosis showing multiple widespread yellowish ovoid papules like eruptive xanthoma.
Nafiseh Sadat Nabavi +4 more
doaj +2 more sources
Diffuse cutaneous bullous mastocytosis in a neonate
Gajanand M Antakanavar +3 more
doaj +3 more sources
An infant with bullous mastocytosis: A rare form of bullous disorder
Bullous mastocytosis (BM) is a rare variant of diffuse cutaneous mastocytosis where there is disorderly infiltration of the skin by mast cells. We report a 4-month-old male infant with this rare disease who presented with wrinkled tough skin and ...
Aniruddha Ghosh +2 more
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Omalizumab for Pediatric Cutaneous Mastocytosis: Case Report and Review. [PDF]
ABSTRACT We report an 11‐month‐old boy with diffuse cutaneous mastocytosis whose severe pruritus and steroid dependence resolved following off‐label treatment with omalizumab. A literature review identified five additional pediatric cases in which omalizumab led to complete symptom resolution in an average of 2 months and permitted discontinuation of ...
Chang J, King A, Byrne A, Liy-Wong C.
europepmc +2 more sources
Characteristics and outcomes of patients with pediatric-onset non-mastocytosis mast cell activation disorders: A CEREMAST study. [PDF]
Abstract Background Mast cell (MC) activation (MCA) disorders (MCAD) include diseases in which MCs excessively release mediators leading to recurrent manifestations of MCA. MCAD encompasses MCA syndrome (MCAS) which is defined by (i) documented systemic symptoms of MCA, (ii) a 20% increase in serum tryptase level from the individual's baseline plus 2 ...
Weiss M +25 more
europepmc +2 more sources
CD30 Expression in Neoplastic Mast Cells and the Presence of CD30+, CD3+, and PAX-5+ Tumour-Infiltrating Lymphocytes as Prognostic Markers in Canine Cutaneous Mast Cell Tumours. [PDF]
ABSTRACT Canine cutaneous mast cell tumour (MCT) is the most common skin neoplasm in dogs, with histopathology serving as both the diagnostic and primary prognostic tool. However, identifying reliable biomarkers is essential for improving clinical decision‐making.
Ramos FR +6 more
europepmc +2 more sources
Background. Mastocytosis is a disease characterized by the presence of mast cells in various organs. The skin is affected most often. Almost every patient diagnosed with mastocytosis has skin lesions.
O.L. Statkevych, T.V. Sviatenko
doaj +1 more source
Diffuse Cutaneous Mastocytosis with Bullous Presentation: A Rare Case Report
Vibhu Mendiratta +3 more
doaj +2 more sources
Pseudoxanthomatous mastocytosis in a 2-month female infant
Mastocytosis is a rare disease characterized by infiltration of mast cells in various tissues like skin, bone marrow, liver, spleen, and gastrointestinal tract. Here, we present a case report of diffuse cutaneous mastocytosis (pseudoxanthomatous type) in
Tulika Rai +3 more
doaj +1 more source
Localized Pseudoxanthomatous Mastocytosis of Vulva
Cutaneous mastocytosis (CM) is a mast cell proliferative disorder that is common in the pediatric age group. Common entities are urticaria pigmentosa, solitary mastocytoma, telangiectasia macularis eruptive perstans. and diffuse CM.
Shivi Nijhawan +2 more
doaj +1 more source

