Results 31 to 40 of about 3,256 (112)

Aggressive Systemic Mastocytosis with a Relatively Non-aggressive Course

open access: yesIndian Pediatrics Case Reports, 2022
Background: Mastocytosis is a heterogeneous group of disorders that is characterized by excessive proliferation and pathologic accumulation of mast cells in various body tissues.
Aishwarya Madaan   +6 more
doaj   +1 more source

Adult onset of xanthelasmoid mastocytosis: Report of a rare entity

open access: yesIndian Journal of Dermatology, 2016
Xanthelasmoid or pseudoxanthomatous mastocytosis is an extremely rare variant of diffuse cutaneous mastocytosis. Herein, we describe an adult male with cutaneous mastocytosis showing multiple widespread yellowish ovoid papules like eruptive xanthoma.
Nafiseh Sadat Nabavi   +4 more
doaj   +1 more source

Combination of Hypofractionated Radiation Therapy and Gilvetmab for the Treatment of Cutaneous or Subcutaneous Mast Cell Tumours in Dogs

open access: yesVeterinary and Comparative Oncology, EarlyView.
ABSTRACT Gilvetmab is a caninised monoclonal antibody against canine PD‐1. Concurrent or sequential administration of anti‐PD‐1 antibodies and radiation therapy (RT) improves survival time in various species. Eighteen dogs with mast cell tumours (MCTs) were prospectively treated with 24 Gy of RT over Days 0, 7 and 21 and gilvetmab every 2 weeks ...
Tiffany W. Martin   +2 more
wiley   +1 more source

Generalized Blistering in Infancy: A Rare Case Report on Bullous Mastocytosis

open access: yesNepal Journal of Dermatology, Venereology & Leprology
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation of mast cells, associated with c-KIT mutations. The disease is most frequently observed in childhood, with clinical presentations ranging from solitary mastocytoma to diffuse
Aditi Haldar   +3 more
doaj   +1 more source

Smoldering Systemic Mastocytosis Without Detectable KIT Mutation: A Debilitating Course and Therapeutic Challenge

open access: yesCancer Nexus, Volume 2, Issue 3, July 2026.
Graphical abstract illustrating the clinical course and treatment response. ABSTRACT Systemic mastocytosis (SM) is a clonal hematologic neoplasm driven by activating KIT mutations, particularly D816V. Indolent SM typically follows a stable course, progression to higher‐burden subtypes is uncommon.
Homeniuk Anna   +5 more
wiley   +1 more source

Mastocitose bolhosa na criança: relato de caso Bullous mastocytosis in child: case report

open access: yesAnais Brasileiros de Dermatologia, 2005
A mastocitose é doença rara, definida como a infiltração desordenada de mastócitos em vários tecidos. Compreende diferentes quadros clínicos, variando de formas cutâneas indolentes a condições sistêmicas e malignas. O termo mastocitose bolhosa descreve a
Ana Lúcia França da Costa   +2 more
doaj   +1 more source

Bullous mastocytosis

open access: yesIndian Journal of Dermatology, 2007
Mastocytosis is a condition characterized by the disorderly infiltration of mast cells in several tissues and comprises many different clinical situations varying from indolent cutaneous forms to malignant and systemic conditions. Bullous mastocytosis is
Nayak Surajit   +3 more
doaj  

Diagnosing Systemic Mastocytosis: State of the Art

open access: yesInternational Journal of Laboratory Hematology, Volume 48, Issue 3, Page 551-560, June 2026.
ABSTRACT With the advent of effective multikinase and selective tyrosine kinase inhibitors in systemic mastocytosis, diagnosing this rare disease has been critical to improving patient morbidity and mortality. This state‐of‐the‐art review interprets the international diagnostic criteria, including differences between the WHO 5th edition classification ...
Anton Rets, Tracy I. George
wiley   +1 more source

An infant with bullous mastocytosis: A rare form of bullous disorder

open access: yesIndian Journal of Paediatric Dermatology, 2017
Bullous mastocytosis (BM) is a rare variant of diffuse cutaneous mastocytosis where there is disorderly infiltration of the skin by mast cells. We report a 4-month-old male infant with this rare disease who presented with wrinkled tough skin and ...
Aniruddha Ghosh   +2 more
doaj   +1 more source

A 60-year-old lady with leonine facies: A rare diagnosis

open access: yesIndian Journal of Pathology and Microbiology, 2012
Systemic mastocytosis is a rare clonal disorder characterized by mast cell infiltration of one or more organs, with or without skin involvement. Leonine facies is a rare presentation and corresponds to the morphologic manifestation of diffuse dermal ...
Deepti Mutreja   +3 more
doaj   +1 more source

Home - About - Disclaimer - Privacy