Results 71 to 80 of about 4,486 (172)
Biochemistry and Biophysics Reports, 2019 A-type lamins gene (LMNA) mutations cause an autosomal dominant inherited form of Emery-Dreifuss muscular dystrophy (EDMD). EDMD is characterized by slowly progressive muscle weakness and wasting and dilated cardiomyopathy, often leading to heart failure-
Nicolas Vignier +3 more
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Phenotype-Genotype Analysis of Chinese Patients with Early-Onset LMNA-Related Muscular Dystrophy. [PDF]
PLoS ONE, 2015 This study aimed to analyze the correlation between the phenotype and genotype of Chinese patients with early-onset lamin A (LMNA)-related muscular dystrophy (MD).
Dandan Tan +8 more
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Disease Models & Mechanisms, 2017 Mutations in the gene encoding emerin cause Emery–Dreifuss muscular dystrophy (EDMD). Emerin is an integral inner nuclear membrane protein and a component of the nuclear lamina. EDMD is characterized by skeletal muscle wasting, cardiac conduction defects
Carol M. Collins +2 more
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Cells, 2020 LMNA encodes for Lamin A/C, type V intermediate filaments that polymerize under the inner nuclear membrane to form the nuclear lamina. A small fraction of Lamin A/C, less polymerized, is also found in the nucleoplasm. Lamin A/C functions include roles in
Anne T. Bertrand +8 more
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The Canadian Journal of Chemical Engineering, Volume 103, Issue 3, Page 1099-1111, March 2025.In this work we develop a data‐driven modelling approach which integrates an autoencoder‐like neural network and dynamic mode decomposition (DMD) methods, to result in a nonlinear modelling technique. In addition, we develop a quadratic programming based model predictive controller (MPC) for the proposed model and implement an observer using ...
Xiaonian Wang +3 more
wiley +1 more source
Linear stability analysis of detonations via numerical computation and dynamic mode decomposition
, 2017 We introduce a new method to investigate linear stability of gaseous detonations that is based on an accurate shock-fitting numerical integration of the linearized reactive Euler equations with a subsequent analysis of the computed solution via the ...
Kabanov, Dmitry I., Kasimov, Aslan R.
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Proceedings in Applied Mathematics and Mechanics, Volume 25, Issue 1, March 2025.ABSTRACT We consider the Koopman operator semigroup (Kt)t≥0$(K^t)_{t\ge 0}$ associated with stochastic differential equations of the form dXt=AXtdt+BdWt$dX_t = AX_t\,dt + B\,dW_t$ with constant matrices A$A$ and B$B$ and Brownian motion Wt$W_t$. We prove that the reproducing kernel Hilbert space HC$\mathbb {H}_C$ generated by a Gaussian kernel with a ...
Friedrich M. Philipp +4 more
wiley +1 more source
, 2012 We report large-scale computer simulations of the hard-disk system at high densities in the region of the melting transition. Our simulations reproduce the equation of state, previously obtained using the event-chain Monte Carlo algorithm, with a ...
Anderson, Joshua A. +5 more
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IET Renewable Power Generation, Volume 19, Issue 1, January/December 2025.A method for system identification and prediction that combines the delay embedding technique with the Koopman operator is proposed. This novel approach allows for the recovery of system states even when only a partial set of state variables is measurable.
Le Zheng +4 more
wiley +1 more source
Noro-Frenkel scaling in short-range square well: A Potential Energy Landscape study
, 2006 We study the statistical properties of the potential energy landscape of a system of particles interacting via a very short-range square-well potential (of depth $-u_0$), as a function of the range of attraction $\Delta$ to provide thermodynamic insights
D. C. Rapaport +6 more
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