Results 31 to 40 of about 3,256 (112)
Aggressive Systemic Mastocytosis with a Relatively Non-aggressive Course
Background: Mastocytosis is a heterogeneous group of disorders that is characterized by excessive proliferation and pathologic accumulation of mast cells in various body tissues.
Aishwarya Madaan +6 more
doaj +1 more source
Adult onset of xanthelasmoid mastocytosis: Report of a rare entity
Xanthelasmoid or pseudoxanthomatous mastocytosis is an extremely rare variant of diffuse cutaneous mastocytosis. Herein, we describe an adult male with cutaneous mastocytosis showing multiple widespread yellowish ovoid papules like eruptive xanthoma.
Nafiseh Sadat Nabavi +4 more
doaj +1 more source
ABSTRACT Gilvetmab is a caninised monoclonal antibody against canine PD‐1. Concurrent or sequential administration of anti‐PD‐1 antibodies and radiation therapy (RT) improves survival time in various species. Eighteen dogs with mast cell tumours (MCTs) were prospectively treated with 24 Gy of RT over Days 0, 7 and 21 and gilvetmab every 2 weeks ...
Tiffany W. Martin +2 more
wiley +1 more source
Generalized Blistering in Infancy: A Rare Case Report on Bullous Mastocytosis
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation of mast cells, associated with c-KIT mutations. The disease is most frequently observed in childhood, with clinical presentations ranging from solitary mastocytoma to diffuse
Aditi Haldar +3 more
doaj +1 more source
Graphical abstract illustrating the clinical course and treatment response. ABSTRACT Systemic mastocytosis (SM) is a clonal hematologic neoplasm driven by activating KIT mutations, particularly D816V. Indolent SM typically follows a stable course, progression to higher‐burden subtypes is uncommon.
Homeniuk Anna +5 more
wiley +1 more source
Mastocitose bolhosa na criança: relato de caso Bullous mastocytosis in child: case report
A mastocitose é doença rara, definida como a infiltração desordenada de mastócitos em vários tecidos. Compreende diferentes quadros clínicos, variando de formas cutâneas indolentes a condições sistêmicas e malignas. O termo mastocitose bolhosa descreve a
Ana Lúcia França da Costa +2 more
doaj +1 more source
Mastocytosis is a condition characterized by the disorderly infiltration of mast cells in several tissues and comprises many different clinical situations varying from indolent cutaneous forms to malignant and systemic conditions. Bullous mastocytosis is
Nayak Surajit +3 more
doaj
Diagnosing Systemic Mastocytosis: State of the Art
ABSTRACT With the advent of effective multikinase and selective tyrosine kinase inhibitors in systemic mastocytosis, diagnosing this rare disease has been critical to improving patient morbidity and mortality. This state‐of‐the‐art review interprets the international diagnostic criteria, including differences between the WHO 5th edition classification ...
Anton Rets, Tracy I. George
wiley +1 more source
An infant with bullous mastocytosis: A rare form of bullous disorder
Bullous mastocytosis (BM) is a rare variant of diffuse cutaneous mastocytosis where there is disorderly infiltration of the skin by mast cells. We report a 4-month-old male infant with this rare disease who presented with wrinkled tough skin and ...
Aniruddha Ghosh +2 more
doaj +1 more source
A 60-year-old lady with leonine facies: A rare diagnosis
Systemic mastocytosis is a rare clonal disorder characterized by mast cell infiltration of one or more organs, with or without skin involvement. Leonine facies is a rare presentation and corresponds to the morphologic manifestation of diffuse dermal ...
Deepti Mutreja +3 more
doaj +1 more source

